{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2024,8,5]],"date-time":"2024-08-05T15:14:31Z","timestamp":1722870871538},"reference-count":17,"publisher":"Akademiai Kiado Zrt.","issue":"2","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["MaSeb"],"published-print":{"date-parts":[[2009,4,1]]},"abstract":"<jats:title>Absztrakt<\/jats:title>\n        <jats:p>\n          <jats:italic>Esetismertet\u00e9s:<\/jats:italic> Ismertetj\u00fck egy fiatal n\u0151beteg rendk\u00edv\u00fcl ritka retroperitonealis daganat\u00e1nak, a vena cava inferior primer leiomyosarcom\u00e1j\u00e1nak (VCI-LMS) t\u00fcnettan\u00e1t, diagnosztik\u00e1j\u00e1t, valamint seb\u00e9szi kezel\u00e9s\u00e9t. M\u0171t\u00e9t sor\u00e1n der\u00fclt f\u00e9ny a VCI k\u00f6z\u00e9ps\u0151 szegmens\u00e9nek fal\u00e1b\u00f3l kiindul\u00f3, jelent\u0151s m\u00e9ret\u0171 malignit\u00e1sra, amelyet cavaresecti\u00f3val \u00e9s szintetikusgraft-p\u00f3tl\u00e1ssal lehetett rekonstru\u00e1lni. 8 \u00e9vvel k\u00e9s\u0151bb recid\u00edva miatt \u00fajabb m\u0171t\u00e9tre ker\u00fclt sor, azonban a bal v. renalis \u00e9rintetts\u00e9ge komoly m\u0171t\u00e9ttechnikai probl\u00e9m\u00e1kat vetett fel. \u00dajabb cavaresectio \u00e9s graftp\u00f3tl\u00e1sos v. renalis reimplant\u00e1ci\u00f3 t\u00f6rt\u00e9nt. A beteg sz\u00f6v\u0151dm\u00e9nymentesen t\u00e1vozott otthon\u00e1ba. <jats:italic>Megbesz\u00e9l\u00e9s:<\/jats:italic> A VCI-LMS egy rendk\u00edv\u00fcl ritka seb\u00e9sz-patol\u00f3giai entit\u00e1s, mely a v\u00e9nafal medi\u00e1j\u00e1b\u00f3l kiindulva terjedhet intraluminalisan, extraluminalisan vagy mindk\u00e9t ir\u00e1nyba egyar\u00e1nt. Lokaliz\u00e1ci\u00f3j\u00e1t\u00f3l f\u00fcgg\u0151en, amennyiben az 1. szegmensben (vv. hepaticae f\u00f6l\u00f6tt), a 2. szegmensben (vv. renales \u00e9s vv. hepaticae k\u00f6z\u00f6tt) vagy a 3. szegmensben (vv. renales \u00e9s v. iliaca k\u00f6z\u00f6tt) tal\u00e1lhat\u00f3, kapcsolatban lehet a m\u00e1j, illetve a vese ven\u00e1ival, azokat infiltr\u00e1lva. T\u00fcnettanilag a fels\u0151 szegmens tumora a Budd\u2013Chiari-t\u00fcnetegy\u00fcttes (hepatomegalia, hasi f\u00e1jdalom, s\u00e1rgas\u00e1g, ascites) mellett rendk\u00edv\u00fcl rossz progn\u00f3zis\u00fa, m\u00edg a k\u00f6z\u00e9ps\u0151 lokaliz\u00e1ci\u00f3j\u00fa jobb felhasi f\u00e1jdalom mellett epe\u00fati megbeteged\u00e9s k\u00e9p\u00e9t ut\u00e1nozza, \u00e9s jelent\u0151sen jobb hossz\u00fa t\u00e1v\u00fa kimenetellel b\u00edr. A tapasztalat azt mutatja, hogy a radio-kemoter\u00e1pia ezen daganat kezel\u00e9s\u00e9ben nem j\u00e1rhat\u00f3 \u00fat. A radik\u00e1lis \u2018en bloc\u2019-resectio tumormentes sz\u00e9lek biztos\u00edt\u00e1s\u00e1val, majd az \u00e9rintett szakasz rekonstrukci\u00f3ja jelenti az egyetlen adekv\u00e1t kezel\u00e9si m\u00f3dot.<\/jats:p>","DOI":"10.1556\/maseb.62.2009.2.6","type":"journal-article","created":{"date-parts":[[2009,4,23]],"date-time":"2009-04-23T01:12:51Z","timestamp":1240449171000},"page":"83-86","source":"Crossref","is-referenced-by-count":2,"title":["Primer vena cava inferior leiomyosarcoma (VCI-LMS) seb\u00e9szi kezel\u00e9ser"],"prefix":"10.1556","volume":"62","author":[{"given":"Zolt\u00e1n J\u00f3zsef","family":"Bir\u00f3","sequence":"first","affiliation":[{"name":"1 Seb\u00e9szeti Klinika, P\u00e9csi Tudom\u00e1nyegyetem, \u00c1ltal\u00e1nos Orvostudom\u00e1nyi Kar, Klinikai K\u00f6zpont, 7624, P\u00e9cs, Ifj\u00fas\u00e1g \u00fat 13."}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"K\u00e1roly","family":"Kalm\u00e1r Nagy","sequence":"additional","affiliation":[{"name":"1 Seb\u00e9szeti Klinika, P\u00e9csi Tudom\u00e1nyegyetem, \u00c1ltal\u00e1nos Orvostudom\u00e1nyi Kar, Klinikai K\u00f6zpont, 7624, P\u00e9cs, Ifj\u00fas\u00e1g \u00fat 13."}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Eszter","family":"Feh\u00e9r","sequence":"additional","affiliation":[{"name":"2 Radiol\u00f3giai Klinika, P\u00e9csi Tudom\u00e1nyegyetem, \u00c1ltal\u00e1nos Orvostudom\u00e1nyi Kar, Klinikai K\u00f6zpont, P\u00e9cs"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"\u00c9va","family":"G\u00f6m\u00f6ri","sequence":"additional","affiliation":[{"name":"3 Pathol\u00f3giai Int\u00e9zet, P\u00e9csi Tudom\u00e1nyegyetem, \u00c1ltal\u00e1nos Orvostudom\u00e1nyi Kar, Klinikai K\u00f6zpont, P\u00e9cs"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"\u00d6rs P\u00e9ter","family":"Horv\u00e1th","sequence":"additional","affiliation":[{"name":"1 Seb\u00e9szeti Klinika, P\u00e9csi Tudom\u00e1nyegyetem, \u00c1ltal\u00e1nos Orvostudom\u00e1nyi Kar, Klinikai K\u00f6zpont, 7624, P\u00e9cs, Ifj\u00fas\u00e1g \u00fat 13."}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"425","reference":[{"key":"1","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1016\/S0039-6060(97)90179-3","article-title":"Radical resection of tumours of the inferior vena cava with vascular reconstruction and kidney autotransplantation","volume":"121","author":"Kraybill WG","year":"1997","journal-title":"Surgery"},{"key":"2","doi-asserted-by":"crossref","first-page":"1077","DOI":"10.1002\/(SICI)1097-0142(19990301)85:5<1077::AID-CNCR10>3.0.CO;2-0","article-title":"Leiomyosarcoma of the inferior vena cava","volume":"85","author":"Hinnes OJ","year":"1999","journal-title":"Cancer"},{"key":"3","first-page":"455","article-title":"Intramural leiomyosarcoma of the inferior vena cava. 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