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Cardiopulmonary manifestations of portovenous shunts from congenital absence of the portal vein: Pulmonary hypertension and pulmonary vascular dilatation. <i>Pediatr Transplant<\/i> 2011; 15: E162\u2013E168.","DOI":"10.1111\/j.1399-3046.2010.01355.x"},{"key":"23","doi-asserted-by":"crossref","unstructured":"23. Galie N, Hoeper MM, Humbert M, Torbicki A, Vachiery JL, Barbera JA, et al. Guidelines for the diagnosis and treatment of pulmonary hypertension: The Task Force for the Diagnosis and Treatment of Pulmonary Hypertension of the European Society of Cardiology (ESC) and the European Respiratory Society (ERS), endorsed by the International Society of Heart and Lung Transplantation (ISHLT). <i>Eur Heart J<\/i> 2009; 30: 2493\u20132537.","DOI":"10.1093\/eurheartj\/ehp297"},{"key":"24","doi-asserted-by":"crossref","unstructured":"24. Galie N, Humbert M, Vachiery JL, Gibbs S, Lang I, Torbicki A, et al. 2015 ESC\/ERS guidelines for the diagnosis and treatment of pulmonary hypertension: The Joint Task Force for the Diagnosis and Treatment of Pulmonary Hypertension of the European Society of Cardiology (ESC) and the European Respiratory Society (ERS): Endorsed by: Association for European Paediatric and Congenital Cardiology (AEPC), International Society for Heart and Lung Transplantation (ISHLT). <i>Eur Heart J<\/i> 2016; 37: 67\u2013119.","DOI":"10.1093\/eurheartj\/ehv317"},{"key":"25","doi-asserted-by":"crossref","unstructured":"25. Bambul Heck P, Eicken A, Kasnar-Samprec J, Ewert P, Hager A. Early pulmonary arterial hypertension immediately after closure of a ventricular or complete atrioventricular septal defect beyond 6 months of age. <i>Int J Cardiol<\/i> 2017; 228: 313\u2013318.","DOI":"10.1016\/j.ijcard.2016.11.056"},{"key":"26","unstructured":"26. Hazama K, Nakanishi T, Nakazawa M, Momma K. 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Heterotaxy syndrome: Asplenia and polysplenia as indicators of visceral malposition and complex congenital heart disease. <i>Biol Neonate<\/i> 2005; 88: 278\u2013290.","DOI":"10.1159\/000087625"},{"key":"30","doi-asserted-by":"crossref","unstructured":"30. Burton EC, Olson M, Rooper L. Defects in laterality with emphasis on heterotaxy syndromes with asplenia and polysplenia: An autopsy case series at a single institution. <i>Pediatr Dev Pathol<\/i> 2014; 17: 250\u2013264.","DOI":"10.2350\/13-11-1406-OA.1"},{"key":"31","doi-asserted-by":"crossref","unstructured":"31. Papagiannis J, Kanter RJ, Effman EL, Pratt PC, Arcille R, Browning IB, et al. Polysplenia with pulmonary arteriovenous malformations. <i>Pediatr Cardiol<\/i> 1993; 14: 127\u2013129.","DOI":"10.1007\/BF00796995"},{"key":"32","doi-asserted-by":"crossref","unstructured":"32. McElhinney DB, Marx GR, Newburger JW. Congenital portosystemic venous connections and other abdominal venous abnormalities in patients with polysplenia and functionally univentricular heart disease: A case series and literature review. <i>Congenit Heart Dis<\/i> 2011; 6: 28\u201340.","DOI":"10.1111\/j.1747-0803.2010.00478.x"},{"key":"33","doi-asserted-by":"crossref","unstructured":"33. Schidlow DV, Katz SM, Turtz MG, Donner RM, Capasso S. Polysplenia and kartagener syndromes in a sibship: Association with abnormal respiratory cilia. <i>J Pediatr<\/i> 1982; 100: 401\u2013403.","DOI":"10.1016\/S0022-3476(82)80439-3"},{"key":"34","doi-asserted-by":"crossref","unstructured":"34. Gershoni-Baruch R, Gottfried E, Pery M, Sahin A, Etzioni A. Immotile cilia syndrome including polysplenia, situs inversus, and extrahepatic biliary atresia. <i>Am J Med Genet<\/i> 1989; 33: 390\u2013393.","DOI":"10.1002\/ajmg.1320330320"},{"key":"35","doi-asserted-by":"crossref","unstructured":"35. 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Application of nitric oxide measurements in clinical conditions beyond asthma. <i>Eur Clin Respir J<\/i> 2015; 2: 28517.","DOI":"10.3402\/ecrj.v2.28517"},{"key":"39","unstructured":"39. Myers PO, Tissot C, Beghetti M. Assessment of operability of patients with pulmonary arterial hypertension associated with congenital heart disease: Do we have the good tools to predict success? <i>Circ J<\/i> 2014; 78: 4\u201311."}],"container-title":["Circulation Journal"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.jstage.jst.go.jp\/article\/circj\/83\/4\/83_CJ-18-0933\/_pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2019,5,24]],"date-time":"2019-05-24T23:19:28Z","timestamp":1558739968000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.jstage.jst.go.jp\/article\/circj\/83\/4\/83_CJ-18-0933\/_article"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2019,3,25]]},"references-count":39,"journal-issue":{"issue":"4","published-print":{"date-parts":[[2019]]}},"URL":"https:\/\/doi.org\/10.1253\/circj.cj-18-0933","relation":{},"ISSN":["1346-9843","1347-4820"],"issn-type":[{"value":"1346-9843","type":"print"},{"value":"1347-4820","type":"electronic"}],"subject":[],"published":{"date-parts":[[2019,3,25]]}}}