{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,3]],"date-time":"2026-10-03T15:09:34Z","timestamp":1791040174582,"version":"4.1.0"},"reference-count":0,"publisher":"Pakistan Journal of Medical Sciences","issue":"7","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pak J Med Sci"],"abstract":"<jats:p>Objective: To determine the prevalence and features of inner ear anomalies in children with congenital profound hearing loss who presented at our cochlear implant center based on imaging studies.\r\nMethods: This retrospective study reviewed charts of children with congenital SNHL, who presented to Department of Otolaryngology &amp; Auditory Implant Centre, Capital Hospital Islamabad over a period of 2 years from 1st May 2017 to 30th April 2019. These included 481 cases of both genders aged between 1 to 12 years. After gathering demographic data, audiological data, computed tomography findings of the temporal bone were analyzed. Data was analyzed using SPSS 22.\r\nResults: The Inner Ear Malformations were identified in 48(10%) children including 28 (58.33%) males and 20 (41.67%) female. Most 20(41.67%) presented at &gt;3-5 years of age followed by 19(39.58%) at 2-3 years. However, no significant association of gender (p=0.57, p=0.076) and age of presentation (p=0.344, p=0.697) for right and left ears was noted with inner ear malformations. The most common anomaly noted were CLA, CH-III and CH-II in decreasing order of frequency in both ears.\r\nConclusion: The prevalence of IEM\u2019s was found to be 48(10%). Commonest anomalies noted were CLA, CH-III and CH-II. No significant association of gender and age of presentation was noted with type of anomaly in both ears.\r\ndoi: https:\/\/doi.org\/10.12669\/pjms.36.7.3134\r\nHow to cite this:Ahmed J, Saqulain G, Khan MIJ, Kausar M. Prevalence &amp; features of inner ear malformations among children with congenital sensorineural hearing loss: A\u00a0Public\u00a0Cochlear Implant Centre Experience . Pak J Med Sci. 2020;36(7):1511-1516.\u00a0\u00a0doi: https:\/\/doi.org\/10.12669\/pjms.36.7.3134\r\nThis is an Open Access article distributed under the terms of the Creative Commons Attribution License (http:\/\/creativecommons.org\/licenses\/by\/3.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.<\/jats:p>","DOI":"10.12669\/pjms.36.7.3134","type":"journal-article","created":{"date-parts":[[2020,9,25]],"date-time":"2020-09-25T04:05:25Z","timestamp":1601006725000},"source":"Crossref","is-referenced-by-count":9,"title":["Prevalence &amp; features of inner ear malformations among\u00a0children with congenital sensorineural hearing loss: A\u00a0Public\u00a0Cochlear Implant Centre Experience"],"prefix":"10.12669","volume":"36","author":[{"given":"Jawwad","family":"Ahmed","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-6452-9339","authenticated-orcid":false,"given":"Ghulam","family":"Saqulain","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Muhammad Iqbal javed","family":"Khan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mobeen","family":"Kausar","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"4935","published-online":{"date-parts":[[2020,10,17]]},"container-title":["Pakistan Journal of Medical Sciences"],"original-title":[],"link":[{"URL":"https:\/\/pjms.org.pk\/index.php\/pjms\/article\/download\/3134\/698","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/pjms.org.pk\/index.php\/pjms\/article\/download\/3134\/698","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,5,9]],"date-time":"2026-05-09T06:58:50Z","timestamp":1778309930000},"score":1,"resource":{"primary":{"URL":"https:\/\/pjms.org.pk\/index.php\/pjms\/article\/view\/3134"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2020,10,17]]},"references-count":0,"journal-issue":{"issue":"7","published-online":{"date-parts":[[2020,9,23]]}},"URL":"https:\/\/doi.org\/10.12669\/pjms.36.7.3134","relation":{},"ISSN":["1681-715X","1682-024X"],"issn-type":[{"value":"1681-715X","type":"electronic"},{"value":"1682-024X","type":"print"}],"subject":[],"published":{"date-parts":[[2020,10,17]]}}}