{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2024,11,8]],"date-time":"2024-11-08T05:24:07Z","timestamp":1731043447831,"version":"3.28.0"},"reference-count":8,"publisher":"Texas Heart Institute Journal","issue":"4","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2017,8]]},"abstract":"<jats:p>Isolated supravalvular aortic stenosis in adults is a rare form of left ventricular outflow tract obstruction. We describe a case in a 41-year-old man in whom the supravalvular aorta had narrowed to approximately the size of the left anterior descending coronary artery. The patient underwent aortic surgery with replacement of the ascending aorta and repair of supravalvular aortic stenosis with a pantaloon graft. A postoperative echocardiogram showed substantial improvement: the mean gradient across the aorta had fallen from 48 to 8 mmHg. Surgery is the definitive treatment in symptomatic patients with supravalvular aortic stenosis.<\/jats:p>","DOI":"10.14503\/thij-16-5910","type":"journal-article","created":{"date-parts":[[2017,8,30]],"date-time":"2017-08-30T14:18:16Z","timestamp":1504102696000},"page":"287-289","source":"Crossref","is-referenced-by-count":0,"title":["Isolated Diffuse Supravalvular Aortic Stenosis with Severe Aortic Narrowing in a 41-Year-Old Man"],"prefix":"10.14503","volume":"44","author":[{"given":"Vinod","family":"Namana","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Sabah","family":"Siddiqui","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ram","family":"Balasubramanian","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jacob","family":"Shani","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Adnan","family":"Sadiq","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"5628","reference":[{"issue":"22","key":"i1526-6702-44-4-287-b1","series-title":"Circulation","first-page":"2412","article-title":"Left ventricular outflow obstruction: subaortic stenosis, bicuspid aortic valve, supravalvar aortic stenosis, and coarctation of the aorta","volume":"114","year":"2006","unstructured":"Aboulhosn\n              J\n            , ChildJS.\n          Left ventricular outflow obstruction: subaortic stenosis, bicuspid aortic valve, supravalvar aortic stenosis, and coarctation of the aorta. Circulation2006;114(22):2412\u201322."},{"issue":"23","key":"i1526-6702-44-4-287-b2","series-title":"Circulation","first-page":"2395","article-title":"ACC\/AHA 2008 Guidelines for the Management of Adults with Congenital Heart Disease: executive summary: a report of the American College of Cardiology\/American Heart Association Task Force on Practice Guidelines (writing committee to develop guidelines for the management of adults with congenital heart disease)","volume":"118","year":"2008","unstructured":"Warnes\n              CA\n            , WilliamsRG, BashoreTM, ChildJS, ConnollyHM, DearaniJA, \n          et al. ACC\/AHA 2008 Guidelines for the Management of Adults with Congenital Heart Disease: executive summary: a report of the American College of Cardiology\/American Heart Association Task Force on Practice Guidelines (writing committee to develop guidelines for the management of adults with congenital heart disease). Circulation2008;118(23):2395\u2013451."},{"key":"i1526-6702-44-4-287-b3","series-title":"Hurst's the heart","first-page":"1904","article-title":"Congenital heart diseases in adults","year":"2013","unstructured":"Aboulhosn\n              AJ\n            , ChildSJ.\n          Congenital heart diseases in adults. In: WalshRA, FangJC, FusterV, editors. Hurst's the heart. 13th ed. New York: McGraw-Hill Medical; 2013. p. 1904\u20135."},{"key":"i1526-6702-44-4-287-b4","series-title":"J Saudi Heart Assoc","article-title":"Isolated supravalvular aortic stenosis with left ventricular diverticulum and cleft mitral valve: surgical repair in adulthood","year":"2017","unstructured":"Nagamalesh\n              UM\n            , ShettyRS, NarayanR, KumarA, NaikR, UzmaS, NaiduK. \n          Isolated supravalvular aortic stenosis with left ventricular diverticulum and cleft mitral valve: surgical repair in adulthood. J Saudi Heart Assoc2017. In press. Available from: http:\/\/www.journalofthesaudiheart.com\/article\/S1016-7315(17)30014-3\/pdf."},{"issue":"7","key":"i1526-6702-44-4-287-b5","series-title":"J Assoc Physicians India","first-page":"104","article-title":"Isolated supravalvular aortic stenosis with infective endocarditis presenting as pyrexia of unknown origin","volume":"65","year":"2017","unstructured":"Mishra\n              DK\n            , KhullarV, GautamS, KhullarT.\n          Isolated supravalvular aortic stenosis with infective endocarditis presenting as pyrexia of unknown origin. J Assoc Physicians India2017;65(7):104\u20136."},{"issue":"4","key":"i1526-6702-44-4-287-b6","series-title":"J Med Genet","first-page":"306","article-title":"Fluorescent in situ hybridisation (FISH) for hemizygous deletion at the elastin locus in patients with isolated supravalvular aortic stenosis","volume":"34","year":"1997","unstructured":"Fryssira\n              H\n            , PalmerR, Hallidie-SmithKA, TaylorJ, DonnaiD, ReardonW.\n          Fluorescent in situ hybridisation (FISH) for hemizygous deletion at the elastin locus in patients with isolated supravalvular aortic stenosis. J Med Genet1997;34(4):306\u20138."},{"issue":"Suppl 4","key":"i1526-6702-44-4-287-b7","series-title":"Pediatr Res","first-page":"230A","article-title":"Supravalvular aortic stenosis without Williams syndrome [abstract]","volume":"21","year":"1987","unstructured":"Schmidt\n              MA\n            , MichelsVV, FeldtRH, HaglerDJ, EnsingGJ, CarterGA.\n          Supravalvular aortic stenosis without Williams syndrome [abstract]. Pediatr Res1987;21(Suppl 4):230A. Available from: http:\/\/www.nature.com\/pr\/journal\/v21\/n4s\/pdf\/pr1987468a.pdf."},{"issue":"1","key":"i1526-6702-44-4-287-b8","series-title":"Eur J Cardiothorac Surg","first-page":"50","article-title":"Surgical repair of congenital supravalvular aortic stenosis in children","volume":"21","year":"2002","unstructured":"Brown\n              JW\n            , RuzmetovM, VijayP, TurrentineMW.\n          Surgical repair of congenital supravalvular aortic stenosis in children. 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