{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,4,9]],"date-time":"2025-04-09T05:47:50Z","timestamp":1744177670714},"reference-count":28,"publisher":"FapUNIFESP (SciELO)","issue":"10","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Arq. Neuro-Psiquiatr."],"abstract":"<jats:p>Amyotrophic lateral sclerosis is a progressive neuromuscular disease, resulting in respiratory muscle weakness, reduced pulmonary volumes, ineffective cough, secretion retention, and respiratory failure. Measures as vital capacity, maximal inspiratory and expiratory pressures, sniff nasal inspiratory pressure, cough peak flow and pulse oximetry are recommended to monitor the respiratory function. The patients should be followed up by a multidisciplinary team, focused in improving the quality of life and deal with the respiratory symptoms. The respiratory care approach includes airway clearance techniques, mechanically assisted cough and noninvasive mechanical ventilation. Vaccination and respiratory pharmacological support are also recommended. To date, there is no enough evidence supporting the inspiratory muscle training and diaphragmatic pacing.<\/jats:p>","DOI":"10.1590\/0004-282x20150132","type":"journal-article","created":{"date-parts":[[2015,8,29]],"date-time":"2015-08-29T23:12:56Z","timestamp":1440889976000},"page":"873-876","source":"Crossref","is-referenced-by-count":5,"title":["Current issues in the respiratory care of patients with amyotrophic lateral sclerosis"],"prefix":"10.1590","volume":"73","author":[{"given":"Marco","family":"Orsini","sequence":"first","affiliation":[{"name":"Centro Universit\u00e1rio Augusto Motta, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Agnaldo Jos\u00e9","family":"Lopes","sequence":"additional","affiliation":[{"name":"Centro Universit\u00e1rio Augusto Motta, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Sara Lucia Silveira de","family":"Menezes","sequence":"additional","affiliation":[{"name":"Centro Universit\u00e1rio Augusto Motta, Brazil; Universidade Federal do Rio de Janeiro, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Acary Bulle","family":"Oliveira","sequence":"additional","affiliation":[{"name":"Universidade Federal de S\u00e3o Paulo, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Marcos Raimundo Gomes de","family":"Freitas","sequence":"additional","affiliation":[{"name":"Universidade Federal Fluminense, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Osvaldo Jose Moreira do","family":"Nascimento","sequence":"additional","affiliation":[{"name":"Universidade Federal Fluminense, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Fernando Silva","family":"Guimar\u00e3es","sequence":"additional","affiliation":[{"name":"Centro Universit\u00e1rio Augusto Motta, Brazil; Universidade Federal do Rio de Janeiro, Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"530","published-online":{"date-parts":[[2015,9,1]]},"reference":[{"key":"ref1","first-page":"1","article-title":"Prevalence of amyotrophic lateral sclerosis - United States, 2010-2011","volume":"63","author":"Mehta P","year":"2014","journal-title":"MMWR Surveill Summ"},{"issue":"3","key":"ref2","doi-asserted-by":"crossref","first-page":"668","DOI":"10.1016\/j.clinthera.2014.12.020","article-title":"Therapeutic development in amyotrophic lateral sclerosis","volume":"37","author":"Bucchia M","year":"2015","journal-title":"Clin Ther"},{"issue":"5","key":"ref3","doi-asserted-by":"crossref","first-page":"524","DOI":"10.1097\/WCO.0000000000000135","article-title":"The evidence for symptomatic treatments in amyotrophic lateral sclerosis","volume":"27","author":"Jenkins TM","year":"2014","journal-title":"Curr Opin Neurol"},{"issue":"4","key":"ref4","doi-asserted-by":"crossref","first-page":"533","DOI":"10.4187\/respcare.03367","article-title":"Muscle impairment in neuromuscular disease using an expiratory\/inspiratory pressure ratio","volume":"60","author":"Fregonezi G","year":"2015","journal-title":"Respir Care"},{"issue":"6","key":"ref5","doi-asserted-by":"crossref","first-page":"719","DOI":"10.1590\/S0100-879X1999000600007","article-title":"Reference values for lung function tests. 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