{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2023,10,30]],"date-time":"2023-10-30T10:24:10Z","timestamp":1698661450280},"reference-count":14,"publisher":"Akademiai Kiado Zrt.","issue":"40","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2008,10,1]]},"abstract":"<jats:p>A szerz\u0151k \n <jats:italic>c\u00e9lja<\/jats:italic>\n volt csecsem\u0151korban vizsg\u00e1lni a velesz\u00fcletett mitralisbillenty\u0171-sz\u0171k\u00fclet \u00e9s -el\u00e9gtelens\u00e9g seb\u00e9szi kezel\u00e9s\u00e9t, valamint a komplett atrioventricularis septumdefektus (CAVD) teljes korrekci\u00f3ja sor\u00e1n a mitralis billenty\u0171 kialak\u00edt\u00e1s\u00e1nak, p\u00f3tl\u00e1s\u00e1nak lehet\u0151s\u00e9g\u00e9t. \n <jats:italic>Betegek:<\/jats:italic>\n 2001 \u00e9s 2007 k\u00f6z\u00f6tt 82, egy \u00e9vn\u00e9l fiatalabb csecsem\u0151n a korrekci\u00f3s m\u0171t\u00e9tet k\u00f6vet\u0151en 7 betegben (5 h\u00e9t\u20137 h\u00f3nap, 3,5\u20135 kg) mitralis (bileaflet) m\u0171billenty\u0171 korai be\u00fcltet\u00e9se v\u00e1lt sz\u00fcks\u00e9gess\u00e9. A k\u00e9t m\u0171t\u00e9t k\u00f6zti id\u0151 0\u20137 nap, de a legkisebb csecsem\u0151n\u00e9l intenz\u00edv kezel\u00e9s mellett 38 napot kellett v\u00e1rni az annulus felt\u00e1gul\u00e1s\u00e1ra, hogy a legkisebb m\u0171billenty\u0171 be\u00fcltethet\u0151 lehessen. A\u00a0m\u0171billenty\u0171k t\u00edpusa: 16 mm-es Carbomedics 2, 16 mm-es ATS 3, 17 mm-es Sorin 1, 19 mm-es Sorin 1. Congenitalis mitralis stenosis, illetve insufficientia miatt 2-2 csecsem\u0151be kellett 16 mm-es ATS billenty\u0171t be\u00fcltetni. \n <jats:italic>Eredm\u00e9ny:<\/jats:italic>\n 30 napos mortalit\u00e1s 0. Egy-egy csecsem\u0151 a 46., illetve a 71. posztoperat\u00edv napon szepszisben meghalt. 1\u20136 (\u00e1tlag 3) \u00e9ves ut\u00e1nk\u00f6vet\u00e9s: 1 betegben kellett\u00a0pannust elt\u00e1vol\u00edtani, a betegek panaszmentesek. Az antikoagul\u00e1ns ter\u00e1pia helyes be\u00e1ll\u00edt\u00e1sa neh\u00e9zs\u00e9get jelentett. \n <jats:italic>\u00d6sszefoglal\u00e1s:<\/jats:italic>\n Congenitalis mitralis stenosis \u00e9s el\u00e9gtelens\u00e9g, valamint a CAVD seb\u00e9szi korrekci\u00f3ja m\u00e1r kis s\u00faly\u00fa \u00fajsz\u00fcl\u00f6tteken is sikerrel elv\u00e9gezhet\u0151. Kedvez\u0151tlen anat\u00f3miai helyzetben a mitralis billenty\u0171 kialak\u00edt\u00e1s\u00e1nak lehetetlens\u00e9ge eset\u00e9n csak a m\u0171billenty\u0171-be\u00fcltet\u00e9s a megold\u00e1s. Ez kil\u00e1t\u00e1stalannak t\u0171n\u0151 helyzetben (kis mitralis annulus) is elv\u00e9gezhet\u0151 j\u00f3 eredm\u00e9nnyel. (Tudom\u00e1sunk szerint 3500 g s\u00faly\u00fa beteg\u00fcnk a legkisebb, sikeresen oper\u00e1lt eset.) Ezt igazolj\u00e1k eseteink korai \u00e9s k\u00f6z\u00e9pt\u00e1v\u00fa eredm\u00e9nyei.<\/jats:p>","DOI":"10.1556\/oh.2008.28417","type":"journal-article","created":{"date-parts":[[2008,9,25]],"date-time":"2008-09-25T01:08:32Z","timestamp":1222304912000},"page":"1891-1894","source":"Crossref","is-referenced-by-count":1,"title":["Surgical management with mitral valve replacement in young infants with congenital mitral valve diseases and complete atrioventricular septal defect"],"prefix":"10.1556","volume":"149","author":[{"given":"Istv\u00e1n","family":"Harty\u00e1nszky","sequence":"first","affiliation":[{"name":"1 Gottsegen Gy\u00f6rgy Orsz\u00e1gos Kardiol\u00f3giai Int\u00e9zet Gyermeksz\u00edv K\u00f6zpont Budapest Haller u. 29. 1096"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"S\u00e1ndor","family":"Mih\u00e1lyi","sequence":"additional","affiliation":[{"name":"1 Gottsegen Gy\u00f6rgy Orsz\u00e1gos Kardiol\u00f3giai Int\u00e9zet Gyermeksz\u00edv K\u00f6zpont Budapest Haller u. 29. 1096"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"G\u00e1bor","family":"Bodor","sequence":"additional","affiliation":[{"name":"1 Gottsegen Gy\u00f6rgy Orsz\u00e1gos Kardiol\u00f3giai Int\u00e9zet Gyermeksz\u00edv K\u00f6zpont Budapest Haller u. 29. 1096"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"425","reference":[{"key":"atypb1","volume-title":"Pediatric cardiac surgery","year":"2003"},{"key":"atypb2","doi-asserted-by":"crossref","first-page":"860","DOI":"10.1016\/j.ejcts.2007.02.006","volume":"31","year":"2007","journal-title":"Eu. 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