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Symptoms include breathlessness, cough, fatigue and anxiety. Treatment options are limited, and include medications to slow progression, exercise and oxygen therapy. Patient care has advanced as a result of using evidence-based practice set out in National Institute for Health Excellence guidelines and the Irish Thoracic Society position statement on IPF. The availability of resources and patient preferences can influence treatment options. The respiratory advanced nurse practitioner is in a unique position to manage the care of the person with IPF holistically, through patient education, symptom management, pulmonary rehabilitation and palliative care. The development of a national clinical care programme for ILD could facilitate standardised care and outcomes for patients. <\/jats:p>","DOI":"10.12968\/bjon.2024.0432","type":"journal-article","created":{"date-parts":[[2025,7,2]],"date-time":"2025-07-02T17:17:26Z","timestamp":1751476646000},"page":"675-682","source":"Crossref","is-referenced-by-count":2,"title":["Idiopathic pulmonary fibrosis: the role of the respiratory advanced nurse practitioner"],"prefix":"10.12968","volume":"34","author":[{"given":"Lynn","family":"Fox","sequence":"first","affiliation":[{"name":"ILD Respiratory Advanced Nurse Practitioner, Mater Misericordiae University Hospital, Ireland"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Bridget","family":"Murray","sequence":"additional","affiliation":[{"name":"Lecturer and Programme Director, Respiratory Care in Nursing Practice, School of Nursing, Royal College of Surgeons, Dublin, Ireland"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"5130","reference":[{"key":"B2","doi-asserted-by":"publisher","DOI":"10.1016\/j.pupt.2017.02.005"},{"issue":"3","key":"B3","doi-asserted-by":"crossref","first-page":"141","DOI":"10.1097\/SPC.0000000000000285","volume":"11","author":"Bajwah S","year":"2017","journal-title":"Curr Opin Support Palliat Care"},{"key":"B4","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2648.2012.06124.x"},{"issue":"9","key":"B7","first-page":"672","volume":"115","author":"Cassidy N","year":"2022","journal-title":"Ir Med J"},{"issue":"1","key":"B8","doi-asserted-by":"crossref","first-page":"93","DOI":"10.1186\/s12890-021-01431-8","volume":"21","author":"Delameillieure A","year":"2021","journal-title":"BMC Pulm Med"},{"issue":"2","key":"B9","first-page":"CD006322","volume":"2","author":"Dowman L","year":"2021","journal-title":"Cochrane Database Syst Rev"},{"issue":"1","key":"B14","doi-asserted-by":"crossref","first-page":"e001276","DOI":"10.1136\/bmjresp-2022-001276","volume":"9","author":"Hoyer N","year":"2022","journal-title":"BMJ Open Respir Res"},{"issue":"1","key":"B17","doi-asserted-by":"crossref","first-page":"66","DOI":"10.1111\/resp.14154","volume":"27","author":"Lancaster L","year":"2022","journal-title":"Respirology"},{"issue":"1","key":"B18","doi-asserted-by":"crossref","first-page":"54","DOI":"10.1186\/s12890-023-02340-8","volume":"23","author":"Lee JH","year":"2023","journal-title":"BMC Pulm Med"},{"issue":"1","key":"B19","doi-asserted-by":"crossref","first-page":"124","DOI":"10.1186\/s12890-017-0468-5","volume":"17","author":"Maher TM","year":"2017","journal-title":"BMC Pulm Med"},{"issue":"2","key":"B20","doi-asserted-by":"crossref","first-page":"383","DOI":"10.1111\/jan.13453","volume":"74","author":"McVeigh C","year":"2018","journal-title":"J Adv Nurs"},{"key":"B24","volume-title":"Position paper one. 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