{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,10]],"date-time":"2026-07-10T05:29:04Z","timestamp":1783661344688,"version":"3.55.0"},"reference-count":10,"publisher":"Wiley","issue":"3","license":[{"start":{"date-parts":[[2010,9,1]],"date-time":"2010-09-01T00:00:00Z","timestamp":1283299200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Epileptic Disorders"],"published-print":{"date-parts":[[2010,9]]},"abstract":"<jats:title>ABSTRACT<\/jats:title>\n                  <jats:p>\n                    Creutzfeldt\u2010Jakob disease (CJD) is a rare human transmissible spongiform subacute encephalopathy. The most common clinical manifestations of CJD include rapidly progressive dementia, behavioural changes, cerebellar dysfunction and myoclonus. Other seizure types are rare and nonconvulsive status epilepticus (SE) is exceptional. We report a case of a 44\u2010year\u2010old man who presented a psychotic episode followed by akinetic mutism and refractory nonconvulsive SE. The final diagnosis was CJD. Continuous video\u2010EEG monitoring revealed the ictal pattern of nonconvulsive SE to be periodic sharp wave complexes characteristic of CJD.\n                    <jats:italic>[Published with video sequences]<\/jats:italic>\n                  <\/jats:p>","DOI":"10.1684\/epd.2010.0318","type":"journal-article","created":{"date-parts":[[2019,8,2]],"date-time":"2019-08-02T09:24:19Z","timestamp":1564737859000},"page":"239-242","source":"Crossref","is-referenced-by-count":15,"title":["Refractory nonconvulsive status epilepticus in Creutzfeldt\u2010Jakob disease"],"prefix":"10.1002","volume":"12","author":[{"given":"Maria","family":"Aiguabella","sequence":"first","affiliation":[{"name":"Neurology Department Hospital de Bellvitge Hospitalet de Llobregat Barcelona Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Merc\u00e8","family":"Falip","sequence":"additional","affiliation":[{"name":"Neurology Department Hospital de Bellvitge Hospitalet de Llobregat Barcelona Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Misericordia","family":"Veciana","sequence":"additional","affiliation":[{"name":"Neurology Department Hospital de Bellvitge Hospitalet de Llobregat Barcelona Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jordi","family":"Bruna","sequence":"additional","affiliation":[{"name":"Neurology Department Hospital de Bellvitge Hospitalet de Llobregat Barcelona Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Antoni","family":"Palas\u00ed","sequence":"additional","affiliation":[{"name":"Neurology Department Hospital de Bellvitge Hospitalet de Llobregat Barcelona Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Luisa","family":"Corral","sequence":"additional","affiliation":[{"name":"Intensive Care Unit Hospital de Bellvitge Hospitalet de Llobregat Barcelona 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Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2010,9]]},"reference":[{"key":"e_1_2_5_2_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.yebeh.2004.06.019"},{"key":"e_1_2_5_3_1","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.37.8.879"},{"key":"e_1_2_5_4_1","doi-asserted-by":"publisher","DOI":"10.1157\/13043320"},{"key":"e_1_2_5_5_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.clinph.2003.10.012"},{"key":"e_1_2_5_6_1","doi-asserted-by":"publisher","DOI":"10.1056\/NEJM199812313392707"},{"key":"e_1_2_5_7_1","doi-asserted-by":"publisher","DOI":"10.1016\/S1059-1311(02)00378-3"},{"key":"e_1_2_5_8_1","doi-asserted-by":"publisher","DOI":"10.1054\/jocn.2000.0845"},{"key":"e_1_2_5_9_1","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.66.3.406"},{"key":"e_1_2_5_10_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.clinph.2007.08.002"},{"key":"e_1_2_5_11_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.clinph.2005.12.007"}],"container-title":["Epileptic Disorders"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1684\/epd.2010.0318","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,3,18]],"date-time":"2024-03-18T12:09:16Z","timestamp":1710763756000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1684\/epd.2010.0318"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2010,9]]},"references-count":10,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2010,9]]}},"alternative-id":["10.1684\/epd.2010.0318"],"URL":"https:\/\/doi.org\/10.1684\/epd.2010.0318","archive":["Portico"],"relation":{"is-cited-by":[{"id-type":"doi","id":"10.1155\/2013\/630141","asserted-by":"object"}]},"ISSN":["1294-9361","1950-6945"],"issn-type":[{"value":"1294-9361","type":"print"},{"value":"1950-6945","type":"electronic"}],"subject":[],"published":{"date-parts":[[2010,9]]}}}