{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,4,2]],"date-time":"2026-04-02T22:19:23Z","timestamp":1775168363718,"version":"3.50.1"},"reference-count":10,"publisher":"FapUNIFESP (SciELO)","issue":"6 suppl 1","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["An. Bras. Dermatol."],"published-print":{"date-parts":[[2013,12]]},"abstract":"<jats:p>Blastic plasmacytoid dendritic cell neoplasm is a rare and aggressive hematodermic neoplasia with frequent cutaneous involvement and leukemic dissemination. We report the case of a 76-year-old man with a 2 month history of violaceous nodules and a tumor with stony consistency, located on the head, and mandibular, cervical and supraclavicular lymphadenopathies. Multiple thoracic and abdominal adenopathies were identified on computerized tomography. Flow cytometry analysis of the skin, lymph node and bone marrow biopsies demonstrated the presence of plasmocytoid dendritic cell neoplastic precursor cells (CD4+, CD45+, CD56+ and CD123+ phenotype). After initial clinical and laboratorial complete remission with chemotherapy, the patient died due to relapse of the disease associated with the appearance of a cervical mass with medullary compromise.<\/jats:p>","DOI":"10.1590\/abd1806-4841.20132388","type":"journal-article","created":{"date-parts":[[2014,1,30]],"date-time":"2014-01-30T19:47:00Z","timestamp":1391111220000},"page":"158-161","source":"Crossref","is-referenced-by-count":11,"title":["Blastic plasmacytoid dendritic cell neoplasm"],"prefix":"10.1590","volume":"88","author":[{"given":"Andr\u00e9","family":"Lencastre","sequence":"first","affiliation":[{"name":"Centro Hospitalar de Lisboa Central, EPE,  Portugal"}]},{"given":"Joana","family":"Cabete","sequence":"additional","affiliation":[{"name":"Hospital Center of Central Lisbon, EPE,  Portugal"}]},{"given":"Alexandre","family":"Jo\u00e3o","sequence":"additional","affiliation":[{"name":"Centro Hospitalar de Lisboa Central, EPE,  Portugal"}]},{"given":"Pedro","family":"Farinha","sequence":"additional","affiliation":[{"name":"Centro Hospitalar de Lisboa Central, EPE,  Portugal"}]},{"given":"Gilda","family":"Ferreira","sequence":"additional","affiliation":[{"name":"Centro Hospitalar de Lisboa Central, EPE,  Portugal"}]},{"given":"Sara","family":"Lestre","sequence":"additional","affiliation":[{"name":"Centro Hospitalar de Lisboa Central, EPE,  Portugal"}]}],"member":"530","reference":[{"key":"ref1","series-title":"WHO classification of Tumours of Haematopoietic and Lymphoid Tissues","first-page":"145","volume-title":"Blastic plasmacytoid dendritic cells neoplasm","author":"Facchetti F","year":"2008","edition":"4th ed"},{"key":"ref2","doi-asserted-by":"crossref","first-page":"278","DOI":"10.1002\/ajh.2830470406","article-title":"High expression of CD56 (N-CAM) in a patient with cutaneous CD4-positive lymphoma","volume":"47","author":"Adachi M","year":"1994","journal-title":"Am J Hematol"},{"key":"ref3","doi-asserted-by":"crossref","first-page":"662","DOI":"10.1309\/GJWNPD8HU5MAJ837","article-title":"Blastic NK-Cell Lymphomas (Agranular CD4+CD56+ Hematodermic Neoplasms)","volume":"123","author":"Petrella T","year":"2005","journal-title":"Am J Clin Pathol"},{"key":"ref4","first-page":"1","article-title":"Blastic plasmacytoid dendritic cell neoplasm","volume":"3","author":"Facchetti F","year":"2009","journal-title":"Haematol Meet Rep"},{"key":"ref5","first-page":"7","article-title":"Lymphoproliferative processes of the skin: part 2 - cutaneous T-cell and NK-cell lymphomas","volume":"81","author":"Sanches J","year":"2006","journal-title":"An Bras Dermatol"},{"key":"ref6","doi-asserted-by":"crossref","first-page":"1556","DOI":"10.1182\/blood.V99.5.1556","article-title":"Clinical and biological features of CD4+ CD56+ malignancies","volume":"99","author":"Feuillard J","year":"2002","journal-title":"Blood"},{"key":"ref7","doi-asserted-by":"crossref","first-page":"852","DOI":"10.1097\/00000478-200207000-00003","article-title":"Agranular CD4+ CD56+ hematodermic neoplasm (blastic NK-cell lymphoma) originates from a population of CD56+ precursor cells related to plasmocytoid monocytes","volume":"26","author":"Petrella T","year":"2002","journal-title":"Am J Surg Pathol"},{"key":"ref8","doi-asserted-by":"crossref","first-page":"481","DOI":"10.1097\/01.pai.0000213139.39654.40","article-title":"CD4+\/CD56+ hematodermic neoplasm: presentation of 2 cases and review of the concept of an uncommon tumor originated in plasmacytoid dendritic cells expressing CD123 (IL-3 receptor alpha)","volume":"15","author":"Pi\u00f1a-Oviedo S","year":"2007","journal-title":"Appl Immunohistochem Mol Morphol"},{"key":"ref9","doi-asserted-by":"crossref","first-page":"137","DOI":"10.1097\/00000478-199902000-00001","article-title":"CD4+ CD56+ cutaneous neoplasms: a distinct hematological entity? Groupe Fran\u00e7ais d'Etude des Lymphomes Cutan\u00e9s (GFELC)","volume":"23","author":"Petrella T","year":"1999","journal-title":"Am J Surg Pathol"},{"key":"ref10","article-title":"The CD4+ CD56+ CD116- CD123+ CD45RA+ CD45RO- profile is specific of DC2 malignancies","volume":"88","author":"Trimoreau F","year":"2003","journal-title":"Haematologica"}],"container-title":["Anais Brasileiros de Dermatologia"],"original-title":[],"link":[{"URL":"http:\/\/www.scielo.br\/pdf\/abd\/v88n6s1\/0365-0596-abd-88-06-s1-0158.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,5,19]],"date-time":"2025-05-19T15:00:41Z","timestamp":1747666841000},"score":1,"resource":{"primary":{"URL":"http:\/\/www.scielo.br\/scielo.php?script=sci_arttext&pid=S0365-05962013000800158&lng=en&tlng=en"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2013,12]]},"references-count":10,"journal-issue":{"issue":"6 suppl 1","published-print":{"date-parts":[[2013,12]]}},"alternative-id":["S0365-05962013000800158"],"URL":"https:\/\/doi.org\/10.1590\/abd1806-4841.20132388","relation":{},"ISSN":["0365-0596"],"issn-type":[{"value":"0365-0596","type":"electronic"}],"subject":[],"published":{"date-parts":[[2013,12]]}}}