{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,29]],"date-time":"2026-08-29T02:51:01Z","timestamp":1787971861683,"version":"build-2784847793"},"reference-count":18,"publisher":"FapUNIFESP (SciELO)","issue":"1","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J. bras. pneumol."],"abstract":"<jats:p>ABSTRACT Pleuroparenchymal fibroelastosis (PPFE) is a rare lung disease. It can be idiopathic or associated with any one of various conditions. To our knowledge, this is the first report of two cases of PPFE in Brazil. Our first patient presented with pleural and subpleural fibrosis in the upper lobes; a spiculated nodule in the left upper lobe; and a mild reticular pattern in the lower lobes. Surgical lung biopsy revealed PPFE in the upper lobes, including the nodule, and unclassified interstitial pneumonia in the left lower lobe. Our second patient had a history of exposure to domestic birds, indicating a risk of hypersensitivity pneumonitis, and presented with advanced lung disease, predominantly in the upper lobes, together with subpleural fibrosis.That patient underwent lung transplantation. In the explant specimen, PPFE and granulomas were identified, suggesting hypersensitivity pneumonitis as an associated cause.<\/jats:p>","DOI":"10.1590\/s1806-37562016000000045","type":"journal-article","created":{"date-parts":[[2017,1,21]],"date-time":"2017-01-21T21:29:09Z","timestamp":1485034149000},"page":"72-75","source":"Crossref","is-referenced-by-count":4,"title":["Pleuroparenchymal fibroelastosis: report of two cases in Brazil"],"prefix":"10.1590","volume":"43","author":[{"given":"Paula Silva","family":"Gomes","sequence":"first","affiliation":[{"name":"Universidade Federal de S\u00e3o Paulo,  Brazil"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Christina","family":"Shiang","sequence":"additional","affiliation":[{"name":"Hospital Israelita Albert Einstein,  Brazil"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Gilberto","family":"Szarf","sequence":"additional","affiliation":[{"name":"Universidade Federal de S\u00e3o Paulo,  Brazil"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ester Nei Aparecida Martins","family":"Coletta","sequence":"additional","affiliation":[{"name":"Universidade Federal de S\u00e3o Paulo,  Brazil; Instituto de Assist\u00eancia ao Servidor P\u00fablico Estadual de S\u00e3o Paulo,  Brasil"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Carlos Alberto de Castro","family":"Pereira","sequence":"additional","affiliation":[{"name":"Universidade Federal de S\u00e3o Paulo,  Brazil"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"530","published-online":{"date-parts":[[2017,1,23]]},"reference":[{"issue":"6","key":"ref1","doi-asserted-by":"crossref","first-page":"733","DOI":"10.1164\/rccm.201308-1483ST","article-title":"An official American Thoracic Society\/European Respiratory Society statement Update of the international multidisciplinary classification of the idiopathic interstitial pneumonias","volume":"188","author":"Travis WD","year":"2013","journal-title":"Am J Respir Crit Care Med"},{"issue":"10","key":"ref2","doi-asserted-by":"crossref","first-page":"509","DOI":"10.1016\/j.arbr.2015.07.001","article-title":"Pleuroparenchymal fibroelastosis is it also an idiopathic entity?","volume":"51","author":"Portillo K","year":"2015","journal-title":"Arch Bronconeumol"},{"issue":"3","key":"ref3","doi-asserted-by":"crossref","first-page":"316","DOI":"10.1136\/thx.30.3.316","article-title":"Idiopathic progressive pulmonary fibrosis","volume":"30","author":"Davies D","year":"1975","journal-title":"Thorax"},{"key":"ref4","first-page":"693","article-title":"Idiopathic pulmonary upper lobe fibrosis","volume":"11","author":"Amitani R","year":"1992","journal-title":"Kokyu"},{"key":"ref5","first-page":"S161","article-title":"Pathology of idiopathic pulmonary upper lobe fibrosis","volume":"62","author":"Kawabata Y","year":"2003","journal-title":"Nihon Kyobu Rinsho"},{"issue":"6","key":"ref6","doi-asserted-by":"crossref","first-page":"2007","DOI":"10.1378\/chest.126.6.2007","article-title":"Idiopathic pleuroparenchymal fibroelastosis Description of a novel clinicopathologic entity","volume":"126","author":"Frankel SK","year":"2004","journal-title":"Chest"},{"key":"ref7","first-page":"299","article-title":"Pleuroparenchymal fibroelastosis its clinical characteristics","volume":"9","author":"Watanabe K","year":"2013","journal-title":"Curr Respir Med Rev"},{"issue":"5","key":"ref8","doi-asserted-by":"crossref","first-page":"1248","DOI":"10.1378\/chest.13-2866","article-title":"Distinct characteristics of pleuroparenchymal fibroelastosis with usual interstitial pneumonia compared with idiopathic pulmonary fibrosis","volume":"146","author":"Oda T","year":"2014","journal-title":"Chest"},{"key":"ref9","first-page":"7","article-title":"Idiopathic pleuroparenchymatous fibroelastosis A case report and brief review of the literature","volume":"12","author":"Cuppens K","year":"2014","journal-title":"Respir Med Case Rep"},{"issue":"12","key":"ref10","doi-asserted-by":"crossref","first-page":"1633","DOI":"10.1038\/modpathol.2011.114","article-title":"Pleuroparenchymal fibroelastosis in patients with pulmonary disease secondary to bone marrow transplantation","volume":"24","author":"von der Th\u00fcsen JH","year":"2011","journal-title":"Mod Pathol"},{"issue":"2","key":"ref11","doi-asserted-by":"crossref","first-page":"523","DOI":"10.1183\/09031936.00214713","article-title":"Pleuroparenchymal fibroelastosis as a late complication of chemotherapy agents","volume":"44","author":"Beynat-Mouterde C","year":"2014","journal-title":"Eur Respir J"},{"issue":"4","key":"ref12","doi-asserted-by":"crossref","first-page":"1183","DOI":"10.1183\/09031936.00214714","article-title":"Pleuroparenchymal fibroelastosis from a consecutive database a rare disease entity?","volume":"45","author":"Nakatani T","year":"2015","journal-title":"Eur Respir J"},{"issue":"2","key":"ref13","doi-asserted-by":"crossref","first-page":"289","DOI":"10.1183\/09031936.00088414","article-title":"Pleuroparenchymal fibroelastosis one more walk on the wild side of drugs?","volume":"44","author":"Camus P","year":"2014","journal-title":"Eur Respir J"},{"issue":"1","key":"ref14","doi-asserted-by":"crossref","first-page":"65","DOI":"10.1097\/LBR.0b013e318207b396","article-title":"Pleuroparenchymal fibroelastosis presenting as a hypermetabolic lung nodule","volume":"18","author":"Machuca JS","year":"2011","journal-title":"J Bronchology Interv Pulmonol"},{"issue":"1","key":"ref15","doi-asserted-by":"crossref","first-page":"191","DOI":"10.1111\/resp.12654","article-title":"Pleuroparenchymal fibroelastosis in association with carcinomas","volume":"21","author":"Baroke E","year":"2016","journal-title":"Respirology"},{"issue":"2","key":"ref16","doi-asserted-by":"crossref","first-page":"377","DOI":"10.1183\/09031936.00165111","article-title":"Pleuroparenchymal fibroelastosis a spectrum of histopathological and imaging phenotypes","volume":"40","author":"Reddy TL","year":"2012","journal-title":"Eur Respir J"},{"issue":"1","key":"ref17","doi-asserted-by":"crossref","first-page":"243","DOI":"10.1183\/09031936.00103912","article-title":"Pleuroparenchymal fibroelastosis as a manifestation of chronic lung rejection","volume":"41","author":"Hirota T","year":"2013","journal-title":"Eur Respir J"},{"issue":"5","key":"ref18","doi-asserted-by":"crossref","first-page":"e115","DOI":"10.1016\/j.athoracsur.2014.07.045","article-title":"Lung transplantation for pleuroparenchymal fibroelastosis after chemotherapy","volume":"98","author":"Chen F","year":"2014","journal-title":"Ann Thorac Surg"}],"container-title":["Jornal Brasileiro de Pneumologia"],"original-title":[],"link":[{"URL":"http:\/\/www.scielo.br\/pdf\/jbpneu\/v43n1\/1806-3713-jbpneu-2016000000045.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2018,3,6]],"date-time":"2018-03-06T02:05:40Z","timestamp":1520301940000},"score":1,"resource":{"primary":{"URL":"http:\/\/www.scielo.br\/scielo.php?script=sci_arttext&pid=S1806-37132017000100072&lng=en&tlng=en"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017,1,23]]},"references-count":18,"journal-issue":{"issue":"1","published-online":{"date-parts":[[2017,2]]}},"alternative-id":["S1806-37132017000100072"],"URL":"https:\/\/doi.org\/10.1590\/s1806-37562016000000045","relation":{},"ISSN":["1806-3756","1806-3713"],"issn-type":[{"value":"1806-3756","type":"electronic"},{"value":"1806-3713","type":"print"}],"subject":[],"published":{"date-parts":[[2017,1,23]]}}}