{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,7,30]],"date-time":"2025-07-30T13:53:33Z","timestamp":1753883613351,"version":"3.41.2"},"reference-count":14,"publisher":"The Endocrine Society","issue":"7","license":[{"start":{"date-parts":[[2025,5,21]],"date-time":"2025-05-21T00:00:00Z","timestamp":1747785600000},"content-version":"vor","delay-in-days":6,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc-nd\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2025,5,15]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:p>Cystic fibrosis (CF), a genetic disorder caused by pathogenic variants in the CFTR gene, is associated with various complications including cystic fibrosis\u2013related diabetes (CFRD). CFRD is an entity distinct from type 1 or type 2 diabetes. We report a rare case of diabetic ketoacidosis (DKA) in a pediatric patient with CFRD, occurring during a significant pulmonary exacerbation. The patient's management involved addressing fluid and electrolyte imbalances, careful monitoring of nutritional status, and correction of hyperglycemia with insulin. This case serves as a reminder to consider DKA in the differential diagnosis of patients with CF presenting with respiratory distress, even in the absence of typical symptoms such as polyuria and polydipsia.<\/jats:p>","DOI":"10.1210\/jcemcr\/luaf114","type":"journal-article","created":{"date-parts":[[2025,5,21]],"date-time":"2025-05-21T08:01:11Z","timestamp":1747814471000},"source":"Crossref","is-referenced-by-count":0,"title":["Diabetic Ketoacidosis in a Pediatric Patient with Cystic Fibrosis\u2013related Diabetes"],"prefix":"10.1210","volume":"3","author":[{"given":"Shyam","family":"Harinarayanan","sequence":"first","affiliation":[{"name":"Department of Pediatrics, UT Southwestern Medical Center , Dallas, TX 75390-9063 ,","place":["USA"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Taylor","family":"Merritt","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, UT Southwestern Medical Center , Dallas, TX 75390-9063 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