{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,20]],"date-time":"2026-10-20T16:02:24Z","timestamp":1792512144633,"version":"4.5.0"},"reference-count":36,"publisher":"Japanese Society for Pediatric Endocrinology","issue":"3","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Clin Pediatr Endocrinol"],"published-print":{"date-parts":[[2024]]},"DOI":"10.1297\/cpe.2023-0062","type":"journal-article","created":{"date-parts":[[2024,3,7]],"date-time":"2024-03-07T17:11:56Z","timestamp":1709831516000},"page":"131-138","source":"Crossref","is-referenced-by-count":2,"title":["Use of a long-term continuous glucose monitor for predicting sulfonylurea          dose in patients with neonatal diabetes mellitus: a case series"],"prefix":"10.1297","volume":"33","author":[{"given":"Koji","family":"Tagawa","sequence":"first","affiliation":[{"name":"Department of Pediatrics, Shiga University of Medical Science, Shiga,              Japan"},{"name":"Department of Pediatrics, Sapporo Tokushukai Hospital, Hokkaido,              Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Katsuyuki","family":"Matsui","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Shiga University of Medical Science, Shiga,              Japan"},{"name":"Division of Endocrinology, Metabolism &amp; Diabetes, Shiga Medical Center              for Children, Shiga, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Atsushi","family":"Tsukamura","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Shiga University of Medical Science, Shiga,              Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Masami","family":"Shibata","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Shiga University of Medical Science, Shiga,              Japan"},{"name":"Department of Pediatrics, Ogaki Municipal Hospital, Gifu,              Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hidemi","family":"Tsutsui","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Shiga University of Medical Science, Shiga,              Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shizuyo","family":"Nagai","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Shiga University of Medical Science, Shiga,              Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yoshihiro","family":"Maruo","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Shiga University of Medical Science, Shiga,              Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"125","reference":[{"key":"1","doi-asserted-by":"crossref","unstructured":"1. Aguilar-Bryan,                L, Bryan,                J. Neonatal            diabetes mellitus. Endocr Rev          2008;29: 265\u201391.","DOI":"10.1210\/er.2007-0029"},{"key":"2","doi-asserted-by":"crossref","unstructured":"2. Hattersley,                AT,              Greeley, SAW,                Polak, M,                Rubio-Cabezas,              O, Nj\u00f8lstad,                PR,                Mlynarski,              W, et al.            ISPAD Clinical Practice Consensus Guidelines 2018: The diagnosis and            management of monogenic diabetes in children and adolescents.            Pediatr Diabetes          2018;19(Suppl 27):            47\u201363.","DOI":"10.1111\/pedi.12772"},{"key":"3","doi-asserted-by":"crossref","unstructured":"3. Polak,              M, Cav\u00e9,                H. Neonatal            diabetes mellitus: a disease linked to multiple mechanisms.            Orphanet J Rare Dis          2007;2: 12.","DOI":"10.1186\/1750-1172-2-12"},{"key":"4","doi-asserted-by":"crossref","unstructured":"4. Libman,              I, Haynes,                A, Lyons,                S, Pradeep,                P,              Rwagasor, E,                Tung, JY,              et al. ISPAD Clinical Practice Consensus            Guidelines 2022: Definition, epidemiology, and classification of diabetes in children            and adolescents. Pediatr Diabetes          2022;23: 1160\u201374.","DOI":"10.1111\/pedi.13454"},{"key":"5","doi-asserted-by":"crossref","unstructured":"5. De                Franco, E,                Flanagan,              SE, Houghton,                JA, Lango                Allen, H,                Mackay, DJ,                Temple, IK,              et al. The effect of early, comprehensive            genomic testing on clinical care in neonatal diabetes: an international cohort            study. Lancet          2015;386: 957\u201363.","DOI":"10.1016\/S0140-6736(15)60098-8"},{"key":"6","doi-asserted-by":"crossref","unstructured":"6. Suzuki,              S, Makita,                Y, Mukai,                T, Matsuo,                K, Ueda,                O, Fujieda,                K. Molecular            basis of neonatal diabetes in Japanese patients. J Clin            Endocrinol Metab          2007;92: 3979\u201385.","DOI":"10.1210\/jc.2007-0486"},{"key":"7","doi-asserted-by":"publisher","unstructured":"7. Iafusco,              D, Stazi,                MA,                Cotichini,              R,              Cotellessa,            M, Martinucci,                ME,                Mazzella,            M, et al.            Early Onset Diabetes Study Group of the Italian Society of Paediatric            Endocrinology and Diabetology. Permanent diabetes mellitus            in the first year of life. Diabetologia          2002;45: 798\u2013804.","DOI":"10.1007\/s00125-002-0837-2"},{"key":"8","doi-asserted-by":"crossref","unstructured":"8. Garcin,              L, Mericq,                V,                Fauret-Amsellem,              AL, Cave,                H, Polak,                M,              Beltrand,            J. Neonatal            diabetes due to potassium channel mutation: Response to sulfonylurea according to the            genotype. Pediatr Diabetes          2020;21: 932\u201341.","DOI":"10.1111\/pedi.13041"},{"key":"9","doi-asserted-by":"crossref","unstructured":"9. Rabbone,              I, Barbetti,                F,                Gentilella,              R, Mossetto,                G,              Bonfanti, R,                Maffeis, C,              et al. Insulin therapy in neonatal diabetes            mellitus: a review of the literature. Diabetes Res Clin            Pract          2017;129: 126\u201335.","DOI":"10.1016\/j.diabres.2017.04.007"},{"key":"10","doi-asserted-by":"crossref","unstructured":"10. Beardsall,                K,                Pesterfield,              CL, Acerini,                CL. Neonatal            diabetes and insulin pump therapy. Arch Dis Child Fetal Neonatal            Ed          2011;96: F223\u20134.","DOI":"10.1136\/adc.2010.196709"},{"key":"11","doi-asserted-by":"crossref","unstructured":"11. Olinder,                AL,              Kernell, A,                Smide,            B. Treatment with            CSII in two infants with neonatal diabetes mellitus. Pediatr            Diabetes          2006;7: 284\u20138.","DOI":"10.1111\/j.1399-5448.2006.00203.x"},{"key":"12","doi-asserted-by":"publisher","unstructured":"12. Bharucha,                T, Brown,                J,                McDonnell,              C, Gebert,                R,                McDougall,              P, Cameron,                F, et al.            Neonatal diabetes mellitus: Insulin pump as an alternative management            strategy. J Paediatr Child Health          2005;41: 522\u20136.","DOI":"10.1111\/j.1440-1754.2005.00696.x"},{"key":"13","doi-asserted-by":"crossref","unstructured":"13. Wintergerst,                KA,                Hargadon,            S, Hsiang,                HY.            Continuous subcutaneous insulin infusion in neonatal diabetes            mellitus. Pediatr Diabetes          2004;5: 202\u20136.","DOI":"10.1111\/j.1399-543X.2004.00067.x"},{"key":"14","doi-asserted-by":"crossref","unstructured":"14. Passanisi,                S,                Timpanaro,              T, Lo Presti,                D, Mamm\u00ec,                C,                Caruso-Nicoletti,              M. Treatment of            transient neonatal diabetes mellitus: insulin pump or insulin glargine? Our            experience. Diabetes Technol Ther          2014;16: 880\u20134.","DOI":"10.1089\/dia.2014.0055"},{"key":"15","doi-asserted-by":"crossref","unstructured":"15. Ortolani,                F,              Piccinno, E,                Grasso, V,                Papadia, F,                Panzeca, R,                Cortese, C,              et al. Diabetes associated with dominant            insulin gene mutations: outcome of 24-month, sensor-augmented insulin pump            treatment. Acta Diabetol          2016;53: 499\u2013501.","DOI":"10.1007\/s00592-015-0793-1"},{"key":"16","doi-asserted-by":"crossref","unstructured":"16. Iwata,              N, Asui,                R,              Mizumoto, H,                Hata,            D. Management of            a case of transient neonatal diabetes mellitus using continuous glucose            monitoring. Clin Pediatr Endocrinol          2020;29: 77\u201380.","DOI":"10.1297\/cpe.29.77"},{"key":"17","doi-asserted-by":"crossref","unstructured":"17. Fukuda,              Y, Ishii,                A,              Kamasaki, H,                Fusagawa,            S, Terada,                K,              Igarashi, L,              et al. Long-term sensor-augmented pump            therapy for neonatal diabetes mellitus: a case series. Clin            Pediatr Endocrinol          2022;31: 178\u201384.","DOI":"10.1297\/cpe.2022-0005"},{"key":"18","doi-asserted-by":"crossref","unstructured":"18. Lyra,              A, Ferreira,                FR, Mois\u00e9s,                RCS, de                Noronha, RM,                Calliari,              LE. The role of            intermittent continuous glucose monitoring in a successful outpatient transition from            insulin to glibenclamide in a patient with transient neonatal diabetes.            Arch Endocrinol Metab          2022;66: 429\u201335.","DOI":"10.20945\/2359-3997000000484"},{"key":"19","doi-asserted-by":"crossref","unstructured":"19. Rabbone,              I, Barbetti,                F,                Marigliano,              M, Bonfanti,                R,              Piccinno, E,                Ortolani,            F, et al.            Successful treatment of young infants presenting neonatal diabetes            mellitus with continuous subcutaneous insulin infusion before genetic            diagnosis. Acta Diabetol          2016;53: 559\u201365.","DOI":"10.1007\/s00592-015-0828-7"},{"key":"20","doi-asserted-by":"crossref","unstructured":"20. Massa,              O, Iafusco,                D, D\u2019Amato,                E, Gloyn,                AL,                Hattersley,              AT, Pasquino,                B, et al.            Early Onset Diabetes Study Group of the Italian Society of Pediatric            Endocrinology and Diabetology. KCNJ11 activating mutations            in Italian patients with permanent neonatal diabetes. Hum            Mutat          2005;25: 22\u20137.","DOI":"10.1002\/humu.20124"},{"key":"21","doi-asserted-by":"crossref","unstructured":"21. Skupien,              J, Malecki,                MT,                Mlynarski,              W, Klupa,                T, Wanic,                K, Gach,                A, et al.            Assessment of insulin sensitivity in adults with permanent neonatal            diabetes mellitus due to mutations in the KCNJ11 gene encoding Kir6.2.            Rev Diabet Stud          2006;3: 17\u201320.","DOI":"10.1900\/RDS.2006.3.17"},{"key":"22","doi-asserted-by":"crossref","unstructured":"22. Pearson,                ER,                Flechtner,              I, Nj\u00f8lstad,                PR,              Malecki, MT,                Flanagan,              SE, Larkin,                B, et al.            Neonatal Diabetes International Collaborative Group.            Switching from insulin to oral sulfonylureas in patients with diabetes            due to Kir6.2 mutations. N Engl J Med          2006;355: 467\u201377.","DOI":"10.1056\/NEJMoa061759"},{"key":"23","doi-asserted-by":"crossref","unstructured":"23. Lemelman,                MB,                Letourneau,              L, Greeley,                SAW. Neonatal            diabetes mellitus: an update on diagnosis and management. Clin            Perinatol          2018;45: 41\u201359.","DOI":"10.1016\/j.clp.2017.10.006"},{"key":"24","doi-asserted-by":"crossref","unstructured":"24. Li,                X, Xu,                A, Sheng,                H, Ting,                TH, Mao,                X, Huang,                X, et al.            Early transition from insulin to sulfonylureas in neonatal diabetes and            follow-up: Experience from China. Pediatr Diabetes          2018;19: 251\u20138.","DOI":"10.1111\/pedi.12560"},{"key":"25","doi-asserted-by":"crossref","unstructured":"25. de Gouveia                Buff Passone, C,                Giani, E,                Vaivre-Douret,              L,                Kariyawasam,              D, Berdugo,                M, Garcin,                L, et al.            Sulfonylurea for improving neurological features in neonatal diabetes: A            systematic review and meta-analyses. Pediatr Diabetes          2022;23: 675\u201392.","DOI":"10.1111\/pedi.13376"},{"key":"26","doi-asserted-by":"crossref","unstructured":"26. Hashimoto,                Y, Dateki,                S, Hirose,                M,              Satomura, K,                Sawada, H,                Mizuno, H,              et al. Molecular and clinical features of              K<sub>ATP<\/sub> -channel neonatal diabetes mellitus in Japan.            Pediatr Diabetes          2017;18: 532\u20139.","DOI":"10.1111\/pedi.12447"},{"key":"27","doi-asserted-by":"crossref","unstructured":"27. Shah,              RP, Spruyt,                K, Kragie,                BC,              Greeley, SA,                Msall,            ME. Visuomotor            performance in KCNJ11-related neonatal diabetes is impaired in children with            DEND-associated mutations and may be improved by early treatment with            sulfonylureas. Diabetes Care          2012;35: 2086\u20138.","DOI":"10.2337\/dc11-2225"},{"key":"28","doi-asserted-by":"crossref","unstructured":"28. Shimomura,                K, Maejima,                Y.              K<sub>ATP<\/sub> channel mutations and neonatal          diabetes. Intern Med          2017;56: 2387\u201393.","DOI":"10.2169\/internalmedicine.8454-16"},{"key":"29","doi-asserted-by":"crossref","unstructured":"29. Babiker,              T, Vedovato,                N, Patel,                K, Thomas,                N, Finn,                R,              M\u00e4nnikk\u00f6, R,              et al. Successful transfer to sulfonylureas            in KCNJ11 neonatal diabetes is determined by the mutation and duration of            diabetes. Diabetologia          2016;59: 1162\u20136.","DOI":"10.1007\/s00125-016-3921-8"},{"key":"30","doi-asserted-by":"crossref","unstructured":"30. Mlynarski,                W, Tarasov,                AI, Gach,                A, Girard,                CA,                Pietrzak,            I, Zubcevic,                L, et al.            Sulfonylurea improves CNS function in a case of intermediate DEND            syndrome caused by a mutation in KCNJ11. Nat Clin Pract            Neurol          2007;3: 640\u20135.","DOI":"10.1038\/ncpneuro0640"},{"key":"31","doi-asserted-by":"crossref","unstructured":"31. Ashcroft,                FM,              Puljung, MC,                Vedovato,            N. Neonatal            diabetes and the K<sub>ATP<\/sub> channel: from mutation to therapy.            Trends Endocrinol Metab          2017;28: 377\u201387.","DOI":"10.1016\/j.tem.2017.02.003"},{"key":"32","doi-asserted-by":"publisher","unstructured":"32. Beltrand,                J, Elie,                C, Busiah,                K,              Fournier, E,                Boddaert,            N,              Bahi-Buisson,              N, et al.            GlidKir Study Group. Sulfonylurea therapy            benefits neurological and psychomotor functions in patients with neonatal diabetes owing            to potassium channel mutations. Diabetes Care          2015;38: 2033\u201341.","DOI":"10.2337\/dc15-0837"},{"key":"33","doi-asserted-by":"publisher","unstructured":"33. Shimomura,                K, H\u00f6rster,                F, de Wet,                H,              Flanagan, SE,                Ellard, S,                Hattersley,              AT, et al.            A novel mutation causing DEND syndrome: a treatable channelopathy of            pancreas and brain. Neurology          2007;69: 1342\u20139.","DOI":"10.1212\/01.wnl.0000268488.51776.53"},{"key":"34","doi-asserted-by":"crossref","unstructured":"34. Bergenstal,                RM,                Tamborlane,              WV, Ahmann,                A, Buse,                JB, Dailey,                G, Davis,                SN, et al.            STAR 3 Study GroupEffectiveness of            sensor-augmented insulin-pump therapy in type 1 diabetes. N Engl            J Med          2010;363: 311\u201320.","DOI":"10.1056\/NEJMoa1002853"},{"key":"35","doi-asserted-by":"crossref","unstructured":"35. Poon,              SW, Chung,                BH, Tsang,                MH, Tung,                JY.            Successful transition from insulin to sulphonylurea in a child with            neonatal diabetes mellitus diagnosed beyond six months of age due to C42R mutation in            the <i>KCNJ11<\/i> gene. Clin Pediatr            Endocrinol          2022;31: 168\u201371.","DOI":"10.1297\/cpe.2022-0013"},{"key":"36","doi-asserted-by":"crossref","unstructured":"36. Mancioppi,                V, Pozzi,                E, Zanetta,                S,              Missineo, A,                Savastio,            S, Barbetti,                F, et al.            Case report: Better late than never, but sooner is better: switch from            CSII to sulfonylureas in two patients with neonatal diabetes due to KCNJ11            variants. Front Endocrinol (Lausanne)          2023;14: 1143736.","DOI":"10.3389\/fendo.2023.1143736"}],"container-title":["Clinical Pediatric Endocrinology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/www.jstage.jst.go.jp\/article\/cpe\/33\/3\/33_2023-0062\/_pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,7,6]],"date-time":"2024-07-06T00:26:06Z","timestamp":1720225566000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.jstage.jst.go.jp\/article\/cpe\/33\/3\/33_2023-0062\/_article"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024]]},"references-count":36,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2024]]}},"URL":"https:\/\/doi.org\/10.1297\/cpe.2023-0062","relation":{},"ISSN":["0918-5739","1347-7358"],"issn-type":[{"value":"0918-5739","type":"print"},{"value":"1347-7358","type":"electronic"}],"subject":[],"published":{"date-parts":[[2024]]},"article-number":"2023-0062"}}