{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,7,12]],"date-time":"2025-07-12T22:45:27Z","timestamp":1752360327107,"version":"3.37.3"},"reference-count":5,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2021,6,7]],"date-time":"2021-06-07T00:00:00Z","timestamp":1623024000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"},{"start":{"date-parts":[[2021,6,7]],"date-time":"2021-06-07T00:00:00Z","timestamp":1623024000000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["CVIR Endovasc"],"published-print":{"date-parts":[[2021,12]]},"abstract":"Abstract<\/jats:title>\n Background<\/jats:title>\n Anomalies of the portal venous system can be congenital or acquired, the latter being related to spontaneous thrombosis or iatrogenic alterations such as complications of perinatal catheterization of the umbilical vein. These conditions can be clinically silent for years and then manifest abruptly causing severe clinical emergencies.<\/jats:p>\n <\/jats:sec>\n Case presentation<\/jats:title>\n This case report describes the diagnosis and interventional management of a singular abnormality in the portal venous system of an 8-year-old female that led to severe portal hypertension and acute variceal bleeding. Peculiar imaging findings were not pathognomonic for any of the known congenital and acquired portal vein anomalies: absence of a normal extrahepatic portal vein; splenic and mesenteric veins merging into a dilated left gastric vein; presence of an aberrant mesenteric venous collateral with a stenotic connection with the intrahepatic right portal branch; and absence of porto-systemic shunt. The case was successfully managed with percutaneous transhepatic portography and angioplasty.<\/jats:p>\n <\/jats:sec>\n Conclusions<\/jats:title>\n Prompt non-invasive imaging characterization allowed to understand the singular vascular abnormality and mini-invasive interventional radiology management resolved portal hypertension and variceal bleeding.<\/jats:p>\n <\/jats:sec>","DOI":"10.1186\/s42155-021-00239-1","type":"journal-article","created":{"date-parts":[[2021,6,7]],"date-time":"2021-06-07T05:02:38Z","timestamp":1623042158000},"update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":1,"title":["Percutaneous transhepatic treatment of a unique portal vein malformation with portal hypertension in a pediatric patient"],"prefix":"10.1186","volume":"4","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-4935-8110","authenticated-orcid":false,"given":"Paolo","family":"Marra","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ludovico","family":"Dulcetta","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Claudia","family":"Pellegrinelli","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Lorenzo","family":"D\u2019Antiga","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Sandro","family":"Sironi","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2021,6,7]]},"reference":[{"issue":"3","key":"239_CR1","doi-asserted-by":"publisher","first-page":"842","DOI":"10.1148\/rg.2019180146","volume":"39","author":"BK Albers","year":"2019","unstructured":"Albers BK, Khanna G (2019) Vascular anomalies of the pediatric liver. RadioGraphics 39(3):842\u2013856. https:\/\/doi.org\/10.1148\/rg.2019180146","journal-title":"RadioGraphics"},{"issue":"1","key":"239_CR2","doi-asserted-by":"publisher","first-page":"38","DOI":"10.1186\/s13244-019-0716-8","volume":"10","author":"C Carneiro","year":"2019","unstructured":"Carneiro C, Brito J, Bilreiro C, Barros M, Bahia C, Santiago I, Caseiro-Alves F (2019) All about portal vein: a pictorial display to anatomy, variants and physiopathology. Insights Imaging 10(1):38. https:\/\/doi.org\/10.1186\/s13244-019-0716-8","journal-title":"Insights Imaging"},{"issue":"2","key":"239_CR3","doi-asserted-by":"publisher","first-page":"87","DOI":"10.1007\/s00247-005-0010-4","volume":"36","author":"JAG Corness","year":"2006","unstructured":"Corness JAG, McHugh K, Roebuck DJ, Taylor AM (2006) The portal vein in children: radiological review of congenital anomalies and acquired abnormalities. Pediatr Radiol 36(2):87\u201396. https:\/\/doi.org\/10.1007\/s00247-005-0010-4","journal-title":"Pediatr Radiol"},{"issue":"5","key":"239_CR4","doi-asserted-by":"publisher","first-page":"788","DOI":"10.1016\/j.jvir.2019.08.007","volume":"31","author":"S Rajeswaran","year":"2020","unstructured":"Rajeswaran S, Johnston A, Green J, Riaz A, Thornburg B, Mouli S, Lautz T, Lemoine C, Superina R, Donaldson J (2020) Abernethy malformations: evaluation and management of congenital portosystemic shunts. J Vasc Interv Radiol 31(5):788\u2013794. https:\/\/doi.org\/10.1016\/j.jvir.2019.08.007","journal-title":"J Vasc Interv Radiol"},{"issue":"39","key":"239_CR5","doi-asserted-by":"publisher","first-page":"5969","DOI":"10.3748\/wjg.14.5969","volume":"14","author":"G-HHL-G Shen","year":"2008","unstructured":"Shen G-HHL-G, Zhu JYJ-HMY-F (2008) Insight into congenital absence of the portal vein: is it rare? World J Gastroenterol 14(39):5969. https:\/\/doi.org\/10.3748\/wjg.14.5969","journal-title":"World J Gastroenterol"}],"container-title":["CVIR Endovascular"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1186\/s42155-021-00239-1.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1186\/s42155-021-00239-1\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1186\/s42155-021-00239-1.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,6,7]],"date-time":"2021-06-07T05:02:57Z","timestamp":1623042177000},"score":1,"resource":{"primary":{"URL":"https:\/\/CVIRendovasc.springeropen.com\/articles\/10.1186\/s42155-021-00239-1"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2021,6,7]]},"references-count":5,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2021,12]]}},"alternative-id":["239"],"URL":"https:\/\/doi.org\/10.1186\/s42155-021-00239-1","relation":{},"ISSN":["2520-8934"],"issn-type":[{"type":"electronic","value":"2520-8934"}],"subject":[],"published":{"date-parts":[[2021,6,7]]},"assertion":[{"value":"16 March 2021","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"28 May 2021","order":2,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"7 June 2021","order":3,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Declarations"}},{"value":"Due to the retrospective nature of the case report the need for approval was waived by the Ethical Committee.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Ethics approval and consent to participate"}},{"value":"Written informed consent was obtained from the patient for publication of this case report and any accompanying images.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Consent for publication"}},{"value":"The authors declare that they have no competing interests.","order":4,"name":"Ethics","group":{"name":"EthicsHeading","label":"Competing interests"}}],"article-number":"47"}}