{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2022,4,5]],"date-time":"2022-04-05T18:51:47Z","timestamp":1649184707361},"reference-count":31,"publisher":"FapUNIFESP (SciELO)","issue":"2","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Acta Cir. Bras."],"published-print":{"date-parts":[[2002,4]]},"abstract":"<jats:p>O carcinoma secretor (CS) da mama \u00e9 uma neoplasia muito rara. O CS da mama foi inicialmente descrito em crian\u00e7as e adolescentes, mas a maioria dos casos \u00e9 descrito em doentes adultos. \u00c9 muitas vezes associado a um progn\u00f3stico particularmente favor\u00e1vel, mas em doentes adultos com tumores de maiores dimens\u00f5es pode apresentar um comportamento mais agressivo. Apresenta-se um caso de uma doente com 62 anos de idade, que apresentava uma volumosa tumefac\u00e7\u00e3o da mama com 16 anos de evolu\u00e7\u00e3o. O exame objetivo revelou extensa fixa\u00e7\u00e3o da les\u00e3o \u00e0 pele, com sinais inflamat\u00f3rios acentuados e \u00e1reas de necrose cut\u00e2nea. O tratamento inicial consistiu numa mastectomia simples, com inten\u00e7\u00e3o paliativa. O diagn\u00f3stico anatomopatol\u00f3gico de carcinoma secretor (3,5 cm), sem invas\u00e3o cut\u00e2nea, motivou a posterior realiza\u00e7\u00e3o de esvaziamento ganglionar axilar, que revelou met\u00e1stases em 2 dos 13 g\u00e2nglios isolados. A doente faleceu 24 meses depois, por dissemina\u00e7\u00e3o da doen\u00e7a, comprovando a maior agressividade do CS em doentes adultos com tumores de maiores dimens\u00f5es (T2) e com metastiza\u00e7\u00e3o ganglionar (N1). Os autores rev\u00eaem a literatura com particular \u00eanfase nos factores de progn\u00f3stico importantes para decis\u00e3o terap\u00eautica deste tipo raro de carcinoma da mama, em doentes adultos.<\/jats:p>","DOI":"10.1590\/s0102-86502002000200009","type":"journal-article","created":{"date-parts":[[2005,4,28]],"date-time":"2005-04-28T17:02:36Z","timestamp":1114707756000},"page":"135-142","source":"Crossref","is-referenced-by-count":0,"title":["Carcinoma secretor da mama no adulto: existem par\u00e2metros bem definidos para decis\u00e3o terap\u00eautica?"],"prefix":"10.1590","volume":"17","author":[{"given":"Ant\u00f3nio Manuel Ferreira","family":"Gouveia","sequence":"first","affiliation":[{"name":"Hospital de S\u00e3o Jo\u00e3o"}]},{"given":"Jos\u00e9 Manuel","family":"Lopes","sequence":"additional","affiliation":[{"name":"Faculdade de Medicina do Porto; Universidade do Porto"}]},{"given":"Amadeu P. Ara\u00fajo","family":"Pimenta","sequence":"additional","affiliation":[{"name":"Faculdade de Medicina do Porto; Universidade do Porto"}]}],"member":"530","reference":[{"key":"ref1","series-title":"Diagnostic histopathology of the breast","first-page":"236","volume-title":"Uncommon types of invasive carcinoma","author":"Page DL","year":"1987"},{"key":"ref2","doi-asserted-by":"crossref","first-page":"388","DOI":"10.1001\/jama.1966.03100050096033","article-title":"Breast carcinoma in children","volume":"195","author":"Mc Divitt RW","year":"1966","journal-title":"JAMA","ISSN":"http:\/\/id.crossref.org\/issn\/0098-7484","issn-type":"print"},{"key":"ref3","doi-asserted-by":"crossref","first-page":"2404","DOI":"10.1002\/1097-0142(19800501)45:9<2404::AID-CNCR2820450928>3.0.CO;2-8","article-title":"Secretory carcinoma of the breast","volume":"45","author":"Tavassoli 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