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This case highlights the variability of phenotypic presentation and apparent disunity between routine immunologic investigations and severe disease in X-linked agammaglobulinemia, necessitating clinical acumen to make the diagnosis.<\/jats:p>","DOI":"10.1542\/peds.2014-3907","type":"journal-article","created":{"date-parts":[[2015,11,3]],"date-time":"2015-11-03T02:03:51Z","timestamp":1446516231000},"page":"e1621-e1624","source":"Crossref","is-referenced-by-count":9,"title":["X-linked Agammaglobulinemia With Normal Immunoglobulin and Near-Normal Vaccine Seroconversion"],"prefix":"10.1542","volume":"136","author":[{"given":"Kahn","family":"Preece","sequence":"first","affiliation":[{"name":"Paediatric Immunology Department, Starship Children\u2019s Health, Auckland, New Zealand; and"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Graeme","family":"Lear","sequence":"additional","affiliation":[{"name":"Department of Paediatrics, Tairawhiti District Health, Gisborne, New Zealand"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"417","published-online":{"date-parts":[[2015,12,1]]},"reference":[{"key":"2021120906140453000_B1","unstructured":"Modell J. 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