{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,3,13]],"date-time":"2026-03-13T18:00:25Z","timestamp":1773424825383,"version":"3.50.1"},"reference-count":5,"publisher":"Royal College of Surgeons of England","issue":"1","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["annals"],"published-print":{"date-parts":[[2017,1]]},"abstract":"<jats:sec><jats:title>INTRODUCTION<\/jats:title><jats:p> Larsen syndrome is an autosomal-dominant osteochondrodysplasia characterised by large joint dislocations and craniofacial anomalies. <\/jats:p><\/jats:sec><jats:sec><jats:title>CASE HISTORY<\/jats:title><jats:p> We present a rare case of Larsen syndrome with bilateral dislocated hips and knees and severe clubfeet at 7-year follow-up. We undertook bilateral open reduction of both hips at age 8 months. This procedure was preceded by open reduction and left-knee V\u2013Y quadricepsplasty at age 4 months following a failed trial of closed reduction of the left knee. Both feet had a severe deformity (Pirani score of 5.5 and 6.0) and were treated using the Ponseti method, but the left foot relapsed at 24 months and required posteromedial release. <\/jats:p><\/jats:sec><jats:sec><jats:title>CONCLUSIONS<\/jats:title><jats:p> We tried to address the difficult questions on the timing and sequence of surgical interventions by treating clubfeet and dislocated knees early using Ponseti casts which included the knees. Open reduction of hips was done later, and further interventions were guided by functional needs. <\/jats:p><\/jats:sec>","DOI":"10.1308\/rcsann.2016.0258","type":"journal-article","created":{"date-parts":[[2016,8,9]],"date-time":"2016-08-09T09:34:58Z","timestamp":1470735298000},"page":"e8-e10","source":"Crossref","is-referenced-by-count":9,"title":["Management of joint dislocations of the lower limb in Larsen syndrome: practical approach"],"prefix":"10.1308","volume":"99","author":[{"given":"HE","family":"Matar","sequence":"first","affiliation":[{"name":"Alder Hey Children\u2019s Hospital, UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"NK","family":"Garg","sequence":"additional","affiliation":[{"name":"Alder Hey Children\u2019s Hospital, UK"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"171","reference":[{"key":"bib1","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-3476(50)80268-8"},{"key":"bib2","doi-asserted-by":"publisher","DOI":"10.2106\/00004623-196951020-00005"},{"key":"bib3","doi-asserted-by":"publisher","DOI":"10.1542\/peds.113.2.376"},{"key":"bib4","first-page":"259","volume":"60","author":"Rodr\u00edguez A","year":"1994","journal-title":"Acta Orthop Belg"},{"key":"bib5","doi-asserted-by":"publisher","DOI":"10.1097\/BPO.0b013e3181a6bf77"}],"container-title":["The Annals of The Royal College of Surgeons of England"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/publishing.rcseng.ac.uk\/doi\/pdf\/10.1308\/rcsann.2016.0258","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,5,15]],"date-time":"2023-05-15T10:24:43Z","timestamp":1684146283000},"score":1,"resource":{"primary":{"URL":"https:\/\/publishing.rcseng.ac.uk\/doi\/10.1308\/rcsann.2016.0258"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017,1]]},"references-count":5,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2017,1]]}},"alternative-id":["10.1308\/rcsann.2016.0258"],"URL":"https:\/\/doi.org\/10.1308\/rcsann.2016.0258","relation":{},"ISSN":["0035-8843","1478-7083"],"issn-type":[{"value":"0035-8843","type":"print"},{"value":"1478-7083","type":"electronic"}],"subject":[],"published":{"date-parts":[[2017,1]]}}}