{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2022,6,23]],"date-time":"2022-06-23T23:34:04Z","timestamp":1656027244578},"reference-count":13,"publisher":"FapUNIFESP (SciELO)","issue":"2","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J. bras. pneumol."],"published-print":{"date-parts":[[2007,4]]},"abstract":"<jats:p>A linfangiomatose, doen\u00e7a rara e de origem controversa, ocorre em indiv\u00edduos de todas as faixas et\u00e1rias, predominando entre os mais jovens, sem predile\u00e7\u00e3o por sexo. Comumente cursa com envolvimento tor\u00e1cico, por\u00e9m \u00f3rg\u00e3os como ossos, ba\u00e7o e f\u00edgado podem ser acometidos. Histologicamente, o envolvimento pulmonar cursa com prolifera\u00e7\u00e3o, anastomoses complexas e dilata\u00e7\u00e3o secund\u00e1ria do sistema linf\u00e1tico. Clinicamente, a apresenta\u00e7\u00e3o \u00e9 vari\u00e1vel. Os achados radiogr\u00e1ficos podem ser sugestivos e o diagn\u00f3stico \u00e9 definido pela histologia. Relatamos dois casos da doen\u00e7a; uma das pacientes era oligossintom\u00e1tica e encontra-se em tratamento; na outra, a doen\u00e7a foi mais agressiva e o diagn\u00f3stico muito tardio, culminando em \u00f3bito.<\/jats:p>","DOI":"10.1590\/s1806-37132007000200020","type":"journal-article","created":{"date-parts":[[2007,9,28]],"date-time":"2007-09-28T22:12:54Z","timestamp":1191017574000},"page":"229-233","source":"Crossref","is-referenced-by-count":4,"title":["Linfangiomatose pulmonar: relato de dois casos"],"prefix":"10.1590","volume":"33","author":[{"given":"Adma Silva de","family":"Lima","sequence":"first","affiliation":[{"name":"Universidade Federal do Paran\u00e1,  Brasil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mariane Gon\u00e7alves","family":"Martynychen","sequence":"additional","affiliation":[{"name":"Universidade Federal do Paran\u00e1,  Brasil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Roseni 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