{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,20]],"date-time":"2025-10-20T10:26:15Z","timestamp":1760955975545},"reference-count":14,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2019,10,15]],"date-time":"2019-10-15T00:00:00Z","timestamp":1571097600000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"},{"start":{"date-parts":[[2019,10,15]],"date-time":"2019-10-15T00:00:00Z","timestamp":1571097600000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["BMC Med Imaging"],"published-print":{"date-parts":[[2019,12]]},"abstract":"<jats:title>Abstract<\/jats:title>\n              <jats:sec>\n                <jats:title>Background<\/jats:title>\n                <jats:p>Primary angiitis of the central nervous system (PACNS) is a rare disease, and tumor-like primary angiitis of the central nervous system is even rarer. Histopathology is the gold standard for tumor-mimicking PACNS. However, pathological diagnosis is relatively limited due to fewer biopsy opportunities.<\/jats:p>\n              <\/jats:sec>\n              <jats:sec>\n                <jats:title>Case presentation<\/jats:title>\n                <jats:p>A 68-year-old male presented with ataxia, and was diagnosed with tumor-like primary angiitis of the central nervous system. The patient underwent Intravenous drip glucocorticoid therapy (10\u2009mg of dexamethasone, daily). After 10\u2009days, the symptoms of the patient were completely relieved. Radiology revealed that the low density lesion in the right cerebellar hemisphere obviously narrowed. Cyclophosphamide therapy was not initiated.<\/jats:p>\n              <\/jats:sec>\n              <jats:sec>\n                <jats:title>Conclusion<\/jats:title>\n                <jats:p>It is crucial for clinicians to be aware of changes in radiology that indicate PACNS, since the diagnosis of tumor-like PACNS remains quite challenging. Glucocorticoid therapy is an effective therapy in this condition, and the prognosis can be favorable.<\/jats:p>\n              <\/jats:sec>","DOI":"10.1186\/s12880-019-0382-9","type":"journal-article","created":{"date-parts":[[2019,10,15]],"date-time":"2019-10-15T12:47:42Z","timestamp":1571143662000},"update-policy":"http:\/\/dx.doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":4,"title":["Ataxia as the main manifestation of tumor-like primary angiitis of the central nervous system: a case report and literature review"],"prefix":"10.1186","volume":"19","author":[{"given":"Yu-Jing","family":"Huang","sequence":"first","affiliation":[]},{"given":"Li","family":"Zhang","sequence":"additional","affiliation":[]},{"given":"Ying","family":"Mao","sequence":"additional","affiliation":[]},{"given":"Guang-Xian","family":"Nan","sequence":"additional","affiliation":[]}],"member":"297","published-online":{"date-parts":[[2019,10,15]]},"reference":[{"issue":"12","key":"382_CR1","doi-asserted-by":"publisher","first-page":"1732","DOI":"10.1136\/ard.2008.096800","volume":"67","author":"ES Molloy","year":"2008","unstructured":"Molloy ES, Singhal AB, Calabrese LH. Tumour-like mass lesion: an under-recognised presentation of primary angiitis of the central nervous system. Ann Rheum Dis. 2008;67(12):1732\u20135.","journal-title":"Ann Rheum Dis"},{"issue":"4","key":"382_CR2","doi-asserted-by":"publisher","first-page":"873","DOI":"10.1148\/rg.344135028","volume":"34","author":"AA Abdel Razek","year":"2014","unstructured":"Abdel Razek AA, Alvarez H, Bagg S, Refaat S, Castillo M. Imaging spectrum of CNS vasculitis. Radiographics. 2014;34(4):873\u201394.","journal-title":"Radiographics"},{"issue":"9","key":"382_CR3","doi-asserted-by":"publisher","first-page":"2401","DOI":"10.1161\/STROKEAHA.116.013917","volume":"47","author":"H de Boysson","year":"2016","unstructured":"de Boysson H, Boulouis G, Dequatre N, Godard S, N\u00e9el A, Arquizan C, et al. French Vasculitis study group. Tumor-like presentation of primary angiitis of the central nervous system. 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This study was conducted with approval from the Ethics Committee of China-Japan Union Hospital of Jilin University. A written informed consent was obtained from all participants.","order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Ethics approval and consent to participate"}},{"value":"A written informed consent was obtained from the patient for the publication of this case report and any accompanying images. A copy of the written consent is available for review upon reasonable request.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Consent for publication"}},{"value":"The authors declare that they have no competing interests.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Competing interests"}}],"article-number":"79"}}