{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,27]],"date-time":"2026-02-27T04:25:08Z","timestamp":1772166308205,"version":"3.50.1"},"reference-count":12,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2024,2,20]],"date-time":"2024-02-20T00:00:00Z","timestamp":1708387200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"},{"start":{"date-parts":[[2024,2,20]],"date-time":"2024-02-20T00:00:00Z","timestamp":1708387200000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["J Cardiothorac Surg"],"abstract":"<jats:title>Abstract<\/jats:title>\n                  <jats:sec>\n                    <jats:title>Background<\/jats:title>\n                    <jats:p>Junctional epidermolysis bullosa is a rare skin and mucosal disorder characterized by blister formation in response to minor trauma and extracutaneous manifestations. There have been no reports of cardiac surgery and prognostication in patients with epidermolysis bullosa due to skin and mucosal fragility.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Case presentation<\/jats:title>\n                    <jats:p>A 55-year-old man presented with congenital junctional epidermolysis bullosa, hypertension, and vasospastic angina. He complained of dyspnea on exertion, and transthoracic echocardiography revealed severe aortic valve regurgitation, moderate aortic valve stenosis (tricuspid valve), and severe mitral valve regurgitation. Considering that the skin condition in the right chest wall was relatively healthy, the right thoracotomy approach was preferred and totally endoscopic concomitant mitral valve repair and aortic valve replacement were performed using a sutureless bioprosthetic valve (Perceval\u2122 (Corcym, Group, Milan, Italy)). Polyurethane and silicon dressing foams were used to protect the skin at the site of contact with the bag valve mask, arterial pressure catheter, intravenous catheter, and the tracheal intubation tube. Vertical mattress sutures were used for the skin sutures. The postoperative course was uneventful, and the patient was discharged nine days after the operation. There was no indication for reoperation until three years follow-up period.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Conclusions<\/jats:title>\n                    <jats:p>The totally endoscopic concomitant aortic and mitral valve surgery using Perceval\u2122 prosthesis can be performed safely in patients with junctional epidermolysis bullosa by adequate protection of the skin and mucosa.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.1186\/s13019-024-02567-4","type":"journal-article","created":{"date-parts":[[2024,2,20]],"date-time":"2024-02-20T07:04:41Z","timestamp":1708412681000},"update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["Totally endoscopic concomitant aortic and mitral valve surgery in junctional epidermolysis bullosa: a case report"],"prefix":"10.1186","volume":"19","author":[{"given":"Kazufumi","family":"Yoshida","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Soshi","family":"Yoshida","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Yoshimasa","family":"Hori","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hideki","family":"Tsubota","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ryosuke","family":"Mochizuki","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Tohru","family":"Nagano","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Tadaaki","family":"Koyama","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2024,2,20]]},"reference":[{"key":"2567_CR1","doi-asserted-by":"publisher","first-page":"182","DOI":"10.2174\/1573396317666210525161252","volume":"18","author":"KL Hon","year":"2022","unstructured":"Hon KL, Chu S, Leung AKC. Epidermolysis bullosa: pediatric perspectives. Curr Pediatr Rev. 2022;18:182\u201390. https:\/\/doi.org\/10.2174\/1573396317666210525161252.","journal-title":"Curr Pediatr Rev"},{"key":"2567_CR2","unstructured":"Junctional epidermolysis bullosa. https:\/\/ghr.nlm.nih.gov\/condition\/junctional-epidermolysis-bullosa#"},{"key":"2567_CR3","doi-asserted-by":"publisher","first-page":"189","DOI":"10.1146\/annurev.me.44.020193.001201","volume":"44","author":"AN Lin","year":"1993","unstructured":"Lin AN, Carter DM. Epidermolysis bullosa. Annu Rev Med. 1993;44:189\u201399. https:\/\/doi.org\/10.1146\/annurev.me.44.020193.001201.","journal-title":"Annu Rev Med"},{"key":"2567_CR4","doi-asserted-by":"publisher","first-page":"404","DOI":"10.1046\/j.1524-4741.1999.98022.x","volume":"5","author":"JA Lyons","year":"1999","unstructured":"Lyons JA, Schlesinger TE, Smith MD, Camisa C, Turner JM, Crowe J, et al. Successful breast conservation in a patient with epidermolysis bullosa simplex. Breast J. 1999;5:404\u20136. https:\/\/doi.org\/10.1046\/j.1524-4741.1999.98022.x.","journal-title":"Breast J"},{"key":"2567_CR5","first-page":"e3","volume":"13","author":"CR Albornoz","year":"2013","unstructured":"Albornoz CR, Goldstein J, Hespe GE, Sacchini V, Matros E. CASE REPORT successful breast reconstruction in a patient with epidermolysis bullosa. Eplasty. 2013;13:e3.","journal-title":"Eplasty"},{"key":"2567_CR6","doi-asserted-by":"publisher","DOI":"10.1093\/mmcts\/mmv016","author":"N Walcot","year":"2015","unstructured":"Walcot N, Hohenberger W, Lakew F, Batz G, Diegeler A, Perier P. Totally endoscopic set-up for mitral valve repairMultimed. Multimed Man Cardiothorac Surg. 2015. https:\/\/doi.org\/10.1093\/mmcts\/mmv016.","journal-title":"Multimed Man Cardiothorac Surg"},{"key":"2567_CR7","doi-asserted-by":"publisher","first-page":"14","DOI":"10.15420\/icr.2017:30:1","volume":"13","author":"KM Van Praet","year":"2018","unstructured":"Van Praet KM, Stamm C, S\u00fcndermann SH, Meyer A, Unbehaun A, Montagner M, et al. Minimally invasive surgical mitral valve repair: State of the art review. Interv Cardiol. 2018;13:14\u20139. https:\/\/doi.org\/10.15420\/icr.2017:30:1.","journal-title":"Interv Cardiol"},{"key":"2567_CR8","doi-asserted-by":"publisher","first-page":"e72","DOI":"10.1161\/CIR.0000000000000923","volume":"143","author":"CM Otto","year":"2021","unstructured":"Otto CM, Nishimura RA, Bonow RO, Carabello BA, Erwin JP 3rd, Gentile F, et al. 2020 ACC\/AHA guideline for the management of patients with valvular heart disease: a report of the American College of Cardiology\/American Heart Association joint committee on clinical practice guidelines. Circulation. 2021;143:e72\u2013227. https:\/\/doi.org\/10.1161\/CIR.0000000000000923.","journal-title":"Circulation"},{"key":"2567_CR9","doi-asserted-by":"publisher","first-page":"561","DOI":"10.1093\/eurheartj\/ehab395","volume":"43","author":"A Vahanian","year":"2022","unstructured":"Vahanian A, Beyersdorf F, Praz F, Milojevic M, Baldus S, Bauersachs J, et al. 2021 ESC\/EACTS Guidelines for the management of valvular heart disease. Eur Heart J. 2022;43:561\u2013632. https:\/\/doi.org\/10.1093\/eurheartj\/ehab395.","journal-title":"Eur Heart J"},{"key":"2567_CR10","doi-asserted-by":"publisher","first-page":"1331","DOI":"10.1016\/j.athoracsur.2020.06.064","volume":"111","author":"D Szecel","year":"2021","unstructured":"Szecel D, Eurlings R, Rega F, Verbrugghe P, Meuris B. Perceval sutureless aortic valve implantation: midterm outcomes. Ann Thorac Surg. 2021;111:1331\u20137. https:\/\/doi.org\/10.1016\/j.athoracsur.2020.06.064.","journal-title":"Ann Thorac Surg"},{"key":"2567_CR11","doi-asserted-by":"publisher","DOI":"10.5761\/atcs.ra.22-00125","author":"G Colarossi","year":"2022","unstructured":"Colarossi G, Migliorini F, Becker M, Arias JP, Autschbach R, Moza A, et al. Conventional prostheses versus sutureless perceval for aortic valve replacement: a meta-analysis. Ann Thorac Cardiovasc Surg. 2022. https:\/\/doi.org\/10.5761\/atcs.ra.22-00125.","journal-title":"Ann Thorac Cardiovasc Surg"},{"key":"2567_CR12","doi-asserted-by":"publisher","first-page":"2414","DOI":"10.1016\/j.jtcvs.2017.12.154","volume":"155","author":"C Baran","year":"2018","unstructured":"Baran C, Durdu MS, Gumus F, Cakici M, Inan MB, Sirlak M, et al. Sutureless aortic valve replacement with concomitant valvular surgery. J Thorac Cardiovasc Surg. 2018;155:2414\u201322. https:\/\/doi.org\/10.1016\/j.jtcvs.2017.12.154.","journal-title":"J Thorac Cardiovasc Surg"}],"container-title":["Journal of Cardiothoracic Surgery"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1186\/s13019-024-02567-4.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1186\/s13019-024-02567-4\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1186\/s13019-024-02567-4.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,2,20]],"date-time":"2024-02-20T07:16:55Z","timestamp":1708413415000},"score":1,"resource":{"primary":{"URL":"https:\/\/cardiothoracicsurgery.biomedcentral.com\/articles\/10.1186\/s13019-024-02567-4"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024,2,20]]},"references-count":12,"journal-issue":{"issue":"1","published-online":{"date-parts":[[2024,12]]}},"alternative-id":["2567"],"URL":"https:\/\/doi.org\/10.1186\/s13019-024-02567-4","relation":{"has-preprint":[{"id-type":"doi","id":"10.21203\/rs.3.rs-2636503\/v1","asserted-by":"object"}]},"ISSN":["1749-8090"],"issn-type":[{"value":"1749-8090","type":"electronic"}],"subject":[],"published":{"date-parts":[[2024,2,20]]},"assertion":[{"value":"28 February 2023","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"30 January 2024","order":2,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"20 February 2024","order":3,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Declarations"}},{"value":"This case report was approved by the institutional review board of Kobe City Medical Center General Hospital. Verbal informed consent was obtained from the patient for publication of this case report and any accompanying images and recorded in the medical records.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Ethics approval and consent to participate"}},{"value":"Verbal informed consent was obtained from the patient for publication of this case report and accompanying images and recorded in electronic records.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Consent for publication"}},{"value":"All authors declare that they have no competing interests.","order":4,"name":"Ethics","group":{"name":"EthicsHeading","label":"Competing interests"}}],"article-number":"102"}}