{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,3,22]],"date-time":"2025-03-22T11:14:32Z","timestamp":1742642072660},"reference-count":0,"publisher":"Akademiai Kiado Zrt.","issue":"22","license":[{"start":{"date-parts":[[2020,5,1]],"date-time":"2020-05-01T00:00:00Z","timestamp":1588291200000},"content-version":"unspecified","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["akjournals.com"],"crossmark-restriction":true},"short-container-title":["OH"],"published-print":{"date-parts":[[2020,5]]},"abstract":"<jats:title>Absztrakt: <\/jats:title>\n                <jats:p>Egy h\u00e9t\u00e9ves le\u00e1nygyermek az als\u00f3 \u00e1llcsont lingualis felsz\u00edn\u00e9n szimmetrikusan\n                    elhelyezked\u0151, f\u00e1jdalmatlan, diff\u00faz, nem gyullad\u00e1sos eredet\u0171 \u00ednyduzzanat miatt\n                    ker\u00fclt a Semmelweis Egyetem Parodontol\u00f3giai Klinik\u00e1j\u00e1ra. A csal\u00e1di\n                    k\u00f3rt\u00f6rt\u00e9netb\u0151l kider\u00fclt, hogy a p\u00e1ciens \u00e9desanyja \u00e9s testv\u00e9re\n                    Recklinghausen-k\u00f3rban szenved, a neurofibromatosis-1 (NF1) jellegzetes\n                    b\u0151rt\u00fcneteivel. Mindketten tagjai a Nemzeti NF Regiszternek. Az extraoralis\n                    vizsg\u00e1lat sor\u00e1n a mandibula protrusi\u00f3ja volt \u00e9szlelhet\u0151. Az intraoralis\n                    vizsg\u00e1latkor az \u00edny mindk\u00e9t \u00e1llcsonton buccalisan teljesen \u00e9p \u00e9s gyullad\u00e1smentes\n                    volt. A p\u00e1ciensen a neurofibromatosis (NF1) egy\u00e9b jellegzetes b\u0151rt\u00fcnetei nem\n                    voltak \u00e9szlelhet\u0151k. Sz\u00fcl\u0151i beleegyez\u00e9ssel lok\u00e1lis \u00e9rz\u00e9stelen\u00edt\u00e9s mellett ker\u00fclt\n                    sor a lingualis sz\u00f6vetszaporulat seb\u00e9szi elt\u00e1vol\u00edt\u00e1s\u00e1ra \u00e9s ennek hisztol\u00f3giai\n                    vizsg\u00e1lat\u00e1ra. A sz\u00f6vettani vizsg\u00e1lat igazolta a solitaer neurofibroma\n                    diagn\u00f3zis\u00e1t. A posztoperat\u00edv gy\u00f3gyul\u00e1s zavartalan volt. A p\u00e1ciens fiatal\n                    \u00e9letkor\u00e1ra, valamint az elv\u00e1ltoz\u00e1s nem <jats:italic>in toto<\/jats:italic> elt\u00e1vol\u00edt\u00e1s\u00e1ra\n                    val\u00f3 tekintettel a gyermeket folyamatosan ellen\u0151rizz\u00fck. M\u00e1sf\u00e9l \u00e9vvel a m\u0171t\u00e9tet\n                    k\u00f6vet\u0151en recid\u00edva nem l\u00e9pett fel. A panor\u00e1ma-r\u00f6ntgenfelv\u00e9telen az \u00e9letkornak\n                    megfelel\u0151 vegyes fogazatot \u00e9s a zavartalan fogv\u00e1lt\u00e1s jeleit \u00e9szlelt\u00fck, egy\u00e9b\n                    k\u00f3ros skeletalis elv\u00e1ltoz\u00e1s n\u00e9lk\u00fcl. Nagyon ritka, hogy egy genetikailag igazolt\n                    Recklinghausen-k\u00f3rban szenved\u0151 csal\u00e1dban egy h\u00e9t\u00e9ves p\u00e1ciens sz\u00e1j\u00e1ban\n                    hisztol\u00f3giailag igazolt bilateralis gingivalis neurofibroma fejl\u0151dj\u00f6n ki, egy\u00e9b\n                    jellegzetes b\u0151relv\u00e1ltoz\u00e1sok n\u00e9lk\u00fcl. Eddig ilyen esetet az el\u00e9rhet\u0151 nemzetk\u00f6zi\n                    irodalomban nem v\u00e9lt\u00fcnk felfedezni. Orv Hetil. 2020; 161(22): 924\u2013930.<\/jats:p>","DOI":"10.1556\/650.2020.31737","type":"journal-article","created":{"date-parts":[[2020,5,27]],"date-time":"2020-05-27T10:22:18Z","timestamp":1590574938000},"page":"924-930","update-policy":"http:\/\/dx.doi.org\/10.1556\/policypage.crossmark.crossref.1","source":"Crossref","is-referenced-by-count":1,"title":["Neurofibromatosisban szenved\u0151 anya h\u00e9t\u00e9ves le\u00e1nya als\u00f3 \u00e1llcsontj\u00e1nak k\u00f6z\u00e9pvonal\u00e1ban kifejl\u0151d\u0151, klinikailag gingivalis hyperplasia k\u00e9p\u00e9ben jelentkez\u0151 neurofibroma"],"prefix":"10.1556","volume":"161","author":[{"given":"M\u00e1ria","family":"Eper","sequence":"first","affiliation":[{"name":"1 Fogorvostudom\u00e1nyi Kar, Parodontol\u00f3giai Klinika, Semmelweis Egyetem Budapest, Szentkir\u00e1lyi u. 47., 1088"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"P\u00e9ter","family":"Nagy","sequence":"additional","affiliation":[{"name":"2 \u00c1ltal\u00e1nos Orvostudom\u00e1nyi Kar, I. Patol\u00f3giai \u00e9s K\u00eds\u00e9rleti R\u00e1kkutat\u00f3 Int\u00e9zet, Semmelweis Egyetem Budapest"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Istv\u00e1n","family":"Gera","sequence":"additional","affiliation":[{"name":"1 Fogorvostudom\u00e1nyi Kar, Parodontol\u00f3giai Klinika, Semmelweis Egyetem Budapest, Szentkir\u00e1lyi u. 47., 1088"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"425","container-title":["Orvosi Hetilap"],"original-title":[],"link":[{"URL":"https:\/\/akjournals.com\/view\/journals\/650\/161\/22\/article-p924.xml","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/akjournals.com\/downloadpdf\/journals\/650\/161\/22\/article-p924.xml","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,10,11]],"date-time":"2021-10-11T01:14:05Z","timestamp":1633914845000},"score":1,"resource":{"primary":{"URL":"https:\/\/akjournals.com\/view\/journals\/650\/161\/22\/article-p924.xml"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2020,5]]},"references-count":0,"journal-issue":{"issue":"22"},"URL":"https:\/\/doi.org\/10.1556\/650.2020.31737","relation":{},"ISSN":["0030-6002","1788-6120"],"issn-type":[{"value":"0030-6002","type":"print"},{"value":"1788-6120","type":"electronic"}],"subject":[],"published":{"date-parts":[[2020,5]]}}}