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The measurements consisted of respiratory volumes including functional residual capacity, ventilatory mechanics including compliance and resistance, and thoracoabdominal synchrony. Chest wall compliance was 64% below normal, and the thoracoabdominal motion was indicative of predominantly abdominal displacement during inspiratory breaths. The lungs were functioning at a low functional residual capacity, resulting in low lung compliance and increased pulmonary resistance. As a result of the evaluation, the patient was recommended for lateral thoracic expansion surgery and the ventilatory management was adjusted to focus on end-distending pressure support.<\/jats:p>","DOI":"10.1542\/peds.2006-0135","type":"journal-article","created":{"date-parts":[[2006,9,2]],"date-time":"2006-09-02T00:49:34Z","timestamp":1157158174000},"page":"e1264-e1267","source":"Crossref","is-referenced-by-count":4,"title":["Pulmonary Function Assessment in an Infant With Barnes Syndrome: Proactive Evaluation for Surgical Intervention"],"prefix":"10.1542","volume":"118","author":[{"given":"Thomas L.","family":"Miller","sequence":"first","affiliation":[{"name":"Nemours Research Lung Center"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Timothy","family":"Cox","sequence":"additional","affiliation":[{"name":"Nemours Children's Clinic, Alfred I. duPont Hospital for Children, Wilmington, Delaware"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Thomas","family":"Blackson","sequence":"additional","affiliation":[{"name":"Christiana Care Health System, Newark, Delaware"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"David","family":"Paul","sequence":"additional","affiliation":[{"name":"Christiana Care Health System, Newark, Delaware"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kerry","family":"Weiss","sequence":"additional","affiliation":[{"name":"St Peter's University Hospital, New Brunswick, New Jersey"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Thomas H.","family":"Shaffer","sequence":"additional","affiliation":[{"name":"Nemours Research Lung Center"},{"name":"Departments of Physiology and Pediatrics, Temple University School of Medicine, Philadelphia, Pennsylvania"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"417","published-online":{"date-parts":[[2006,10,1]]},"reference":[{"key":"2021120822435682600_R1","doi-asserted-by":"crossref","unstructured":"Barnes ND, Hull D, Symons JS. 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