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Acta Neuropathol. 110: 443-450.","DOI":"10.1007\/s00401-005-1040-6"},{"key":"12","unstructured":"12. Muldoon, L. L., Neuwelt, E. A., Pagel, M. A. and Weiss, D. L. 1994. Characterization of the molecular defect in a feline model for type II GM2-gangliosidosis (Sandhoff disease). Am. J. Pathol. 144: 1109-1118."},{"key":"13","doi-asserted-by":"crossref","unstructured":"13. Neuwelt, E. A., Johnson, W. G., Blank, N. K., Pagel, M. A., Maslen-McClure, C., McClure, M. J. and Wu, P. M. 1985. Characterization of a new model of GM2-gangliosidosis (Sandhoff's disease) in Korat cats. J. Clin. Invest. 76: 482-490.","DOI":"10.1172\/JCI111997"},{"key":"14","unstructured":"14. Pierce, K. R., Kosanke, S. D., Bay, W. W. and Bridges, C. H. 1976. Animal model of human disease: GM2 gangliosidosis. Am. J. Pathol. 83: 419-422."},{"key":"15","doi-asserted-by":"crossref","unstructured":"15. Read, W. K. and Bridges, C. H. 1968. Cerebrospinal lipodystrophy in swine. A new disease model in comparative pathology. 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Rapid and simple mutation screening of GM1 gangliosidosis in Shiba dogs by direct amplification of deoxyribonucleic acid from various forms of canine whole-blood specimens. J. Vet. Diagn. Invest. 16: 469-472.","DOI":"10.1177\/104063870401600520"},{"key":"21","doi-asserted-by":"crossref","unstructured":"21. Yamato, O., Kobayashi, A., Satoh, H., Endoh, D., Shoda, T., Masuoka, Y., Hatakeyama, A., Jo, E. O., Asano, T., Yonemura, M., Yamasaki, M. and Maede, Y. 2004. Comparison of polymerase chain reaction-restriction fragment length polymorphism assay and enzyme assay for diagnosis of GM1-gangliosidosis in Shiba dogs. J. Vet. Diagn. Invest. 16: 299-304.","DOI":"10.1177\/104063870401600407"},{"key":"22","doi-asserted-by":"crossref","unstructured":"22. Yamato, O., Matsuki, N., Satoh, H., Inaba, M., Ono, K., Yamasaki, M. and Maede, Y. 2002. Sandhoff disease in a golden retriever dog. J. Inherited Metab. Dis. 25: 319-320.","DOI":"10.1023\/A:1016562626961"},{"key":"23","unstructured":"23. 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