{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,15]],"date-time":"2026-09-15T22:56:28Z","timestamp":1789512988172,"version":"build-2803163510"},"reference-count":16,"publisher":"FapUNIFESP (SciELO)","issue":"2","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Arq. Neuro-Psiquiatr."],"published-print":{"date-parts":[[1996,6]]},"abstract":"<jats:p>Relata-se o caso cl\u00ednico de uma crian\u00e7a de 5 meses de idade, do sexo feminino, com achados caracter\u00edsticos da s\u00edndrome de Aicardi: agenesia do corpo caloso, espasmos infantis, anormalidades oculares (\"chorioretinal lacunae\" e microftalmia), atraso do desenvolvimento neuropsicomotor e malforma\u00e7\u00f5es vertebrais com cifoescoliose. Os exames complementares confirmaram o diagn\u00f3stico e as imagens neurorradiol\u00f3gicas evidenciaram, al\u00e9m da agenesia do corpo caloso, massa localizada em regi\u00e3o atrioventricular esquerda (papiloma do plexo cor\u00f3ide). A s\u00edndrome de Aicardi associada a papiloma do plexo cor\u00f3ide \u00e9 rara, sendo este o s\u00e9timo caso relatado na literatura. Os autores sugerem que o papiloma do plexo cor\u00f3ide seja considerado tumor caracter\u00edstico da s\u00edndrome de Aicardi, pois a sua freq\u00fc\u00eancia \u00e9 mais do que coincidental.<\/jats:p>","DOI":"10.1590\/s0004-282x1996000200022","type":"journal-article","created":{"date-parts":[[2010,12,16]],"date-time":"2010-12-16T02:33:40Z","timestamp":1292466820000},"page":"313-317","source":"Crossref","is-referenced-by-count":8,"title":["S\u00edndrome de Aicardi e papiloma do plexo cor\u00f3ide: uma associa\u00e7\u00e3o rara. 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