{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,24]],"date-time":"2026-09-24T10:51:08Z","timestamp":1790247068378,"version":"4.1.0"},"reference-count":34,"publisher":"FapUNIFESP (SciELO)","issue":"4","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Arq. Gastroenterol."],"published-print":{"date-parts":[[2008,12]]},"abstract":"<jats:p>BACKGROUND: Disturbance in chewing, swallowing and digestive motility may predispose to feeding and nutritional abnormalities in patients with Rett syndrome. OBJECTIVE: To evaluate the dietary habits, nutritional status and the prevalence of constipation in patients with classical Rett syndrome. METHODS: Twenty seven female patients between the ages of 2.6 and 21.8 years were studied. The following parameters were evaluated: food register, weight, height and intestinal movement characteristics. Weight and height were compared with the National Center for Health Statistics standards. RESULTS: The inability to ingest solid foods was observed in 80.8% of the patients. A height-to-age deficit was observed in 13 (48.1%) of the girls, being more intense in patients at stage IV. Weight-for-height deficit was found in 10 (37.0%) patients, 15 (55.6%) showed normal weight and 2 (7.4%) were overweight for their height. The median ingestion of energy, according to weight-for-height, was equal to 106.6%. Insufficient iron ingestion was observed in 63.0% and insufficient calcium in 55.6% of the patients. Constipation was verified in 74.1% of the patients and did not show a relationship with the quantity of fiber in the diet. CONCLUSION: Various nutritional problems, as well as, intestinal constipation were observed in these patients with Rett syndrome, and they must be considered in the multidisciplinary therapeutic planning of these individuals.<\/jats:p>","DOI":"10.1590\/s0004-28032008000400005","type":"journal-article","created":{"date-parts":[[2009,1,14]],"date-time":"2009-01-14T14:09:47Z","timestamp":1231942187000},"page":"284-289","source":"Crossref","is-referenced-by-count":30,"title":["Eating practices, nutritional status and constipation in patients with Rett syndrome"],"prefix":"10.1590","volume":"45","author":[{"given":"Flavia","family":"Schwartzman","sequence":"first","affiliation":[{"name":"Federal University of S\u00e3o Paulo, Brasil"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"M\u00e1rcia Regina","family":"V\u00edtolo","sequence":"additional","affiliation":[{"name":"Federal Faculty of Medical Sciences, Brasil"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jos\u00e9 Salom\u00e3o","family":"Schwartzman","sequence":"additional","affiliation":[{"name":"Mackenzie Presbyterian University, Brasil"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mauro Batista de","family":"Morais","sequence":"additional","affiliation":[{"name":"Federal University of S\u00e3o Paulo"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"530","reference":[{"key":"ref1","doi-asserted-by":"crossref","first-page":"613","DOI":"10.1177\/000992289303201011","article-title":"Rett syndrome: An update and review for the primary pediatrician","volume":"32","author":"Braddock SR","year":"1993","journal-title":"Clin Pediatr (Phila)","ISSN":"https:\/\/id.crossref.org\/issn\/0009-9228","issn-type":"print"},{"key":"ref2","doi-asserted-by":"crossref","first-page":"75","DOI":"10.1055\/s-2007-979727","article-title":"Management of Rett syndrome: a ten year 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