{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,10]],"date-time":"2025-10-10T18:59:00Z","timestamp":1760122740663,"version":"3.40.5"},"reference-count":10,"publisher":"Walter de Gruyter GmbH","issue":"4","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2018,3,28]]},"abstract":"Abstract<\/jats:title>\n \n Background:<\/jats:title>\n Acquired lipodystrophy, craniopharyngioma and chronic inflammatory demyelinating polyneuropathy (CIDP) are individually rare disorders, and have never before been reported in a single patient.<\/jats:p>\n <\/jats:sec>\n \n Case presentation:<\/jats:title>\n A 15-year-7 month old Caucasian male presented with lower extremity weakness, frequent falls and abnormal fat distribution occurring over the previous 1 year. He was diagnosed with CIDP, craniopharyngioma and acquired lipodystrophy. The patient underwent tumor debulking and cranial irradiation for the craniopharyngioma, and received monthly intravenous immunoglobulin for the CIDP. The patient initially had some resolution of the lipodystrophy phenotype, but subsequently the abnormal fat distribution recurred and the patient developed additional systemic abnormalities, including mild pancytopenia and hepatic fibrosis.<\/jats:p>\n <\/jats:sec>\n \n Conclusions:<\/jats:title>\n Our patient represents a novel association of acquired lipodystrophy, craniopharyngioma, and CIDP, possibly due to an as yet unidentified paraneoplastic autoantibody.<\/jats:p>\n <\/jats:sec>","DOI":"10.1515\/jpem-2017-0222","type":"journal-article","created":{"date-parts":[[2018,2,27]],"date-time":"2018-02-27T10:45:40Z","timestamp":1519728340000},"page":"479-483","source":"Crossref","is-referenced-by-count":3,"title":["A novel paraneoplastic syndrome with acquired lipodystrophy and chronic inflammatory demyelinating polyneuropathy in an adolescent male with craniopharyngioma"],"prefix":"10.1515","volume":"31","author":[{"given":"Hillary Elizabeth","family":"Lockemer","sequence":"first","affiliation":[{"name":"Division of Pediatric Endocrinology, Department of Pediatrics , UT Southwestern Medical Center , Dallas, TX , USA"},{"name":"Department of Pediatric Endocrinology , WakeMed Health and Hospitals , Raleigh, NC , USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-2182-9574","authenticated-orcid":false,"given":"Kathryn Maria","family":"Sumpter","sequence":"additional","affiliation":[{"name":"Division of Pediatric Endocrinology, Department of Pediatrics , UT Southwestern Medical Center , Dallas, TX , USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Sandy","family":"Cope-Yokoyama","sequence":"additional","affiliation":[{"name":"Department of Pathology , UT Southwestern Medical Center , Dallas, TX , USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Abhimanyu","family":"Garg","sequence":"additional","affiliation":[{"name":"Division of Nutrition and Metabolic Diseases and the Center for Human Nutrition, Department of Internal Medicine , UT Southwestern Medical Center , K5.214, 5323 Harry Hines Blvd , Dallas, TX 75390-8537 , USA"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"374","published-online":{"date-parts":[[2018,2,19]]},"reference":[{"key":"2021021322312300381_j_jpem-2017-0222_ref_001_w2aab3b7c16b1b6b1ab2b2b1Aa","doi-asserted-by":"crossref","unstructured":"Chan JL, Oral EA. Clinical classification and treatment of congenital and acquired lipodystrophy. Endocr Pract 2010;16:310\u201323.","DOI":"10.4158\/EP09154.RA"},{"key":"2021021322312300381_j_jpem-2017-0222_ref_002_w2aab3b7c16b1b6b1ab2b2b2Aa","doi-asserted-by":"crossref","unstructured":"Garg A. Acquired and inherited lipodystrophies. N Engl J Med 2004;350:1220\u201334.","DOI":"10.1056\/NEJMra025261"},{"key":"2021021322312300381_j_jpem-2017-0222_ref_003_w2aab3b7c16b1b6b1ab2b2b3Aa","doi-asserted-by":"crossref","unstructured":"Herranz P, Lucas R, P\u00e9rez-Espa\u00f1a L, Mayor M. Lipodystrophy syndromes. Dermatol Clin 2008;26:569\u201378.","DOI":"10.1016\/j.det.2008.05.004"},{"key":"2021021322312300381_j_jpem-2017-0222_ref_004_w2aab3b7c16b1b6b1ab2b2b4Aa","doi-asserted-by":"crossref","unstructured":"Misra A, Peethambaram A, Garg A. Clinical features and metabolic and autoimmune derangements in acquired partial lipodystrophy: report of 35 cases and review of the literature. 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