{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,4,22]],"date-time":"2026-04-22T19:04:33Z","timestamp":1776884673465,"version":"3.51.2"},"reference-count":21,"publisher":"FapUNIFESP (SciELO)","issue":"2","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Rev. Assoc. Med. Bras."],"abstract":"<jats:p>Summary  Introduction: Pseudomyxoma peritonei (PMP) is a rare clinical condition, with an incidence of 1-2 cases per million, characterized by the dissemination of mucinous implants on the peritoneal surface and progressive gelatinous ascites. Although it usually presents an indolent behavior, its non-specific clinical presentation contributes to many cases remaining undiagnosed until a laparotomy is performed. With late diagnosis, performed after a long period of clinical deterioration and disease progression, it is common to find complications such as the formation of intestinal fistulas and obstruction.  Method: Review of the medical record and search for references in the Medline, Lilacs, SciELO and MD Consult databases.  Results: There are rare case reports found in the literature demonstrating atypical PMP presentations. Our report is that of a 17-year-old adolescent with a sporadic tumor diagnosed in a primary site in the transverse colon, contrary to data commonly found in the literature that mention a more frequent occurrence in women in the fifth decade of life and with a primary site in the ovary and appendix. The development of mucinous adenocarcinoma is rare in the pediatric population, and topography in the transverse colon and non-familial sporadic pattern are unusual.  Conclusion: The case reported not only raises awareness about the atypical presentations of the disease, but also emphasizes the use of imaging examinations for diagnosis, which has an important impact on prognosis and survival if performed timely.<\/jats:p>","DOI":"10.1590\/1806-9282.64.02.195","type":"journal-article","created":{"date-parts":[[2018,4,4]],"date-time":"2018-04-04T15:24:04Z","timestamp":1522855444000},"page":"195-199","source":"Crossref","is-referenced-by-count":3,"title":["Pseudomyxoma peritonei in a pediatric patient: A case report and literature review"],"prefix":"10.1590","volume":"64","author":[{"given":"Ana Claudia de Oliveira","family":"Fernandes","sequence":"first","affiliation":[{"name":"Hospital A.C. Camargo Cancer Center,  Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Gustavo Ricardo Martins da","family":"Rocha","sequence":"additional","affiliation":[{"name":"Hospital A.C. Camargo Cancer Center,  Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-9169-3153","authenticated-orcid":false,"given":"Alex Dias de","family":"Oliveira","sequence":"additional","affiliation":[{"name":"Hospital A.C. Camargo Cancer Center,  Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Marcos Duarte","family":"Guimar\u00e3es","sequence":"additional","affiliation":[{"name":"Hospital A.C. Camargo Cancer Center,  Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Stefane Cajango de","family":"Carvalho","sequence":"additional","affiliation":[{"name":"Hospital A.C. Camargo Cancer Center,  Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Rubens","family":"Chojniak","sequence":"additional","affiliation":[{"name":"Hospital A.C. 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case report","volume":"109","author":"Mavrodin CJ","year":"2014","journal-title":"Chirurgia (Bucur)"},{"key":"ref5","doi-asserted-by":"crossref","first-page":"71","DOI":"10.1186\/1750-1172-9-71","article-title":"Secreted mucins in pseudomyxoma peritonei: pathophysiological significance and potential therapeutic prospects","volume":"9","author":"Amini A","year":"2014","journal-title":"Orphanet J Rare Dis"},{"key":"ref6","doi-asserted-by":"crossref","first-page":"355","DOI":"10.12659\/AJCR.890837","article-title":"Appendiceal mucocele and pseudomyxoma peritonei, boundaries of a subtle disease","volume":"15","author":"Spyropoulos C","year":"2014","journal-title":"Am J Case Rep"},{"issue":"43","key":"ref7","doi-asserted-by":"crossref","first-page":"4757","DOI":"10.3748\/wjg.v17.i43.4757","article-title":"Spectrum of mucin-producing neoplastic conditions of the abdomen and pelvis: cross-sectional imaging evaluation","volume":"17","author":"Lee NK","year":"2011","journal-title":"World J Gastroenterol"},{"key":"ref8","first-page":"608016","article-title":"Pseudomyxoma peritonei originating from an intestinal duplication","volume":"2013","author":"Lemahieu J","year":"2013","journal-title":"Case Rep Pathol"},{"key":"ref9","doi-asserted-by":"crossref","first-page":"14","DOI":"10.1102\/1470-7330.2013.0003","article-title":"Mucinous neoplasms of the appendix: a current comprehensive clinicopathologic and imaging review","volume":"13","author":"Tirumani SH","year":"2013","journal-title":"Cancer Imaging"},{"issue":"2","key":"ref10","doi-asserted-by":"crossref","first-page":"85","DOI":"10.2463\/mrms.8.85","article-title":"Mucinous cystadenocarcinoma of the urachus associated with pseudomyxoma peritonei with emphasis on MR findings","volume":"8","author":"Sugiyama K","year":"2009","journal-title":"Magn Reson Med Sci"},{"issue":"1","key":"ref11","doi-asserted-by":"crossref","first-page":"44","DOI":"10.4251\/wjgo.v2.i1.44","article-title":"Pseudomyxoma peritonei","volume":"2","author":"Bevan KE","year":"2010","journal-title":"World J Gastroinst Oncol"},{"issue":"2","key":"ref12","first-page":"227","article-title":"Pseudomyxoma peritonei: case report","volume":"33","author":"Nikolic O","year":"2012","journal-title":"Eur J Gynaecol Oncol"},{"key":"ref13","doi-asserted-by":"crossref","first-page":"221","DOI":"10.1186\/s12957-015-0639-x","article-title":"Pseudomyxoma peritonei extending to the lower extremity: a case report","volume":"13","author":"Joo MW","year":"2015","journal-title":"World J Surg Oncol"},{"issue":"16","key":"ref14","doi-asserted-by":"crossref","first-page":"2381","DOI":"10.3748\/wjg.v13.i16.2381","article-title":"Appendiceal mucocoeles and pseudomyxoma peritonei","volume":"13","author":"Dixit A","year":"2007","journal-title":"World J Gastroenterol"},{"issue":"2","key":"ref15","doi-asserted-by":"crossref","first-page":"347","DOI":"10.1148\/rg.292085189","article-title":"Secondary tumors and tumorlike lesions of the peritoneal cavity: imaging features with pathologic correlation","volume":"29","author":"Levy AD","year":"2009","journal-title":"Radiographics"},{"issue":"Suppl 1","key":"ref16","first-page":"S47","article-title":"Management of pseudomyxoma peritonei","volume":"20","author":"Fallis SA","year":"2015","journal-title":"J Buon"},{"key":"ref17","first-page":"926963","article-title":"Aggressive pseudomyxoma peritonei: a case report with an unusual clinical presentation","volume":"2013","author":"Touloumis Z","year":"2013","journal-title":"Case Rep Oncol Med"},{"key":"ref18","doi-asserted-by":"crossref","first-page":"60","DOI":"10.1186\/1477-7819-4-60","article-title":"Pseudomyxoma peritonei: a revisit - 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