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However, a cecal mass was identified instead of an inflamed appendix during surgery. Therapeutic decisions were extremely challenging due to clinical deterioration and an uncertain etiology. Only the histopathology report revealed the presence of a complete subserosal appendix which was responsible for the entire symptomatology. Here, we review all case reports regarding intramural, intracecal or subserosal appendixes. A discussion of the general approach to this specific case and the importance of consensual diagnostic criteria for these specimens are also presented. At last, an incidental finding is exposed and final treatment options are discussed given the overall presentation.<\/jats:p>\n              <\/jats:sec><jats:sec>\n                <jats:title>Conclusions<\/jats:title>\n                <jats:p>Considering these variants would guide physicians towards a more accurate approach to similar clinical pictures and hence an improved long-term prognosis.\n<\/jats:p>\n              <\/jats:sec>","DOI":"10.1186\/s12893-021-01429-3","type":"journal-article","created":{"date-parts":[[2021,12,16]],"date-time":"2021-12-16T15:03:18Z","timestamp":1639666998000},"update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":5,"title":["Incidental neuroendocrine tumor of a complete subserosal appendix: an unusual presentation of a rare anatomical variation. A case report and review of literature"],"prefix":"10.1186","volume":"21","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-4706-862X","authenticated-orcid":false,"given":"Stalin Isa\u00edas","family":"Ca\u00f1izares Quisigui\u00f1a","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Luc\u00eda Vanessa","family":"Guam\u00e1n Maldonado","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Iv\u00e1n Marcelo","family":"Hidalgo Jaramillo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Tatiana Paola","family":"Borja Herrera","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Cecilia de los \u00c1ngeles","family":"Carri\u00f3n Guzm\u00e1n","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2021,12,16]]},"reference":[{"issue":"1","key":"1429_CR1","doi-asserted-by":"publisher","first-page":"111","DOI":"10.1007\/s00276-017-1890-3","volume":"40","author":"S Chauhan","year":"2018","unstructured":"Chauhan S, Anand S. 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