{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,12,9]],"date-time":"2025-12-09T08:27:26Z","timestamp":1765268846793},"reference-count":25,"publisher":"Walter de Gruyter GmbH","issue":"1","license":[{"start":{"date-parts":[[2022,1,1]],"date-time":"2022-01-01T00:00:00Z","timestamp":1640995200000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2022,7,21]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:p>Type II Abernethy malformation is an extremely reported congenital extrahepatic portosystemic shunt in complication with nephrotic syndrome. We present the case of an 8-year-old boy who presented with symptoms of type II Abernethy malformation and nephrotic syndrome. This diagnosis of this type II Abernethy malformation was based on physical examination, blood tests, urinalysis, nephrotic and hepatic function tests, routine clinical lipid measurements, abdominal ultrasonography, and computed tomographic angiography. A kidney biopsy revealed the pathological features of nephrotic syndrome. This is the second reported patient diagnosed with type II Abernethy malformation and nephrotic syndrome. Captopril treatment was effective in improving the symptoms of this case. A patient with type II Abernethy malformation related to immune complex-mediated glomerular injury was effectively improved with medication. Type II Abernethy malformation is a causative factor of immune complex-mediated glomerular injury in nephrotic syndrome. Captopril treatment significantly improved the symptoms in this case.<\/jats:p>","DOI":"10.1515\/biol-2022-0086","type":"journal-article","created":{"date-parts":[[2022,7,25]],"date-time":"2022-07-25T09:13:05Z","timestamp":1658740385000},"page":"794-799","source":"Crossref","is-referenced-by-count":6,"title":["A rare presentation of type II Abernethy malformation and nephrotic syndrome: Case report and review"],"prefix":"10.1515","volume":"17","author":[{"given":"Xin","family":"Wu","sequence":"first","affiliation":[{"name":"Department of Pediatrics, Taizhou Central Hospital (Taizhou University Hospital) , Taizhou 318001 , China"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Weizhong","family":"Gu","sequence":"additional","affiliation":[{"name":"Department of Pathology, The Children\u2019s Hospital, Zhejiang University School of Medicine, National Clinical Research Center for Child Health , Hangzhou 310005 , China"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Yongzhi","family":"Lin","sequence":"additional","affiliation":[{"name":"Department of Pediatrics Surgery, Taizhou Central Hospital (Taizhou University Hospital) , Taizhou 318001 , China"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Lina","family":"Ye","sequence":"additional","affiliation":[{"name":"Department of General Surgery, Taizhou Central Hospital (Taizhou University Hospital) , Taizhou 318001 , China"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"374","published-online":{"date-parts":[[2022,7,21]]},"reference":[{"key":"2022120618363532475_j_biol-2022-0086_ref_001","doi-asserted-by":"crossref","unstructured":"Howard ER, Davenport M. Congenital extrahepatic portocaval shunts-the Abernethy malformation. J Pediatr Surg. 1997;32(3):494\u20137.","DOI":"10.1016\/S0022-3468(97)90614-X"},{"key":"2022120618363532475_j_biol-2022-0086_ref_002","doi-asserted-by":"crossref","unstructured":"Baiges A, Turon F, Sim\u00f3n-Talero M, Tasayco S, Bueno J, Zekrini K, et al. Congenital extrahepatic portosystemic shunts (Abernethy Malformation): An international observational study. Hepatology. 2020;71(2):658\u201369.","DOI":"10.1002\/hep.30817"},{"key":"2022120618363532475_j_biol-2022-0086_ref_003","unstructured":"Abernethy J. Account of two instances of uncommon formation in the viscera of the human body: From the philosophical transactions of the royal society of London. Med Facts Obs. 1797;7:100\u20138."},{"key":"2022120618363532475_j_biol-2022-0086_ref_004","doi-asserted-by":"crossref","unstructured":"Morgan G, Superina R. 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