{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,11,14]],"date-time":"2025-11-14T17:45:53Z","timestamp":1763142353510,"version":"3.37.3"},"reference-count":10,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2024,9,20]],"date-time":"2024-09-20T00:00:00Z","timestamp":1726790400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"},{"start":{"date-parts":[[2024,9,20]],"date-time":"2024-09-20T00:00:00Z","timestamp":1726790400000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"}],"funder":[{"DOI":"10.13039\/501100012681","name":"Universit\u00e4tsklinikum K\u00f6ln","doi-asserted-by":"crossref","id":[{"id":"10.13039\/501100012681","id-type":"DOI","asserted-by":"crossref"}]}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Neurol. Res. Pract."],"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Guillain-Barr\u00e9 syndrome is the most common acute inflammatory demyelinating peripheral nerve condition. Occasionally, other autoimmune conditions can mimic Guillain-Barr\u00e9 syndrome but may require different diagnostic workup and treatment. We report here two patients with Evans syndrome, a rare hematological autoimmune condition who developed a subacute inflammatory radiculopathy. Similarities and distinguishing clinical and diagnostic features are discussed.<\/jats:p>","DOI":"10.1186\/s42466-024-00344-1","type":"journal-article","created":{"date-parts":[[2024,9,20]],"date-time":"2024-09-20T03:38:59Z","timestamp":1726803539000},"update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":1,"title":["Differential diagnosis of Guillain-Barr\u00e9 syndrome: steroid-responsive radiculopathy in Evans syndrome"],"prefix":"10.1186","volume":"6","author":[{"given":"Thomas","family":"Schulten","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ansgar","family":"Meyer","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Utz","family":"Krug","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-6205-2293","authenticated-orcid":false,"given":"Helmar C.","family":"Lehmann","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2024,9,20]]},"reference":[{"key":"344_CR1","doi-asserted-by":"publisher","first-page":"3851","DOI":"10.3390\/jcm9123851","volume":"9","author":"S Audia","year":"2020","unstructured":"Audia, S., Grienay, N., Mounier, M., Michel, M., & Bonnotte, B. (2020). Evans\u2019 syndrome: From diagnosis to treatment. J Clin Med, 9, 3851.","journal-title":"J Clin Med"},{"key":"344_CR2","doi-asserted-by":"publisher","first-page":"171","DOI":"10.2147\/JBM.S176144","volume":"9","author":"JC Jaime-P\u00e9rez","year":"2018","unstructured":"Jaime-P\u00e9rez, J. C., Aguilar-Calder\u00f3n, P. E., Salazar-Cavazos, L., & G\u00f3mez-Almaguer, D. (2018). Evans syndrome: Clinical perspectives, biological insights and treatment modalities. J Blood Med, 9, 171\u2013184.","journal-title":"J Blood Med"},{"key":"344_CR3","doi-asserted-by":"publisher","first-page":"361","DOI":"10.1159\/000209461","volume":"34","author":"FA Ala","year":"1965","unstructured":"Ala, F. A., & Shearman, D. J. (1965). A case of autoimmune haemolytic anaemia, Thrombocytopenia and Landry-Guillain-Barr\u00e9 syndrome. Acta Haematologica, 34, 361\u2013369.","journal-title":"Acta Haematologica"},{"key":"344_CR4","first-page":"1600","volume":"12","author":"P Blouin","year":"2005","unstructured":"Blouin, P., Auvrignon, A., Pagnier, A., Thuret, I., Antoni, G., Bader-Meunier, B., et al. (2005). [Evans\u2019 syndrome: A retrospective study from the ship (French Society of Pediatric Hematology and Immunology) (36 cases)]. Arch Pediatr Organe off Soc Francaise Pediatr, 12, 1600\u20131607.","journal-title":"Arch Pediatr Organe off Soc Francaise Pediatr"},{"key":"344_CR5","doi-asserted-by":"publisher","first-page":"189","DOI":"10.1080\/1042819031000123474","volume":"45","author":"V Mail\u00e4nder","year":"2004","unstructured":"Mail\u00e4nder, V., Gleisner, B., Blau, I. W., & Thiel, E. (2004). Guillain-Barre-Strohl syndrome unraveled as paraneoplastic syndrome of B-cell acute lymphoblastic leukemia in a patient with preceding common variable immunodeficiency syndrome with Evans syndrome. Leukaemia & Lymphoma, 45, 189\u2013192.","journal-title":"Leukaemia & Lymphoma"},{"key":"344_CR6","doi-asserted-by":"publisher","first-page":"730","DOI":"10.1212\/01.WNL.0000134606.50529.C7","volume":"63","author":"H Knecht","year":"2004","unstructured":"Knecht, H., Baumberger, M., Tob\u00f2n, A., & Steck, A. (2004). Sustained remission of CIDP associated with Evans syndrome. Neurology, 63, 730\u2013732.","journal-title":"Neurology"},{"key":"344_CR7","first-page":"374","volume":"1","author":"T Guez","year":"1992","unstructured":"Guez, T., Smadja, D., Mas, J. L., & Sicard, D. (1992). Chronic inflammatory demyelinating polyradiculoneuropathy associated with Evans\u2019 syndrome. Eur J Med, 1, 374\u2013376.","journal-title":"Eur J Med"},{"key":"344_CR8","doi-asserted-by":"publisher","first-page":"2866","DOI":"10.1093\/brain\/awy232","volume":"141","author":"AY Doets","year":"2018","unstructured":"Doets, A. Y., Verboon, C., van den Berg, B., Harbo, T., Cornblath, D. R., Willison, H. J., et al. (2018). Regional variation of Guillain-Barr\u00e9 syndrome. Brain J Neurol, 141, 2866\u20132877.","journal-title":"Brain J Neurol"},{"key":"344_CR9","doi-asserted-by":"publisher","first-page":"1214","DOI":"10.1016\/S0140-6736(21)00517-1","volume":"397","author":"N Shahrizaila","year":"2021","unstructured":"Shahrizaila, N., Lehmann, H. C., & Kuwabara, S. (2021). Guillain-Barr\u00e9 syndrome. Lancet, 397, 1214\u20131228.","journal-title":"Lancet"},{"key":"344_CR10","doi-asserted-by":"publisher","first-page":"370","DOI":"10.1007\/s00415-011-6169-8","volume":"259","author":"HC Lehmann","year":"2012","unstructured":"Lehmann, H. C., Macht, S., Jander, S., Hartung, H. P., & Methner, A. (2012). Guillain-Barr\u00e9 syndrome variant with prominent facial diplegia, limb paresthesia, and brisk reflexes. Journal of Neurology, 259, 370\u2013371.","journal-title":"Journal of Neurology"}],"container-title":["Neurological Research and Practice"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1186\/s42466-024-00344-1.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1186\/s42466-024-00344-1\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1186\/s42466-024-00344-1.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,9,20]],"date-time":"2024-09-20T03:42:08Z","timestamp":1726803728000},"score":1,"resource":{"primary":{"URL":"https:\/\/neurolrespract.biomedcentral.com\/articles\/10.1186\/s42466-024-00344-1"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024,9,20]]},"references-count":10,"journal-issue":{"issue":"1","published-online":{"date-parts":[[2024,12]]}},"alternative-id":["344"],"URL":"https:\/\/doi.org\/10.1186\/s42466-024-00344-1","relation":{},"ISSN":["2524-3489"],"issn-type":[{"type":"electronic","value":"2524-3489"}],"subject":[],"published":{"date-parts":[[2024,9,20]]},"assertion":[{"value":"14 May 2024","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"30 August 2024","order":2,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"20 September 2024","order":3,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Declarations"}},{"value":"Not applicable.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Ethics approval and consent to participate"}},{"value":"Obtained.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Consent for publication"}},{"value":"Not applicable.","order":4,"name":"Ethics","group":{"name":"EthicsHeading","label":"Competing interests"}}],"article-number":"45"}}