{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,11,7]],"date-time":"2025-11-07T08:45:54Z","timestamp":1762505154819,"version":"3.40.5"},"reference-count":10,"publisher":"American Academy of Pediatrics (AAP)","issue":"2","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2006,8,1]]},"abstract":"<jats:p>Congenital long-QT syndrome with 2:1 atrioventricular block presenting in the perinatal period is rare, has a poor prognosis, and leads to high risk for lethal ventricular arrhythmic events. An implantable cardioverter-defibrillator seems to be the most effective treatment in the prevention of arrhythmic sudden cardiac death in patients with long-QT syndrome. Technical limitations and risks associated with implantable cardioverter-defibrillators in asymptomatic infants is considered too great to justify use for primary prophylaxis against sudden cardiac death. In this case report we describe the first successful parental use of an automated external defibrillator prescribed for primary prophylaxis against sudden cardiac death in an infant with long-QT syndrome.<\/jats:p>","DOI":"10.1542\/peds.2006-0129","type":"journal-article","created":{"date-parts":[[2006,7,1]],"date-time":"2006-07-01T00:57:13Z","timestamp":1151715433000},"page":"e526-e529","source":"Crossref","is-referenced-by-count":32,"title":["Successful Parental Use of an Automated External Defibrillator for an Infant With Long-QT Syndrome"],"prefix":"10.1542","volume":"118","author":[{"given":"Abhay","family":"Divekar","sequence":"first","affiliation":[{"name":"Section of Pediatric Cardiology, Department of Pediatrics, Health Sciences Center, University of Manitoba, Winnipeg, Manitoba, Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Reeni","family":"Soni","sequence":"additional","affiliation":[{"name":"Section of Pediatric Cardiology, Department of Pediatrics, Health Sciences Center, University of Manitoba, Winnipeg, Manitoba, Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"417","published-online":{"date-parts":[[2006,8,1]]},"reference":[{"key":"2021120822395595000_R1","doi-asserted-by":"crossref","unstructured":"Trippel DL, Parsons MK, Gillette PC. Infants with long-QT syndrome and 2:1 atrioventricular block. Am Heart J.\u20081995;130:1130\u20131134","DOI":"10.1016\/0002-8703(95)90222-8"},{"key":"2021120822395595000_R2","doi-asserted-by":"crossref","unstructured":"Bar-Cohen Y, Walsh EP, Love BA, Cecchin F. First appropriate use of automated external defibrillator in an infant. Resuscitation.\u20082005;67:135\u2013137","DOI":"10.1016\/j.resuscitation.2005.05.003"},{"key":"2021120822395595000_R3","doi-asserted-by":"crossref","unstructured":"Gurnett CA, Atkins DL. Successful use of a biphasic waveform automated external defibrillator in a high-risk child. Am J Cardiol.\u20082000;86:1051\u20131053","DOI":"10.1016\/S0002-9149(00)01151-6"},{"key":"2021120822395595000_R4","doi-asserted-by":"crossref","unstructured":"Zhang L, Timothy KW, Vincent GM, et al. Spectrum of ST-T-wave patterns and repolarization parameters in congenital long-QT syndrome: ECG findings identify genotypes. 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