{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,4]],"date-time":"2026-10-04T08:46:33Z","timestamp":1791103593403,"version":"4.1.0"},"reference-count":42,"publisher":"Springer Science and Business Media LLC","issue":"6","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pediatr Res"],"published-print":{"date-parts":[[2008,6]]},"DOI":"10.1203\/pdr.0b013e31816c9013","type":"journal-article","created":{"date-parts":[[2008,5,23]],"date-time":"2008-05-23T03:22:17Z","timestamp":1211512937000},"page":"702-707","source":"Crossref","is-referenced-by-count":76,"title":["Increased de novo Lipogenesis and Delayed Conversion of Large VLDL into Intermediate Density Lipoprotein Particles Contribute to Hyperlipidemia in Glycogen Storage Disease Type 1a"],"prefix":"10.1038","volume":"63","author":[{"given":"Robert H J","family":"Bandsma","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Berthil H","family":"Prinsen","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Monique","family":"de Sain-van der Velden","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jan-Peter","family":"Rake","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Theo","family":"Boer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"G Peter A","family":"Smit","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Dirk-Jan","family":"Reijngoud","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Folkert","family":"Kuipers","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","reference":[{"key":"pr2008132-bib1","unstructured":""},{"key":"pr2008132-bib2","doi-asserted-by":"crossref","first-page":"215","DOI":"10.1016\/S0022-2275(20)38543-6","volume":"29","author":"Levy E","year":"1988","journal-title":"J Lipid Res"},{"key":"pr2008132-bib3","doi-asserted-by":"crossref","first-page":"381","DOI":"10.1007\/BF02537265","volume":"22","author":"Levy E","year":"1987","journal-title":"Lipids"},{"key":"pr2008132-bib4","doi-asserted-by":"crossref","first-page":"S56","DOI":"10.1007\/BF02072090","volume":"152","author":"Chen YT","year":"1993","journal-title":"Eur J Pediatr"},{"key":"pr2008132-bib5","doi-asserted-by":"crossref","first-page":"327","DOI":"10.1203\/00006450-198904000-00002","volume":"25","author":"Fernandes J","year":"1989","journal-title":"Pediatr Res"},{"key":"pr2008132-bib6","doi-asserted-by":"crossref","first-page":"256","DOI":"10.1067\/mpd.2002.121382","volume":"140","author":"Bandsma RH","year":"2002","journal-title":"J Pediatr"},{"key":"pr2008132-bib7","doi-asserted-by":"crossref","first-page":"19351","DOI":"10.1074\/jbc.272.31.19351","volume":"272","author":"Wang SL","year":"1997","journal-title":"J Biol Chem"},{"key":"pr2008132-bib8","doi-asserted-by":"crossref","first-page":"1052","DOI":"10.1016\/0026-0495(95)90104-3","volume":"44","author":"Watts GF","year":"1995","journal-title":"Metabolism"},{"key":"pr2008132-bib9","doi-asserted-by":"crossref","first-page":"83","DOI":"10.1016\/S0021-9150(97)00153-6","volume":"135","author":"Riches FM","year":"1997","journal-title":"Atherosclerosis"},{"key":"pr2008132-bib10","doi-asserted-by":"crossref","first-page":"833","DOI":"10.2337\/diabetes.42.6.833","volume":"42","author":"Lewis GF","year":"1993","journal-title":"Diabetes"},{"key":"pr2008132-bib11","doi-asserted-by":"crossref","first-page":"114","DOI":"10.1203\/00006450-197402000-00008","volume":"8","author":"Forget PP","year":"1974","journal-title":"Pediatr Res"},{"key":"pr2008132-bib12","doi-asserted-by":"crossref","first-page":"527","DOI":"10.1023\/A:1012407609063","volume":"24","author":"Wierzbicki AS","year":"2001","journal-title":"J Inherit Metab Dis"},{"key":"pr2008132-bib13","doi-asserted-by":"crossref","first-page":"S20","DOI":"10.1007\/BF02679990","volume":"161","author":"Rake JP","year":"2002","journal-title":"Eur J Pediatr"},{"key":"pr2008132-bib14","first-page":"E814","volume":"265","author":"Hellerstein MK","year":"1993","journal-title":"Am J Physiol"},{"key":"pr2008132-bib15","doi-asserted-by":"crossref","first-page":"E136","DOI":"10.1152\/ajpcell.1993.264.1.C136","volume":"264","author":"Neese RA","year":"1993","journal-title":"Am J Physiol"},{"key":"pr2008132-bib16","doi-asserted-by":"crossref","first-page":"994","DOI":"10.1046\/j.1523-1755.1998.00729.x","volume":"53","author":"de Sain-van der Velden MG","year":"1998","journal-title":"Kidney Int"},{"key":"pr2008132-bib17","doi-asserted-by":"crossref","first-page":"2591","DOI":"10.2337\/diabetes.50.11.2591","volume":"50","author":"Bandsma RH","year":"2001","journal-title":"Diabetes"},{"key":"pr2008132-bib18","doi-asserted-by":"crossref","first-page":"1261","DOI":"10.1016\/S0022-2275(20)37908-6","volume":"24","author":"Egusa G","year":"1983","journal-title":"J Lipid Res"},{"key":"pr2008132-bib19","doi-asserted-by":"crossref","first-page":"308","DOI":"10.1006\/abio.1998.2908","volume":"265","author":"de Sain-van der Velden MG","year":"1998","journal-title":"Anal Biochem"},{"key":"pr2008132-bib20","doi-asserted-by":"crossref","first-page":"354","DOI":"10.1016\/0014-5793(91)80330-6","volume":"280","author":"Hu&scaron;ek P","year":"1991","journal-title":"FEBS Lett"},{"key":"pr2008132-bib21","doi-asserted-by":"crossref","first-page":"80","DOI":"10.1006\/abio.1997.2535","volume":"258","author":"Ackermans MT","year":"1998","journal-title":"Anal Biochem"},{"key":"pr2008132-bib22","doi-asserted-by":"crossref","first-page":"2063","DOI":"10.1016\/S0022-2275(20)35348-7","volume":"34","author":"Faix D","year":"1993","journal-title":"J Lipid Res"},{"key":"pr2008132-bib23","first-page":"E1023","volume":"267","author":"Neese RA","year":"1994","journal-title":"Am J Physiol"},{"key":"pr2008132-bib24","doi-asserted-by":"crossref","first-page":"1341","DOI":"10.1194\/jlr.M300023-JLR200","volume":"44","author":"Prinsen BH","year":"2003","journal-title":"J Lipid Res"},{"key":"pr2008132-bib25","doi-asserted-by":"crossref","first-page":"35832","DOI":"10.1074\/jbc.274.50.35832","volume":"274","author":"Shimano H","year":"1999","journal-title":"J Biol Chem"},{"key":"pr2008132-bib26","doi-asserted-by":"crossref","first-page":"35299","DOI":"10.1074\/jbc.273.52.35299","volume":"273","author":"Shimomura I","year":"1998","journal-title":"J Biol Chem"},{"key":"pr2008132-bib27","doi-asserted-by":"crossref","first-page":"10691","DOI":"10.1074\/jbc.M109771200","volume":"277","author":"Tobin KA","year":"2002","journal-title":"J Biol Chem"},{"key":"pr2008132-bib28","doi-asserted-by":"crossref","first-page":"16033","DOI":"10.1074\/jbc.M101557200","volume":"276","author":"Koo SH","year":"2001","journal-title":"J Biol Chem"},{"key":"pr2008132-bib29","doi-asserted-by":"crossref","first-page":"405","DOI":"10.1146\/annurev.nutr.17.1.405","volume":"17","author":"Towle HC","year":"1997","journal-title":"Annu Rev Nutr"},{"key":"pr2008132-bib30","doi-asserted-by":"crossref","first-page":"5107","DOI":"10.1073\/pnas.0730817100","volume":"100","author":"Kabashima T","year":"2003","journal-title":"Proc Natl Acad Sci U S A"},{"key":"pr2008132-bib31","doi-asserted-by":"crossref","first-page":"26461","DOI":"10.1074\/jbc.271.43.26461","volume":"271","author":"Sato R","year":"1996","journal-title":"J Biol Chem"},{"key":"pr2008132-bib32","doi-asserted-by":"crossref","first-page":"253","DOI":"10.1111\/j.1365-2362.1990.tb01852.x","volume":"20","author":"Levy E","year":"1990","journal-title":"Eur J Clin Invest"},{"key":"pr2008132-bib33","doi-asserted-by":"crossref","first-page":"555","DOI":"10.1055\/s-2007-1019077","volume":"14","author":"Asayama K","year":"1982","journal-title":"Horm Metab Res"},{"key":"pr2008132-bib34","doi-asserted-by":"crossref","first-page":"755","DOI":"10.1007\/s00125-005-0125-z","volume":"49","author":"Adiels M","year":"2006","journal-title":"Diabetologia"},{"key":"pr2008132-bib35","doi-asserted-by":"crossref","first-page":"463","DOI":"10.1016\/S0046-8177(74)80024-9","volume":"5","author":"McAdams AJ","year":"1974","journal-title":"Hum Pathol"},{"key":"pr2008132-bib36","doi-asserted-by":"crossref","first-page":"E829","DOI":"10.1152\/ajpendo.00165.2005","volume":"289","author":"Grefhorst A","year":"2005","journal-title":"Am J Physiol Endocrinol Metab"},{"key":"pr2008132-bib37","doi-asserted-by":"crossref","first-page":"257","DOI":"10.1136\/gut.23.4.257","volume":"23","author":"Johnston DG","year":"1982","journal-title":"Gut"},{"key":"pr2008132-bib38","doi-asserted-by":"crossref","first-page":"G967","DOI":"10.1152\/ajpgi.2000.278.6.G967","volume":"278","author":"Shangraw RE","year":"2000","journal-title":"Am J Physiol Gastrointest Liver Physiol"},{"key":"pr2008132-bib39","doi-asserted-by":"crossref","first-page":"363","DOI":"10.1016\/S0021-9150(00)00409-3","volume":"153","author":"de Man FH","year":"2000","journal-title":"Atherosclerosis"},{"key":"pr2008132-bib40","doi-asserted-by":"crossref","first-page":"398","DOI":"10.1016\/S0022-3476(05)82052-9","volume":"119","author":"Greene HL","year":"1991","journal-title":"J Pediatr"},{"key":"pr2008132-bib41","doi-asserted-by":"crossref","first-page":"36B","DOI":"10.1016\/S0002-9149(98)00036-8","volume":"81","author":"Vega GL","year":"1998","journal-title":"Am J Cardiol"},{"key":"pr2008132-bib42","doi-asserted-by":"crossref","first-page":"1157","DOI":"10.1111\/j.1478-3231.2007.01567.x","volume":"27","author":"Mendez-Sanchez N","year":"2007","journal-title":"Liver Int"}],"container-title":["Pediatric Research"],"original-title":[],"deposited":{"date-parts":[[2024,2,26]],"date-time":"2024-02-26T11:13:42Z","timestamp":1708946022000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.nature.com\/doifinder\/10.1203\/PDR.0b013e31816c9013"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2008,6]]},"references-count":42,"journal-issue":{"issue":"6","published-print":{"date-parts":[[2008,6]]}},"alternative-id":["pr2008132"],"URL":"https:\/\/doi.org\/10.1203\/pdr.0b013e31816c9013","relation":{},"ISSN":["0031-3998","1530-0447"],"issn-type":[{"value":"0031-3998","type":"print"},{"value":"1530-0447","type":"electronic"}],"subject":[],"published":{"date-parts":[[2008,6]]}}}