{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,9,28]],"date-time":"2025-09-28T11:13:18Z","timestamp":1759057998824},"reference-count":10,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2021,2,18]],"date-time":"2021-02-18T00:00:00Z","timestamp":1613606400000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"},{"start":{"date-parts":[[2021,2,18]],"date-time":"2021-02-18T00:00:00Z","timestamp":1613606400000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["BMC Anesthesiol"],"published-print":{"date-parts":[[2021,12]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:sec>\n                <jats:title>Background<\/jats:title>\n                <jats:p>Paramyotonia congenita is a rare autosomal dominant myopathy which presents with periodic weakness due to cold and exercise. It is caused by mutations of the SCN4 gene which encodes the sodium channel in skeletal muscles.<\/jats:p>\n              <\/jats:sec><jats:sec>\n                <jats:title>Case presentation<\/jats:title>\n                <jats:p>We report a full term obstetric patient with both paramyotonia congenita and terminal filum lipoma who presents for induction of labour followed by an emergency caesarean section performed under epidural anesthesia. Her recovery is subsequently complicated by a 3-day history of postpartum paraparesis attributed to hypokalemic periodic paralysis.<\/jats:p>\n              <\/jats:sec><jats:sec>\n                <jats:title>Conclusion<\/jats:title>\n                <jats:p>We describe the perioperative anesthesia considerations and challenges in this case with a review of the current literature. This case report highlights the importance of early proactive and collaborative multidisciplinary approach, maintaining normal temperature and electrolytes with a heightened vigilance for muscle-related perioperative complications.<\/jats:p>\n              <\/jats:sec>","DOI":"10.1186\/s12871-021-01262-4","type":"journal-article","created":{"date-parts":[[2021,2,20]],"date-time":"2021-02-20T11:40:36Z","timestamp":1613821236000},"update-policy":"http:\/\/dx.doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":2,"title":["Anaesthesia challenges of a parturient with paramyotonia congenita and terminal filum lipoma presenting for labour and caesarean section under epidural anaesthesia \u2013 a case report"],"prefix":"10.1186","volume":"21","author":[{"given":"Wei Shyan","family":"Siow","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Wan-Ling Alyssa","family":"Chiew","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2021,2,18]]},"reference":[{"issue":"2","key":"1262_CR1","first-page":"343","volume":"29","author":"K Jurkat-Rott","year":"2010","unstructured":"Jurkat-Rott K, Lehmann-Horn F. State of the art in hereditary muscle channelopathies. Acta Myol. 2010;29(2):343\u201350.","journal-title":"Acta Myol"},{"key":"1262_CR2","unstructured":"Adams RD, Victor M, Ropper H. The hereditary myotomas and periodic paralyses. (The channelopathies) In: Principles of Neurology, 6th edition 1997: MC Graw Hill New York; 1997;54:476\u2013488."},{"issue":"5","key":"1262_CR3","doi-asserted-by":"publisher","first-page":"559","DOI":"10.3171\/2014.2.PEDS13528","volume":"13","author":"MJ Cools","year":"2014","unstructured":"Cools MJ, Al-Holou WN, Stetler WR Jr, Wilson TJ, Muraszko KM, Ibrahim M, La Marca F, Garton HJ, Maher CO. Filum terminale lipomas: imaging prevalence, natural history, and conus position. J Neurosurg Pediatr. 2014;13(5):559\u20136.","journal-title":"J Neurosurg Pediatr"},{"issue":"5","key":"1262_CR4","doi-asserted-by":"publisher","first-page":"534","DOI":"10.1177\/0310057X9802600511","volume":"27","author":"RF Grace","year":"1999","unstructured":"Grace RF, Roach VJ. Caesarean section in a patient with paramyotonia congenita. Anaesth Intensive Care. 1999;27(5):534\u20137.","journal-title":"Anaesth Intensive Care"},{"issue":"4","key":"1262_CR5","doi-asserted-by":"publisher","first-page":"345","DOI":"10.5152\/TJAR.2019.69094","volume":"47","author":"NM Najid","year":"2019","unstructured":"Najid NM, Razak TA, Gunaydin DB. Analgesia and Anaesthesia management of labour and Caesarean Delivery for a Parturient with Paramyotonia Congenita. Turk J Anaesthesiol Reanim. 2019;47(4):345\u20137.","journal-title":"Turk J Anaesthesiol Reanim"},{"issue":"1","key":"1262_CR6","doi-asserted-by":"publisher","first-page":"e3","DOI":"10.3171\/foc.2001.10.1.4","volume":"10","author":"JP Blount","year":"2001","unstructured":"Blount JP, Elton S. Spinal lipomas. Neurosurg Focus. 2001;10(1):e3.","journal-title":"Neurosurg Focus"},{"key":"1262_CR7","doi-asserted-by":"publisher","first-page":"692","DOI":"10.1093\/bja\/65.5.692","volume":"65","author":"F Lehmann Horn","year":"1990","unstructured":"Lehmann Horn F, Laizzo PA. Are myotonias and periodic paralysis associated with susceptibility to malignant hyperthermia. Br J Anaesth. 1990;65:692\u20137.","journal-title":"Br J Anaesth"},{"issue":"11","key":"1262_CR8","doi-asserted-by":"publisher","first-page":"1122","DOI":"10.1046\/j.1365-2044.2000.01547-4.x","volume":"55","author":"CR Broadbent","year":"2000","unstructured":"Broadbent CR, Maxwell WB, Ferrie R, Wilson DJ, Gawne-Cain M, Russell R. Ability of anaesthetists to identify a marked lumbar interspace. Anaesthesia. 2000;55(11):1122\u20136.","journal-title":"Anaesthesia"},{"key":"1262_CR9","doi-asserted-by":"publisher","first-page":"3","DOI":"10.1016\/S0065-2660(08)01001-8","volume":"63","author":"B Fontaine","year":"2008","unstructured":"Fontaine B. Periodic paralysis. Adv Genet. 2008;63:3\u201323.","journal-title":"Adv Genet"},{"key":"1262_CR10","doi-asserted-by":"crossref","unstructured":"Statland JM, Fontaine B, Hanna MG, Johnson NE, Kissel JT, Sansone VA, Shieh PB, Tawil RN, Trivedi J, Cannon SC, Griggs RC. Review of the Diagnosis and Treatment of Periodic Paralysis. 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