{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2024,11,8]],"date-time":"2024-11-08T05:23:50Z","timestamp":1731043430268,"version":"3.28.0"},"reference-count":12,"publisher":"Texas Heart Institute Journal","issue":"1","license":[{"start":{"date-parts":[[2024,1,1]],"date-time":"2024-01-01T00:00:00Z","timestamp":1704067200000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2024]]},"abstract":"<jats:title>Abstract<\/jats:title>\n        <jats:p>Erdheim-Chester disease is a rare histiocytosis that primarily affects the skeletal system, but cardiovascular manifestations occur in 75% of cases and are associated with a poor prognosis. Given the small number of cases, the evolution and management of the disease are uncertain. Therefore, it is important to report and share Erdheim-Chester cases. This report presents the case of a young patient with constrictive pericarditis and mitral valve regurgitation resulting from Erdheim-Chester disease.<\/jats:p>","DOI":"10.14503\/thij-23-8201","type":"journal-article","created":{"date-parts":[[2024,2,7]],"date-time":"2024-02-07T05:31:30Z","timestamp":1707283890000},"source":"Crossref","is-referenced-by-count":0,"title":["Pericardiectomy and Mechanical Mitro-Aortic Valve Replacement in a Young Patient With Erdheim-Chester Disease"],"prefix":"10.14503","volume":"51","author":[{"given":"Nerea Lopez","family":"Perez","sequence":"first","affiliation":[{"name":"Division of Cardiovascular Surgery, Department of Surgery, University Hospital of Geneva, Geneva, Switzerland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mathieu van","family":"Steenberghe","sequence":"additional","affiliation":[{"name":"Division of Cardiovascular Surgery, Department of Surgery, University Hospital of Geneva, Geneva, Switzerland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"J\u00f6rg D.","family":"Seebach","sequence":"additional","affiliation":[{"name":"Division of Immunology and Allergy, Department of Medicine, University Hospitals of Geneva, Geneva, Switzerland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Philippe","family":"Meyer","sequence":"additional","affiliation":[{"name":"Division of Cardiology, University Hospital of Geneva, Geneva, Switzerland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Johannes Alexander","family":"Lobrinus","sequence":"additional","affiliation":[{"name":"Division of Clinical Pathology, University Hospital of Geneva, Geneva, Switzerland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Christoph","family":"Huber","sequence":"additional","affiliation":[{"name":"Division of Cardiovascular Surgery, Department of Surgery, University Hospital of Geneva, Geneva, Switzerland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mustafa","family":"Cikirikcioglu","sequence":"additional","affiliation":[{"name":"Division of Cardiovascular Surgery, Department of Surgery, University Hospital of Geneva, Geneva, Switzerland"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"5628","reference":[{"issue":"22","key":"i1526-6702-51-1-e238201-b1","series-title":"Blood","first-page":"1929","article-title":"Erdheim-Chester disease: consensus recommendations for evaluation, diagnosis, and treatment in the molecular era","volume":"135","author":"Goyal\n              G","year":"2020","unstructured":"Goyal\n              G\n            , HeaneyML, CollinM, et al. Erdheim-Chester disease: consensus recommendations for evaluation, diagnosis, and treatment in the molecular era. Blood. 2020;135(22):1929-1945. doi:10.1182\/BLOOD.2019003507"},{"key":"i1526-6702-51-1-e238201-b2","series-title":"Orphanet J Rare Dis","first-page":"137","article-title":"Erdheim-Chester disease: a comprehensive review of the literature","volume":"8","author":"Mazor\n              RD","year":"2013","unstructured":"Mazor\n              RD\n            , Manevich-MazorM, ShoenfeldY. Erdheim-Chester disease: a comprehensive review of the literature. Orphanet J Rare Dis. 2013;8:137. doi:10.1186\/1750-1172-8-137"},{"issue":"6","key":"i1526-6702-51-1-e238201-b3","series-title":"Blood Adv","first-page":"357","article-title":"The clinical spectrum of Erdheim-Chester disease: an observational cohort study","volume":"1","author":"Estrada-Veras\n              JI","year":"2017","unstructured":"Estrada-Veras\n              JI\n            , O\u2019BrienKJ, BoydLC, et al. The clinical spectrum of Erdheim-Chester disease: an observational cohort study. Blood Adv. 2017;1(6):357-366. doi:10.1182\/BLOODADVANCES.2016001784"},{"issue":"8","key":"i1526-6702-51-1-e238201-b4","series-title":"Curr Cardiol Rep","first-page":"75","article-title":"Erdheim-Chester disease: a rare but important cause of recurrent pericarditis","volume":"22","author":"Chahine\n              J","year":"2020","unstructured":"Chahine\n              J\n            , AlzubiJ, AlnajjarH, RamchandJ, ChetritM, KleinAL. Erdheim-Chester disease: a rare but important cause of recurrent pericarditis. Curr Cardiol Rep. 2020;22(8):75. doi:10.1007\/s11886-020-01307-z"},{"issue":"11","key":"i1526-6702-51-1-e238201-b5","series-title":"Can J Cardiol","first-page":"1832.e11","article-title":"Erdheim-Chester disease: an unusual etiology of recurrent massive pericardial effusion","volume":"36","author":"Lin\n              J","year":"2020","unstructured":"Lin\n              J\n            , TangSQ, ChenJC, ZhangYH, ZhangQ. Erdheim-Chester disease: an unusual etiology of recurrent massive pericardial effusion. Can J Cardiol. 2020;36(11):1832.e11-1832.e13. doi:10.1016\/j.cjca.2020.04.040"},{"issue":"12","key":"i1526-6702-51-1-e238201-b6","series-title":"Circ Cardiovasc Imaging","article-title":"Cardiac involvement in Erdheim-Chester disease","volume":"11","author":"Quinaglia-Silva\n              T","year":"2018","unstructured":"Quinaglia-Silva\n              T\n            , MedinaF, RamosCD, Coelho-FilhoOR. Cardiac involvement in Erdheim-Chester disease. Circ Cardiovasc Imaging. 2018;11(12):e008531. doi:10.1161\/CIRCIMAGING.118.008531"},{"issue":"14","key":"i1526-6702-51-1-e238201-b7","series-title":"JACC Case Rep","first-page":"862","article-title":"Pericardiectomy for constrictive pericarditis in a young patient with Erdheim-Chester disease","volume":"4","author":"El-Andari\n              R","year":"2022","unstructured":"El-Andari\n              R\n            , BaghaffarA, O\u2019ConnellA, et al. Pericardiectomy for constrictive pericarditis in a young patient with Erdheim-Chester disease. JACC Case Rep. 2022;4(14):862-867. doi:10.1016\/J.JACCAS.2022.03.024"},{"issue":"9","key":"i1526-6702-51-1-e238201-b8","series-title":"Acta Radiol Open","first-page":"2058460115592273","article-title":"Cardiac involvement in Erdheim-Chester disease: MRI findings and literature revision","volume":"4","author":"Ponsiglione\n              A","year":"2015","unstructured":"Ponsiglione\n              A\n            , PugliaM, BarbutoL, et al. Cardiac involvement in Erdheim-Chester disease: MRI findings and literature revision. Acta Radiol Open. 2015;4(9):2058460115592273doi:10.1177\/2058460115592273"},{"issue":"22","key":"i1526-6702-51-1-e238201-b9","series-title":"Blood","first-page":"1919","article-title":"Management of ECD: the era of targeted therapies","volume":"135","author":"Abla\n              O","year":"2020","unstructured":"Abla\n              O\n            \n          . Management of ECD: the era of targeted therapies. Blood. 2020;135(22):1919-1920. doi:10.1182\/BLOOD.2020005803"},{"issue":"6","key":"i1526-6702-51-1-e238201-b10","series-title":"Cureus","article-title":"Vemurafenib in the treatment of Erdheim Chester disease: a systematic review","volume":"14","author":"Aziz\n              SN","year":"2022","unstructured":"Aziz\n              SN\n            , ProanoL, CruzC, et al. Vemurafenib in the treatment of Erdheim Chester disease: a systematic review. Cureus. 2022;14(6):e25935. doi:10.7759\/CUREUS.25935"},{"issue":"1","key":"i1526-6702-51-1-e238201-b11","series-title":"JACC CardioOncol","first-page":"1","article-title":"Mechanistic and clinical overview cardiovascular toxicity of BRAF and MEK inhibitors: JACC: CardioOncology state-of-the-art review","volume":"4","author":"Glen\n              C","year":"2022","unstructured":"Glen\n              C\n            , TanYY, WaterstonA, et al. Mechanistic and clinical overview cardiovascular toxicity of BRAF and MEK inhibitors: JACC: CardioOncology state-of-the-art review. JACC CardioOncol. 2022;4(1):1-18. doi:10.1016\/j.JACCAO.2022.01.096"},{"issue":"10","key":"i1526-6702-51-1-e238201-b12","series-title":"Blood","first-page":"1163","article-title":"Sirolimus plus prednisone for Erdheim-Chester disease: an open-label trial","volume":"126","author":"Gianfreda\n              D","year":"2015","unstructured":"Gianfreda\n              D\n            , NicastroM, GalettiM, et al. Sirolimus plus prednisone for Erdheim-Chester disease: an open-label trial. Blood. 2015;126(10):1163-1171. doi:10.1182\/BLOOD-2015-01-620377"}],"container-title":["Texas Heart Institute Journal"],"original-title":[],"link":[{"URL":"https:\/\/thij.kglmeridian.com\/view\/journals\/thij\/51\/1\/article-e238201.xml","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/meridian.allenpress.com\/thij\/article-pdf\/doi\/10.14503\/THIJ-23-8201\/3411076\/i1526-6702-51-1-e238201.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"syndication"},{"URL":"https:\/\/thij.kglmeridian.com\/downloadpdf\/journals\/thij\/51\/1\/article-e238201.xml","content-type":"text\/html","content-version":"vor","intended-application":"syndication"},{"URL":"https:\/\/thij.kglmeridian.com\/downloadpdf\/journals\/thij\/51\/1\/article-e238201.xml","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,11,7]],"date-time":"2024-11-07T15:38:09Z","timestamp":1730993889000},"score":1,"resource":{"primary":{"URL":"https:\/\/thij.kglmeridian.com\/view\/journals\/thij\/51\/1\/article-e238201.xml"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024]]},"references-count":12,"journal-issue":{"issue":"1"},"URL":"https:\/\/doi.org\/10.14503\/thij-23-8201","relation":{},"ISSN":["1526-6702","0730-2347"],"issn-type":[{"type":"electronic","value":"1526-6702"},{"type":"print","value":"0730-2347"}],"subject":[],"published":{"date-parts":[[2024]]}}}