{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,5,14]],"date-time":"2025-05-14T16:50:30Z","timestamp":1747241430583},"reference-count":7,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2021,4,1]],"date-time":"2021-04-01T00:00:00Z","timestamp":1617235200000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"},{"start":{"date-parts":[[2021,4,1]],"date-time":"2021-04-01T00:00:00Z","timestamp":1617235200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["J Med Case Reports"],"published-print":{"date-parts":[[2021,12]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:sec>\n                <jats:title>Background<\/jats:title>\n                <jats:p>Unilateral pulmonary artery discontinuity is a rare malformation that is associated with other intracardiac abnormalities. Cases accompanied by other cardiac abnormalities are often missed on prenatal echocardiography. The prenatal diagnosis of isolated unilateral pulmonary artery discontinuity can also be delayed. However, undiagnosed this malformation would have an effect on further prognosis. We report our case of a prenatal diagnosis of pulmonary atresia with ventricular septal defect and left pulmonary artery discontinuity.<\/jats:p>\n              <\/jats:sec><jats:sec>\n                <jats:title>Case presentation<\/jats:title>\n                <jats:p>A 33-year-old Asian woman visited our institution at 24\u00a0weeks of gestation because of suspected fetal congenital heart disease. Fetal echocardiography revealed a small atretic main pulmonary artery giving rise to the right pulmonary artery without bifurcation and the left pulmonary artery arising from the ductus arteriosus originating from the left subclavian artery. The neonate was delivered by cesarean section at 37<jats:sup>6\/7<\/jats:sup> weeks of gestation. Postnatal echocardiography and multidetector computed tomography showed a right aortic arch, with the small right pulmonary artery originating from the atretic main pulmonary artery and the left pulmonary artery originating from the left subclavian artery. Patency of the ductus arteriosus from the left subclavian artery was maintained with prostaglandin E1. Right ventricular outflow tract reconstruction and pulmonary angioplasty with Gore-Tex graft patch was performed 25th day after birth. Unfortunately, the neonate died because of right heart failure 8\u00a0days postoperation.<\/jats:p>\n              <\/jats:sec><jats:sec>\n                <jats:title>Conclusion<\/jats:title>\n                <jats:p>There is a possibility that both pulmonary arteries do not arise from the same great artery (main pulmonary artery or common arterial trunk). Therefore, clinicians should check the origin of both pulmonary arteries.<\/jats:p>\n              <\/jats:sec>","DOI":"10.1186\/s13256-021-02750-4","type":"journal-article","created":{"date-parts":[[2021,4,3]],"date-time":"2021-04-03T15:02:42Z","timestamp":1617462162000},"update-policy":"http:\/\/dx.doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":3,"title":["Pulmonary atresia with a ventricular septal defect and left pulmonary artery discontinuity: a case report\u00a0"],"prefix":"10.1186","volume":"15","author":[{"given":"Hyun-Hwa","family":"Cha","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hae Min","family":"Kim","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Won Joon","family":"Seong","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2021,4,1]]},"reference":[{"key":"2750_CR1","first-page":"24","volume":"2","author":"DR Turner","year":"2000","unstructured":"Turner DR, Vincent JA, Epstein ML. Isolated right pulmonary discontinuity. Images Paediatr Cardiol. 2000;2:24\u201330.","journal-title":"Images Paediatr Cardiol"},{"key":"2750_CR2","doi-asserted-by":"publisher","first-page":"1329","DOI":"10.1016\/j.jtcvs.2006.12.041","volume":"133","author":"M Nathan","year":"2007","unstructured":"Nathan M, Rimmer D, Piercey G, del NIdo PJ, Mayer JE, Bacha EA, et\u00a0al. Early repair of hemitruncus: excellent early and late outcomes. J Thorac Cardiovasc Surg. 2007;133:1329\u201335.","journal-title":"J Thorac Cardiovasc Surg."},{"key":"2750_CR3","doi-asserted-by":"crossref","first-page":"232470961453613","DOI":"10.1177\/2324709614536139","volume":"27","author":"LJ Haywood","year":"2014","unstructured":"Haywood LJ, Chakryan Y, Kim D, Boltzer T, Rivas G, Shavelle D. Abnormal origin of the right pulmonary artery from ascending aorta (Hemitruncus arteriosus). J Investig Med High Impact Case Rep. 2014;27:2324709614536139.","journal-title":"J Investig Med High Impact Case Rep."},{"key":"2750_CR4","doi-asserted-by":"publisher","first-page":"27","DOI":"10.1186\/s13052-018-0465-1","volume":"44","author":"A Raymond","year":"2018","unstructured":"Raymond A, Pedretti E, Privitera G, Cicero C, Biasucci G. Neonatal diagnosis of isolated absence of the right pulmonary artery: a case report and review of the literature. Ital J Pediatr. 2018;44:27.","journal-title":"Ital J Pediatr."},{"key":"2750_CR5","doi-asserted-by":"publisher","first-page":"670","DOI":"10.1378\/chest.108.3.670","volume":"108","author":"D Bouros","year":"1995","unstructured":"Bouros D, Pare P, Panagou P, Tsintiris K, Siafakas N. The varied manifestation of pulmonary artery agenesis in adulthood. Chest. 1995;108:670\u20136.","journal-title":"Chest"},{"key":"2750_CR6","doi-asserted-by":"publisher","first-page":"178","DOI":"10.1136\/hrt.52.2.178","volume":"52","author":"P Presbitero","year":"1984","unstructured":"Presbitero P, Bull C, Hawarth SG, de Leval MR. Absent or occult pulmonary artery. Br Heart J. 1984;52:178\u201385.","journal-title":"Br Heart J"},{"key":"2750_CR7","doi-asserted-by":"publisher","first-page":"2230","DOI":"10.1016\/j.athoracsur.2013.02.057","volume":"96","author":"AY El-Hattab","year":"2013","unstructured":"El-Hattab AY, Calcaterra D, Parekh KR, Rossi NP, Davis JE, Turek JW. Semiautologous repair for congenital discontinuous right pulmonary artery. Ann Thorc Surg. 2013;96:2230\u20131.","journal-title":"Ann Thorc Surg."}],"container-title":["Journal of Medical Case Reports"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1186\/s13256-021-02750-4.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/article\/10.1186\/s13256-021-02750-4\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1186\/s13256-021-02750-4.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,4,3]],"date-time":"2021-04-03T15:03:28Z","timestamp":1617462208000},"score":1,"resource":{"primary":{"URL":"https:\/\/jmedicalcasereports.biomedcentral.com\/articles\/10.1186\/s13256-021-02750-4"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2021,4,1]]},"references-count":7,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2021,12]]}},"alternative-id":["2750"],"URL":"https:\/\/doi.org\/10.1186\/s13256-021-02750-4","relation":{},"ISSN":["1752-1947"],"issn-type":[{"value":"1752-1947","type":"electronic"}],"subject":[],"published":{"date-parts":[[2021,4,1]]},"assertion":[{"value":"10 December 2020","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"22 February 2021","order":2,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"1 April 2021","order":3,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"Written informed consent was obtained from the parents for publications of this case report and accompanying images.","order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Ethical approval and consent to participate"}},{"value":"Written informed consent was obtained from the patient for publication of this case report and any accompanying images. A copy of the written consent is available for review by the Editor-in-Chief of this Journal.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Consent for publication"}},{"value":"The authors declare that they have no competing interests.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Competing interests"}}],"article-number":"190"}}