{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,8]],"date-time":"2026-02-08T02:57:37Z","timestamp":1770519457424,"version":"3.49.0"},"reference-count":28,"publisher":"FapUNIFESP (SciELO)","issue":"4","license":[{"start":{"date-parts":[[2019,1,1]],"date-time":"2019-01-01T00:00:00Z","timestamp":1546300800000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"},{"start":{"date-parts":[[2019,1,1]],"date-time":"2019-01-01T00:00:00Z","timestamp":1546300800000},"content-version":"am","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"},{"start":{"date-parts":[[2019,1,1]],"date-time":"2019-01-01T00:00:00Z","timestamp":1546300800000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J. bras. pneumol."],"abstract":"<jats:p>ABSTRACT  Objective: To characterise the degree of disability in pulmonary hypertension (PH) patients based on the World Health Organisation Disability Assessment Schedule 2.0 (WHODAS 2.0).  Method: A prospective and observational study of patients with documented PH (N = 46). Patients completed the WHODAS 2.0 questionnaire during a scheduled routine clinical visit, and their demographic and clinical characteristics were retrieved from electronic medical records (EMR). In subsequent visits, selected clinical variables were registered to assess disease progression.  Results: WHODAS 2.0 scores were indicative of mild to moderate disability for the domains of mobility (22.0 \u00b1 23.2), life activities (23.7 \u00b1 25.5), and participation in society (17.2 \u00b1 15.9), as well as total WHODAS 2.0 score (15.3 \u00b1 15.2). For the domains of cognition (9.1 \u00b1 14.1), self-care (8.3 \u00b1 14.4), and interpersonal relationships (11.7 \u00b1 15.7), scores were lower. Disability scores were, generally, proportional to the PH severity. The main baseline correlates of disability were World Health Organisation (WHO) functional class, fatigue, dyspnoea, 6-minute walking distance (6MWD), and N-terminal pro b-type natriuretic peptide (NTproBNP). Baseline WHODAS 2.0 scores showed significant associations with disease progression. However, this effect was not transversal to all domains, with only a few domains significantly associated with disease progression variables.  Conclusions: This PH population shows mild disability, with higher degree of disability in the domains of mobility and life activities. This study is the first one to assess disability in PH using WHODAS 2.0. Further studies should apply this scale to larger PH populations with suitable representations of more severe PH forms.<\/jats:p>","DOI":"10.1590\/1806-3713\/e20170355","type":"journal-article","created":{"date-parts":[[2019,5,29]],"date-time":"2019-05-29T20:43:43Z","timestamp":1559162623000},"source":"Crossref","is-referenced-by-count":6,"title":["Disability and its clinical correlates in pulmonary hypertension measured through the World Health Organization Disability Assessment Schedule 2.0: a prospective, observational study"],"prefix":"10.1590","volume":"45","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-4976-3781","authenticated-orcid":false,"given":"Ab\u00edlio","family":"Reis","sequence":"first","affiliation":[{"name":"Hospital de Santo Ant\u00f3nio,  Portugal"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4509-0260","authenticated-orcid":false,"given":"M\u00e1rio","family":"Santos","sequence":"additional","affiliation":[{"name":"Hospital de Santo Ant\u00f3nio,  Portugal; Hospital de Santo Ant\u00f3nio,  Portugal; Faculty of Medicine of Porto,  Portugal"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3985-0718","authenticated-orcid":false,"given":"In\u00eas","family":"Furtado","sequence":"additional","affiliation":[{"name":"Hospital de Santo Ant\u00f3nio,  Portugal"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-5228-2984","authenticated-orcid":false,"given":"C\u00e9lia","family":"Cruz","sequence":"additional","affiliation":[{"name":"Hospital de Santo Ant\u00f3nio,  Portugal"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-5673-8683","authenticated-orcid":false,"given":"Pedro","family":"Sa-Couto","sequence":"additional","affiliation":[{"name":"University of Aveiro,  Portugal"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-3172-7400","authenticated-orcid":false,"given":"Alexandra","family":"Queir\u00f3s","sequence":"additional","affiliation":[{"name":"University of Aveiro,  Portugal; University of Aveiro,  Portugal"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4861-8649","authenticated-orcid":false,"given":"Lu\u00eds","family":"Almeida","sequence":"additional","affiliation":[{"name":"University of Porto,  Portugal"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3801-7249","authenticated-orcid":false,"given":"Nelson","family":"Rocha","sequence":"additional","affiliation":[{"name":"University of Aveiro,  Portugal; University of Aveiro,  Portugal"}]}],"member":"530","published-online":{"date-parts":[[2019]]},"reference":[{"issue":"1","key":"ref1","doi-asserted-by":"crossref","first-page":"67","DOI":"10.1093\/eurheartj\/ehv317","article-title":"2015 ESC\/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension The Joint Task Force for the Diagnosis and Treatment of Pulmonary Hypertension of the European Society of Cardiology (ESC) and the European Respiratory Society (ERS)Endorse","volume":"37","author":"Gali\u00e8 N","year":"2016","journal-title":"Eur Heart J"},{"key":"ref2","doi-asserted-by":"crossref","first-page":"S562","DOI":"10.21037\/jtd.2016.07.33","article-title":"Pulmonary hypertension: evolution of pulmonary arterial hypertension and chronic thromboembolic pulmonary hypertension","volume":"8","author":"Anderson RJ","year":"2016","journal-title":"J Thorac Dis"},{"key":"ref3","first-page":"S3","article-title":"The evolution of prostacyclins in pulmonary arterial hypertension: from classical treatment to modern management","volume":"22","author":"Burger CD","year":"2016","journal-title":"Am J Manag Care"},{"issue":"138","key":"ref4","doi-asserted-by":"crossref","first-page":"621","DOI":"10.1183\/16000617.0063-2015","article-title":"Pulmonary arterial hypertension the burden of disease and impact on quality of life","volume":"24","author":"Delcroix M","year":"2015","journal-title":"Eur Respir Rev"},{"issue":"8","key":"ref5","doi-asserted-by":"crossref","first-page":"751","DOI":"10.1007\/s40273-016-0395-y","article-title":"Systematic Review of Health-Related Quality of Life in Patients with Pulmonary Arterial Hypertension","volume":"34","author":"Gu S","year":"2016","journal-title":"Pharmacoeconomics"},{"key":"ref6","series-title":"Statement on Disability: Pulmonary Hypertension","author":"Oudiz RJ","year":"2010"},{"issue":"6","key":"ref7","doi-asserted-by":"crossref","first-page":"473","DOI":"10.1097\/00005650-199206000-00002","article-title":"The MOS 36-item short-form health survey (SF-36) I. 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