{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2022,3,31]],"date-time":"2022-03-31T17:36:23Z","timestamp":1648748183894},"reference-count":9,"publisher":"FapUNIFESP (SciELO)","issue":"3b","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Arq. Neuro-Psiquiatr."],"published-print":{"date-parts":[[2005,9]]},"abstract":"<jats:p>O hamartoma fibrolipomatoso \u00e9 neoplasia benigna rara que em alguns casos esta associada com macrodactilia. Descrevemos o caso de homem de 31 anos que apresentava desde o nascimento aumento de volume em regi\u00e3o de punho, segundo e terceiro quirod\u00e1ctilos da m\u00e3o esquerda. Aos 23 anos iniciou dor cont\u00ednua, de forte intensidade, predominante no per\u00edodo noturno e de evolu\u00e7\u00e3o progressiva em m\u00e3o esquerda. Associada \u00e0 dor havia hipoestesia e parestesias de predom\u00ednio nos segundo e terceiro quirod\u00e1ctilos esquerdos. A investiga\u00e7\u00e3o complementar com radiografia, ultrassonografia, estudo eletrofisiol\u00f3gico e resson\u00e2ncia magn\u00e9tica de m\u00e3o e punho esquerdos confirmaram a suspeita de s\u00edndrome do t\u00fanel do carpo secund\u00e1ria a macrodactilia com hamartoma fibrolipomatoso do nervo mediano. O paciente foi submetido \u00e0 descompress\u00e3o cir\u00fargica do t\u00fanel do carpo esquerdo devido a aus\u00eancia de resposta ao tratamento cl\u00ednico e evoluiu com melhora dos sintomas em avalia\u00e7\u00e3o ap\u00f3s tr\u00eas meses do procedimento.<\/jats:p>","DOI":"10.1590\/s0004-282x2005000500033","type":"journal-article","created":{"date-parts":[[2006,1,9]],"date-time":"2006-01-09T12:34:55Z","timestamp":1136810095000},"page":"881-884","source":"Crossref","is-referenced-by-count":0,"title":["Hamartoma fibrolipomatoso de nervo mediano: relato de caso"],"prefix":"10.1590","volume":"63","author":[{"given":"Paulo Jos\u00e9","family":"Lorenzoni","sequence":"first","affiliation":[{"name":"Universidade Federal do Paran\u00e1,  Brasil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Marcos Cristiano","family":"Lange","sequence":"additional","affiliation":[{"name":"Universidade Federal do Paran\u00e1,  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