{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,9,26]],"date-time":"2025-09-26T13:11:24Z","timestamp":1758892284397,"version":"3.28.0"},"reference-count":11,"publisher":"Texas Heart Institute Journal","issue":"3","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2023,5,1]]},"abstract":"<jats:title>Abstract<\/jats:title>\n        <jats:p>Catecholaminergic polymorphic ventricular tachycardia is a rare but lethal heritable arrhythmia syndrome associated with both atrial and ventricular arrhythmias. Treatment includes antiarrhythmics, sympathetic denervation, and implantable cardioverter-defibrillators. The use of atrioventricular nodal ablation as a treatment strategy to prevent ventricular arrhythmias in catecholaminergic polymorphic ventricular tachycardia was not found in the literature. This report describes a teenager with a presenting rhythm of atrial and ventricular fibrillation and cardiac arrest. Her clinical arrhythmia was predominantly atrial dysrhythmias, which delayed her diagnosis of catecholaminergic polymorphic ventricular tachycardia. Before her diagnosis, she underwent atrioventricular nodal ablation in an effort to prevent ventricular arrhythmias, which was ultimately ineffective. This report highlights the importance of recognizing atrial arrhythmias in catecholaminergic polymorphic ventricular tachycardia and provides evidence that atrioventricular nodal ablation is not an effective treatment strategy for this disease.<\/jats:p>","DOI":"10.14503\/thij-22-7974","type":"journal-article","created":{"date-parts":[[2023,6,2]],"date-time":"2023-06-02T21:49:19Z","timestamp":1685742559000},"source":"Crossref","is-referenced-by-count":1,"title":["Atrioventricular Nodal Ablation Is Not an Effective Treatment Strategy in Catecholaminergic Polymorphic Ventricular Tachycardia"],"prefix":"10.14503","volume":"50","author":[{"given":"S. Yukiko","family":"Asaki","sequence":"first","affiliation":[{"name":"Division of Cardiology, Department of Pediatrics, Texas Children's Hospital, Baylor College of Medicine, Houston, Texas"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"David","family":"Kessler","sequence":"additional","affiliation":[{"name":"Austin Heart, Austin, Texas"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Aarushi","family":"Nayak","sequence":"additional","affiliation":[{"name":"Division of Cardiology, Department of Pediatrics, Texas Children's Hospital, Baylor College of Medicine, Houston, Texas"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jeffrey J.","family":"Kim","sequence":"additional","affiliation":[{"name":"Division of Cardiology, Department of Pediatrics, Texas Children's Hospital, Baylor College of Medicine, Houston, Texas"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Christina Y.","family":"Miyake","sequence":"additional","affiliation":[{"name":"Division of Cardiology, Department of Pediatrics, Texas Children's Hospital, Baylor College of Medicine, Houston, Texas"},{"name":"Department of Molecular Physiology and Biophysics, Baylor College of Medicine, Houston, Texas"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"5628","reference":[{"issue":"1","key":"i1526-6702-50-3-e227974-b1","series-title":"Circulation.","doi-asserted-by":"publisher","first-page":"69","DOI":"10.1161\/01.cir.0000020013.73106.d8","article-title":"Clinical and molecular characterization of patients with catecholaminergic polymorphic ventricular tachycardia","volume":"106","year":"2002","unstructured":"Priori\n              SG,\n            \n            \n              Napolitano\n              C,\n            \n            Memmi,\n            .\n\t\t\t\n          Clinical and molecular characterization of patients with catecholaminergic polymorphic ventricular 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children.\n\t\t\tCirculation.1995;91(5):1512\u20131519.\n\t\t\tdoi:10.1161\/01.cir.91.5.1512"},{"issue":"3","key":"i1526-6702-50-3-e227974-b3","series-title":"Circ Arrhythm Electrophysiol.","doi-asserted-by":"publisher","first-page":"579","DOI":"10.1161\/CIRCEP.113.000170","article-title":"Efficacy of implantable cardioverter defibrillators in young patients with catecholaminergic polymorphic ventricular tachycardia: success depends on substrate","volume":"6","year":"2013","unstructured":"Miyake\n              CY,\n            \n            \n              Webster\n              G,\n            \n            \n              Czosek\n              RJ,\n            \n          \n          .\n\t\t\tEfficacy of implantable cardioverter defibrillators in young patients with catecholaminergic polymorphic ventricular tachycardia: success depends on substrate.\n\t\t\tCirc Arrhythm 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