{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,28]],"date-time":"2026-09-28T20:46:06Z","timestamp":1790628366817,"version":"4.1.0"},"reference-count":17,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2019,11,8]],"date-time":"2019-11-08T00:00:00Z","timestamp":1573171200000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"},{"start":{"date-parts":[[2019,11,8]],"date-time":"2019-11-08T00:00:00Z","timestamp":1573171200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["J Med Case Reports"],"published-print":{"date-parts":[[2019,12]]},"abstract":"<jats:title>Abstract<\/jats:title>\n              <jats:sec>\n                <jats:title>Background<\/jats:title>\n                <jats:p>Ectodermal dysplasia is a rare genetic disorder that affects ectodermally derived structures, including teeth, nails, hair, and sweat glands. Hypohidrotic ectodermal dysplasia is the most common type, with oligodontia being the most striking dental feature. Prosthetic rehabilitation in children with ectodermal dysplasia is an important step toward improving their overall quality of life. The fixed prosthesis has the advantages of being more stable in the mouth with good child compliance and a good aesthetic outcome.<\/jats:p>\n              <\/jats:sec>\n              <jats:sec>\n                <jats:title>Case presentation<\/jats:title>\n                <jats:p>Our patient was a 5-year-old Middle Eastern boy with oligodontia caused by ectodermal dysplasia. He was managed by fabrication of an upper functional space maintainer and a lower fixed partial denture to restore occlusion, masticatory function, aesthetics, and overall quality of life.<\/jats:p>\n              <\/jats:sec>\n              <jats:sec>\n                <jats:title>Conclusions<\/jats:title>\n                <jats:p>The use of the fixed prosthesis in children is a new and evolving treatment modality that resolves many of the issues caused by removable prostheses. It accommodates jaw growth in the mandible, reduces the need to remake the prosthesis, and has an overall better aesthetic outcome.<\/jats:p>\n              <\/jats:sec>","DOI":"10.1186\/s13256-019-2268-4","type":"journal-article","created":{"date-parts":[[2019,11,8]],"date-time":"2019-11-08T01:02:50Z","timestamp":1573174970000},"update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":26,"title":["Prosthetic rehabilitation with fixed prosthesis of a 5-year-old child with Hypohidrotic Ectodermal Dysplasia and Oligodontia: a case report"],"prefix":"10.1186","volume":"13","author":[{"given":"Reema","family":"AlNuaimi","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mohammad","family":"Mansoor","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2019,11,8]]},"reference":[{"key":"2268_CR1","doi-asserted-by":"publisher","first-page":"351","DOI":"10.1046\/j.1365-2230.2003.01319.x","volume":"28","author":"J Lamartine","year":"2003","unstructured":"Lamartine J. Towards a new classification of ectodermal dysplasia. Clin Exp Dermatol. 2003;28:351\u20135.","journal-title":"Clin Exp Dermatol."},{"key":"2268_CR2","volume-title":"GeneReviews\u00ae [Internet]","author":"JT Wright","year":"2003","unstructured":"Wright JT, Grange DK, Fete M. Hypohidrotic ectodermal dysplasia. In: Adam MP, Ardinger HH, Pagon RA, Wallace SE, LJH B, Stephens K, Amemiya A, editors. GeneReviews\u00ae [Internet]. Seattle: University of Washington, Seattle; 2003. [updated 2017 Jun 1]."},{"key":"2268_CR3","doi-asserted-by":"publisher","first-page":"106","DOI":"10.1016\/S0917-2394(09)70160-0","volume":"19","author":"EB Tuna","year":"2009","unstructured":"Tuna EB, Guven Y, Bozdogan E, Aktoren O. Assessment of dental features in 16 children with hypohidrotic ectodermal dysplasia. Pediatr Dent J. 2009;19:106\u201311.","journal-title":"Pediatr Dent J."},{"key":"2268_CR4","doi-asserted-by":"publisher","first-page":"340","DOI":"10.4172\/2161-1122.1000340","volume":"5","author":"R Grover","year":"2015","unstructured":"Grover R, Manjul M. Prosthodontic management of children with ectodermal dysplasia: review of literature. Dentistry. 2015;5:340. \nhttps:\/\/doi.org\/10.4172\/2161-1122.1000340\n\n.","journal-title":"Dentistry."},{"key":"2268_CR5","first-page":"243","volume":"24","author":"AJ Nowak","year":"1988","unstructured":"Nowak AJ. Dental treatment for patients with ectodermal dysplasia. Birth Defects. 1988;24:243\u201352.","journal-title":"Birth Defects"},{"key":"2268_CR6","first-page":"25","volume":"38","author":"American Academy of Pediatric Dentistry","year":"2015","unstructured":"American Academy of Pediatric Dentistry. Policy on the dental home. American Academy of Pediatric Dentistry oral health policies reference manual. 2015;38:25\u20136.","journal-title":"American Academy of Pediatric Dentistry oral health policies reference manual"},{"key":"2268_CR7","doi-asserted-by":"publisher","first-page":"541","DOI":"10.1016\/S0022-3913(96)90015-3","volume":"76","author":"MA Pigno","year":"1996","unstructured":"Pigno MA, Blackman RB, Cronin RJ, Cavazos E. Prosthodontic management of ectodermal dysplasia: a review of the literature. J Prosthet Dent. 1996;76:541\u20135.","journal-title":"J Prosthet Dent"},{"key":"2268_CR8","doi-asserted-by":"publisher","first-page":"555","DOI":"10.1111\/joor.12638","volume":"45","author":"D Schnabl","year":"2018","unstructured":"Schnabl D, Grunert I, Schmuth M, Kapferer-Seebacher I. Prosthetic rehabilitation of patients with hypohidrotic ectodermal dysplasia: a systematic review. J Oral Rehabil. 2018;45:555\u201370.","journal-title":"J Oral Rehabil"},{"issue":"2","key":"2268_CR9","first-page":"E119","volume":"13","author":"A Pipa Vallejo","year":"2008","unstructured":"Pipa Vallejo A, L\u00f3pez Arranz Monje E, Gonz\u00e1lez Garc\u00eda M, Mart\u00ednez Fern\u00e1ndez M, Blanco Moreno Alvarez Buylla F. Treatment with removable prosthesis in hypohidrotic ectodermal dysplasia: a clinical case. Med Oral Patol Oral Cir Bucal. 2008;13(2):E119\u201323.","journal-title":"Med Oral Patol Oral Cir Bucal"},{"key":"2268_CR10","first-page":"116","volume":"65","author":"L Franchi","year":"1998","unstructured":"Franchi L, Branchi R, Tollaro I. Craniofacial changes following early prosthetic treatment in a case of hypohidrotic ectodermal dysplasia with complete anodontia. ASDC J Dent Child. 1998;65:116\u201321.","journal-title":"ASDC J Dent Child"},{"key":"2268_CR11","doi-asserted-by":"crossref","unstructured":"Van Waas MA, Jonkman RE, Kalk W, Van 't Hof MA, Plooji J, Van OS JH. Differences two years after tooth extraction in mandibular bone reduction in patients treated with immediate overdentures or with immediate complete dentures. J Dent Res. 1993;72:1001-4.","DOI":"10.1177\/00220345930720060101"},{"key":"2268_CR12","first-page":"139","volume":"20","author":"L Ou-Yang","year":"2019","unstructured":"Ou-Yang L, Li T, Tsai A. Early prosthodontics intervention on two three-year-old twin girls with ectodermal dysplasia. Eur J Paediatr Dent. 2019;20:139\u201342.","journal-title":"Eur J Paediatr Dent"},{"key":"2268_CR13","doi-asserted-by":"publisher","first-page":"140","DOI":"10.1111\/j.1600-0501.2006.01180.x","volume":"18","author":"F Kramer","year":"2007","unstructured":"Kramer F, Baethge C, Tschernitschek H. Implants in children with ectodermal dysplasia: a case report and literature review. Clin Oral Implants Res. 2007;18:140\u20136.","journal-title":"Clin Oral Implants Res"},{"key":"2268_CR14","first-page":"41","volume":"22","author":"GV Barrow","year":"1952","unstructured":"Barrow GV, White JR. Developmental changes of the maxillary and mandibular dental arches. Angle Orthod. 1952;22:41\u20136.","journal-title":"Angle Orthod"},{"key":"2268_CR15","volume-title":"Parameters of oral health care for individuals affected by ectodermal dysplasia syndromes","author":"National Foundation for Ectodermal Dysplasias","year":"2003","unstructured":"National Foundation for Ectodermal Dysplasias. Parameters of oral health care for individuals affected by ectodermal dysplasia syndromes. Mascoutah: National Foundation for Ectodermal Dysplasias; 2003."},{"key":"2268_CR16","first-page":"55","volume":"9","author":"RJ Cronin Jr","year":"1994","unstructured":"Cronin RJ Jr, Oesterle LJ, Ranly DM. 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J Prosthet Dent. 2001;86:342\u20137.","journal-title":"J Prosthet Dent"}],"container-title":["Journal of Medical Case Reports"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1186\/s13256-019-2268-4.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/article\/10.1186\/s13256-019-2268-4\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1186\/s13256-019-2268-4.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2020,11,7]],"date-time":"2020-11-07T00:46:53Z","timestamp":1604710013000},"score":1,"resource":{"primary":{"URL":"https:\/\/jmedicalcasereports.biomedcentral.com\/articles\/10.1186\/s13256-019-2268-4"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2019,11,8]]},"references-count":17,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2019,12]]}},"alternative-id":["2268"],"URL":"https:\/\/doi.org\/10.1186\/s13256-019-2268-4","relation":{},"ISSN":["1752-1947"],"issn-type":[{"value":"1752-1947","type":"electronic"}],"subject":[],"published":{"date-parts":[[2019,11,8]]},"assertion":[{"value":"15 October 2018","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"22 September 2019","order":2,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"8 November 2019","order":3,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"Not applicable.","order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Ethics approval and consent to participate"}},{"value":"Written informed consent was obtained from the patient\u2019s legal guardian for publication of this case report and any accompanying images. A copy of the written consent is available for review by the Editor-in-Chief of this journal.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Consent for publication"}},{"value":"The authors declare that they have no competing interests.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Competing interests"}}],"article-number":"329"}}