{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,1]],"date-time":"2026-10-01T06:53:03Z","timestamp":1790837583562,"version":"4.1.0"},"reference-count":30,"publisher":"FapUNIFESP (SciELO)","issue":"3","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Arq. Neuro-Psiquiatr."],"abstract":"<jats:p>ABSTRACT  Objective To assess central auditory function in Friedreich's ataxia.  Methods A cross-sectional, retrospective study was carried out. Thirty patients underwent the anamnesis, otorhinolaryngology examination, pure tone audiometry, acoustic immittance measures and brainstem auditory evoked potential (BAEP) assessments.  Results The observed alterations were: 43.3% in the pure tone audiometry, bilateral in 36.7%; 56.6% in the BAEP test, bilateral in 50%; and 46.6% in the acoustic immittance test. There was a significant difference (p &lt; 0.05) in the comparison between the tests performed.  Conclusion In the audiological screening, there was a prevalence of the descending audiometric configuration at the frequency of 4kHz, and absence of the acoustic reflex at the same frequency. In the BAEP test, there was a prevalence of an increase of the latencies in waves I, III and V, and in the intervals of interpeaks I-III, I-V and III-V. In 13.3% of the patients, wave V was absent, and all waves were absent in 3.3% of patients.<\/jats:p>","DOI":"10.1590\/0004-282x20180008","type":"journal-article","created":{"date-parts":[[2018,3,24]],"date-time":"2018-03-24T20:13:54Z","timestamp":1521922434000},"page":"170-176","source":"Crossref","is-referenced-by-count":10,"title":["The importance of central auditory evaluation in Friedreich's ataxia"],"prefix":"10.1590","volume":"76","author":[{"given":"Bianca Simone","family":"Zeigelboim","sequence":"first","affiliation":[{"name":"Univesidade Tuiuti do Paran\u00e1,  Brazil"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"H\u00e9lio A. G.","family":"Teive","sequence":"additional","affiliation":[{"name":"Universidade Federal do Paran\u00e1,  Brazil"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mich\u00e8lli Rodrigues da","family":"Rosa","sequence":"additional","affiliation":[{"name":"Univesidade Tuiuti do Paran\u00e1,  Brazil"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"J\u00e9ssica Spricigo","family":"Malisky","sequence":"additional","affiliation":[{"name":"Univesidade Tuiuti do Paran\u00e1,  Brazil"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Vinicius Ribas","family":"Fonseca","sequence":"additional","affiliation":[{"name":"Univesidade Tuiuti do Paran\u00e1,  Brazil"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jair Mendes","family":"Marques","sequence":"additional","affiliation":[{"name":"Univesidade Tuiuti do Paran\u00e1,  Brazil"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Paulo 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