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The key to addressing this situation lies in completely removing the extrahepatic cyst. We herein present a case report of a 3-year-old boy with cholangiocarcinoma associated with a choledochal cyst (CDC). Preoperative 3D simulation, based on CT data, played an important role in the treatment of this patient.<\/jats:p>","DOI":"10.1186\/s12887-024-04709-y","type":"journal-article","created":{"date-parts":[[2024,4,5]],"date-time":"2024-04-05T06:02:09Z","timestamp":1712296929000},"update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":1,"title":["Cholangiocarcinoma identified in perforated choledochal cyst in a 3-year-old boy"],"prefix":"10.1186","volume":"24","author":[{"given":"Lun","family":"Yu","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Wenli","family":"Xiu","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Aimei","family":"Yue","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Xiwei","family":"Hao","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Zhong","family":"Jiang","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jie","family":"Wu","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Qian","family":"Dong","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2024,4,5]]},"reference":[{"key":"4709_CR1","doi-asserted-by":"publisher","first-page":"3334","DOI":"10.3748\/wjg.v25.i26.3334","volume":"25","author":"GN Baison","year":"2019","unstructured":"Baison GN, Bonds MM, Helton WS, et al. 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