{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,30]],"date-time":"2026-07-30T17:59:18Z","timestamp":1785434358047,"version":"3.56.0"},"reference-count":14,"publisher":"Vilnius University Press","issue":"2","license":[{"start":{"date-parts":[[2025,11,28]],"date-time":"2025-11-28T00:00:00Z","timestamp":1764288000000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["AML"],"abstract":"<jats:p>Background:\u00a0Obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) syndrome is a rare congenital anomaly of the female urogenital tract. This report presents the clinical features, diagnostic approach, and management of an adolescent girl with OHVIRA syndrome.Clinical case:\u00a0A 14-year-old female was admitted with abdominal pain and irregular menstruation. Ultrasonography and MRI demonstrated uterus didelphys with right-sided hematometrocolpos and ipsilateral renal agenesis. External genital examination revealed an intact hymen with a bluish bulge 2 cm above the hymenal ring. Surgical exploration confirmed an obstructed right hemivagina, which was opened while preserving hymenal integrity. Menstrual blood was drained, and a Foley catheter was placed temporarily to ensure patency. The postoperative course was uneventful, and the patient was discharged on the second day.Discussion and Conclusions:\u00a0This case illustrates successful surgical management of OHVIRA syndrome while preserving hymenal integrity. Early diagnosis and imaging are essential to prevent complications such as hematometrocolpos, endometriosis, and infertility.<\/jats:p>","DOI":"10.15388\/amed.2025.32.2.19","type":"journal-article","created":{"date-parts":[[2025,11,28]],"date-time":"2025-11-28T09:19:35Z","timestamp":1764321575000},"page":"19","source":"Crossref","is-referenced-by-count":0,"title":["Obstructed Hemivagina, Uterine Didelphys, and Ipsilateral Renal Agenesis: A Case Report of OHVIRA Syndrome"],"prefix":"10.15388","volume":"32","author":[{"given":"Mehtap","family":"G\u00fcne\u015f","sequence":"first","affiliation":[{"id":[{"id":"https:\/\/ror.org\/023wdy559","id-type":"ROR","asserted-by":"publisher"}],"name":"University of Health Sciences \u0130stanbul \u00dcmranyie Training and Research Hospital"},{"name":"Umraniye Training and Research Hospital"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-9417-2847","authenticated-orcid":false,"given":"Sevin\u00e7","family":"Ta\u015far","sequence":"additional","affiliation":[{"id":[{"id":"https:\/\/ror.org\/023wdy559","id-type":"ROR","asserted-by":"publisher"}],"name":"University of Health Sciences \u0130stanbul \u00dcmranyie Training and Research Hospital"},{"name":"Umraniye Training and Research Hospital"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hayriye Nihan","family":"Karaman Ayy\u0131ld\u0131z","sequence":"additional","affiliation":[{"id":[{"id":"https:\/\/ror.org\/023wdy559","id-type":"ROR","asserted-by":"publisher"}],"name":"University of Health Sciences \u0130stanbul \u00dcmranyie Training and Research Hospital"},{"name":"Umraniye Training and Research Hospital"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"\u0130brahim","family":"Kale","sequence":"additional","affiliation":[{"id":[{"id":"https:\/\/ror.org\/023wdy559","id-type":"ROR","asserted-by":"publisher"}],"name":"University of Health Sciences \u0130stanbul \u00dcmranyie Training and Research Hospital"},{"name":"Umraniye Training and Research Hospital"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0009-0008-3634-8785","authenticated-orcid":false,"given":"Funda","family":"Alp Uydu","sequence":"additional","affiliation":[{"id":[{"id":"https:\/\/ror.org\/023wdy559","id-type":"ROR","asserted-by":"publisher"}],"name":"University of Health Sciences \u0130stanbul \u00dcmranyie Training and Research Hospital"},{"name":"Umraniye Training and Research Hospital"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Murat","family":"Muhcu","sequence":"additional","affiliation":[{"id":[{"id":"https:\/\/ror.org\/023wdy559","id-type":"ROR","asserted-by":"publisher"}],"name":"University of Health Sciences \u0130stanbul \u00dcmranyie Training and Research Hospital"},{"name":"Umraniye Training and Research Hospital"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"6097","published-online":{"date-parts":[[2025,11,28]]},"reference":[{"key":"ref0","doi-asserted-by":"publisher","unstructured":"Moufawad G, Giannini A, D'Oria O, et al. 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