{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,27]],"date-time":"2026-09-27T07:18:56Z","timestamp":1790493536597,"version":"4.1.0"},"reference-count":35,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"6","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2008,12]]},"DOI":"10.1213\/ane.0b013e3181875a4d","type":"journal-article","created":{"date-parts":[[2008,11,13]],"date-time":"2008-11-13T03:19:45Z","timestamp":1226546385000},"page":"1848-1854","source":"Crossref","is-referenced-by-count":129,"title":["Congenital Supravalvular Aortic Stenosis and Sudden Death Associated with Anesthesia: What\u2019s the Mystery?"],"prefix":"10.1213","volume":"107","author":[{"given":"Thomas M.","family":"Burch","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Francis X.","family":"McGowan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Barry D.","family":"Kussman","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Andrew J.","family":"Powell","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"James A.","family":"DiNardo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","reference":[{"key":"R1-16-20210902","doi-asserted-by":"crossref","first-page":"1311","DOI":"10.1161\/01.CIR.24.6.1311","article-title":"Supravalvular aortic stenosis.","volume":"24","author":"Williams","year":"1961","journal-title":"Circulation"},{"key":"R2-16-20210902","doi-asserted-by":"crossref","first-page":"1235","DOI":"10.1161\/01.CIR.26.6.1235","article-title":"Supravalvular aortic stenosis in association with mental retardation and a certain facial appearance.","volume":"26","author":"Beuren","year":"1962","journal-title":"Circulation"},{"key":"R3-16-20210902","doi-asserted-by":"crossref","first-page":"471","DOI":"10.1016\/0002-9149(64)90154-7","article-title":"The Syndrome of Supravalvular Aortic Stenosis, Peripheral Pulmonary Stenosis, Mental Retardation and Similar Facial Appearance.","volume":"13","author":"Beuren","year":"1964","journal-title":"Am J Cardiol"},{"key":"R4-16-20210902","doi-asserted-by":"crossref","first-page":"1242","DOI":"10.1016\/S0002-9149(98)00114-3","article-title":"Aortic hypoplasia in homozygous familial hypercholesterolemia.","volume":"81","author":"Jones","year":"1998","journal-title":"Am J Cardiol"},{"key":"R5-16-20210902","doi-asserted-by":"crossref","first-page":"12","DOI":"10.1046\/j.1525-1470.2000.01703.x","article-title":"Elastin gene deletions in Williams syndrome patients result in altered deposition of elastic fibers in skin and a subclinical dermal phenotype.","volume":"17","author":"Urban","year":"2000","journal-title":"Pediatr Dermatol"},{"key":"R6-16-20210902","doi-asserted-by":"crossref","first-page":"827","DOI":"10.1007\/s00246-005-0885-8","article-title":"Elastin mutation screening in a group of patients affected by vascular abnormalities.","volume":"26","author":"Rodriguez-Revenga","year":"2005","journal-title":"Pediatr Cardiol"},{"key":"R7-16-20210902","doi-asserted-by":"crossref","first-page":"512","DOI":"10.1007\/s00439-001-0608-z","article-title":"Supravalvular aortic stenosis: genetic and molecular dissection of a complex mutation in the elastin gene.","volume":"109","author":"Urban","year":"2001","journal-title":"Hum Genet"},{"key":"R8-16-20210902","doi-asserted-by":"crossref","first-page":"341","DOI":"10.1097\/01.hco.0000126581.89648.10","article-title":"Arterial stiffness and the systolic hypertension syndrome.","volume":"19","author":"Izzo","year":"2004","journal-title":"Curr Opin Cardiol"},{"key":"R9-16-20210902","doi-asserted-by":"crossref","first-page":"51","DOI":"10.1023\/A:1013749806227","article-title":"Age-related changes in venticular-arterial coupling: pathophysiologic implications.","volume":"7","author":"Kass","year":"2002","journal-title":"Heart Fail Rev"},{"key":"R10-16-20210902","doi-asserted-by":"crossref","first-page":"16","DOI":"10.1016\/S0022-5223(97)70112-0","article-title":"The aortic root in supravalvular aortic stenosis: the potential surgical relevance of morphologic findings.","volume":"114","author":"Stamm","year":"1997","journal-title":"J Thorac Cardiovasc Surg"},{"key":"R11-16-20210902","doi-asserted-by":"crossref","first-page":"195","DOI":"10.1016\/S1010-7940(00)00647-3","article-title":"Congenital supravalvar aortic stenosis: a simple lesion?","volume":"19","author":"Stamm","year":"2001","journal-title":"Eur J Cardiothorac Surg"},{"key":"R12-16-20210902","doi-asserted-by":"crossref","first-page":"37","DOI":"10.1017\/S1047951100007356","article-title":"Natural course of supravalvar aortic stenosis and peripheral pulmonary arterial stenosis in Williams\u2019 syndrome.","volume":"9","author":"Kim","year":"1999","journal-title":"Cardiol Young"},{"key":"R13-16-20210902","doi-asserted-by":"crossref","first-page":"755","DOI":"10.1067\/mtc.2000.107477","article-title":"Surgery for bilateral outflow tract obstruction in elastin arteriopathy.","volume":"120","author":"Stamm","year":"2000","journal-title":"J Thorac Cardiovasc Surg"},{"key":"R14-16-20210902","doi-asserted-by":"crossref","first-page":"874","DOI":"10.1016\/S0022-5223(99)70057-7","article-title":"Forty-one years of surgical experience with congenital supravalvular aortic stenosis.","volume":"118","author":"Stamm","year":"1999","journal-title":"J Thorac Cardiovasc Surg"},{"key":"R15-16-20210902","doi-asserted-by":"crossref","first-page":"16","DOI":"10.1016\/S0003-4975(10)62386-7","article-title":"Obstruction to left coronary artery blood flow secondary to obliteration of the coronary ostium in supravalvular aortic stenosis.","volume":"45","author":"Martin","year":"1988","journal-title":"Ann Thorac Surg"},{"key":"R16-16-20210902","first-page":"237","article-title":"Aortic root pathology and sudden death in youth: review of anatomical varieties.","volume":"4","author":"Thiene","year":"1986","journal-title":"Appl Pathol"},{"key":"R17-16-20210902","doi-asserted-by":"crossref","first-page":"751","DOI":"10.3109\/15513819209024230","article-title":"Sudden death in supravalvular aortic stenosis: fusion of a coronary leaflet to the sinus ridge, dysplasia and stenosis of aortic and pulmonic valves.","volume":"12","author":"Sun","year":"1992","journal-title":"Pediatr Pathol"},{"key":"R18-16-20210902","doi-asserted-by":"crossref","first-page":"1331","DOI":"10.1016\/0003-4975(91)90026-M","article-title":"Extended aortic and left main coronary angioplasty with a single pericardial patch in a patient with Williams syndrome.","volume":"52","author":"Matsuda","year":"1991","journal-title":"Ann Thorac Surg"},{"key":"R19-16-20210902","doi-asserted-by":"crossref","first-page":"926","DOI":"10.1016\/S0022-3476(96)70042-2","article-title":"Sudden death in Williams syndrome: report of ten cases.","volume":"129","author":"Bird","year":"1996","journal-title":"J Pediatr"},{"key":"R20-16-20210902","doi-asserted-by":"crossref","first-page":"21","DOI":"10.1016\/S0022-5223(94)70213-6","article-title":"Pathology of coronary arteries, myocardium, and great arteries in supravalvular aortic stenosis. Report of five cases with implications for surgical treatment.","volume":"108","author":"van Son","year":"1994","journal-title":"J Thorac Cardiovasc Surg"},{"key":"R21-16-20210902","doi-asserted-by":"crossref","first-page":"946","DOI":"10.1016\/j.jtcvs.2004.05.008","article-title":"Dysphagia: an unusual presentation of giant aneurysm of the right coronary artery and supravalvular aortic stenosis in Williams syndrome.","volume":"128","author":"Mignosa","year":"2004","journal-title":"J Thorac Cardiovasc Surg"},{"key":"R22-16-20210902","doi-asserted-by":"crossref","first-page":"251","DOI":"10.1016\/S0022-3476(85)80298-5","article-title":"Myocardial infarction associated with supravalvular aortic stenosis.","volume":"106","author":"Terhune","year":"1985","journal-title":"J Pediatr"},{"key":"R23-16-20210902","doi-asserted-by":"crossref","first-page":"593","DOI":"10.1016\/S0022-3476(05)80696-1","article-title":"Myocardial infarction leading to sudden death in the Williams syndrome: report of three cases.","volume":"117","author":"Conway","year":"1990","journal-title":"J Pediatr"},{"key":"R24-16-20210902","doi-asserted-by":"crossref","first-page":"665","DOI":"10.1007\/s00246-004-0845-8","article-title":"Severe coronary artery disease in the absence of supravalvular stenosis in a patient with Williams syndrome.","volume":"26","author":"van Pelt","year":"2005","journal-title":"Pediatr Cardiol"},{"key":"R25-16-20210902","doi-asserted-by":"crossref","first-page":"751","DOI":"10.1007\/s004310050705","article-title":"Progressive left main coronary artery obstruction leading to myocardial infarction in a child with Williams syndrome.","volume":"156","author":"Bonnet","year":"1997","journal-title":"Eur J Pediatr"},{"key":"R26-16-20210902","doi-asserted-by":"crossref","first-page":"2165","DOI":"10.1161\/01.CIR.103.17.2165","article-title":"Balloon dilation angioplasty of peripheral pulmonary stenosis associated with Williams syndrome.","volume":"103","author":"Geggel","year":"2001","journal-title":"Circulation"},{"key":"R27-16-20210902","doi-asserted-by":"crossref","first-page":"234","DOI":"10.1002\/ajmg.a.30012","article-title":"Risk of sudden death in the Williams-Beuren syndrome.","volume":"127","author":"Wessel","year":"2004","journal-title":"Am J Med Genet A"},{"key":"R28-16-20210902","doi-asserted-by":"crossref","first-page":"1458","DOI":"10.1093\/eurheartj\/14.11.1458","article-title":"Williams-Beuren syndrome: a 30-year follow-up of natural and postoperative course.","volume":"14","author":"Kececioglu","year":"1993","journal-title":"Eur Heart J"},{"key":"R29-16-20210902","doi-asserted-by":"crossref","first-page":"45","DOI":"10.1016\/S0379-0738(99)00120-6","article-title":"Supravalvular aortic stenosis, Williams syndrome and sudden death. A case report.","volume":"106","author":"Suarez-Mier","year":"1999","journal-title":"Forensic Sci Int"},{"key":"R30-16-20210902","doi-asserted-by":"crossref","first-page":"322","DOI":"10.1046\/j.1442-200x.2000.01213.x","article-title":"Sudden death of a 21-year-old female with Williams syndrome showing rare complications.","volume":"42","author":"Imashuku","year":"2000","journal-title":"Pediatr Int"},{"key":"R31-16-20210902","doi-asserted-by":"crossref","first-page":"739","DOI":"10.1053\/jcan.2002.128407","article-title":"Coronary artery disease and anesthesia-related death in children with Williams syndrome.","volume":"16","author":"Horowitz","year":"2002","journal-title":"J Cardiothorac Vasc Anesth"},{"key":"R32-16-20210902","first-page":"287","article-title":"Cardiac arrest under anesthesia in a pediatric patient with Williams syndrome: a case report.","volume":"73","author":"Bragg","year":"2005","journal-title":"AANA J"},{"key":"R33-16-20210902","doi-asserted-by":"crossref","first-page":"1133","DOI":"10.1016\/j.ijporl.2005.11.009","article-title":"Death following tonsillectomy in a child with Williams syndrome.","volume":"70","author":"Monfared","year":"2006","journal-title":"Int J Pediatr Otorhinolaryngol"},{"key":"R35-16-20210902","doi-asserted-by":"crossref","first-page":"e1005","DOI":"10.1542\/peds.2006-0346","article-title":"2005 American Heart Association (AHA) guidelines for cardiopulmonary resuscitation (CPR) and emergency cardiovascular care (ECC) of pediatric and neonatal patients: pediatric advanced life support.","volume":"117","year":"2006","journal-title":"Pediatrics"},{"key":"R36-16-20210902","doi-asserted-by":"crossref","first-page":"1693","DOI":"10.1161\/CIRCULATIONAHA.106.680678","article-title":"Extracorporeal membrane oxygenation to aid cardiopulmonary resuscitation in infants and children.","volume":"116","author":"Thiagarajan","year":"2007","journal-title":"Circulation"}],"container-title":["Anesthesia & Analgesia"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.ovid.com\/10.1213\/ane.0b013e3181875a4d","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,8,7]],"date-time":"2026-08-07T14:16:32Z","timestamp":1786112192000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.ovid.com\/00000539-200812000-00016"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2008,12]]},"references-count":35,"journal-issue":{"issue":"6","published-print":{"date-parts":[[2008]]}},"URL":"https:\/\/doi.org\/10.1213\/ane.0b013e3181875a4d","relation":{},"ISSN":["0003-2999"],"issn-type":[{"value":"0003-2999","type":"print"}],"subject":[],"published":{"date-parts":[[2008,12]]}}}