{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,12]],"date-time":"2026-09-12T03:52:40Z","timestamp":1789185160714,"version":"build-2803163510"},"reference-count":15,"publisher":"Wiley","issue":"3","license":[{"start":{"date-parts":[[2015,10,1]],"date-time":"2015-10-01T00:00:00Z","timestamp":1443657600000},"content-version":"vor","delay-in-days":30,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Epileptic Disorders"],"published-print":{"date-parts":[[2015,9]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Sturge\u2010Weber syndrome is a sporadic congenital neurocutaneous disorder often related to varying degrees of motor impairment. The phenomenon of prolonged ictal paresis is a rare seizure sign that can be due to lesions affecting the centro\u2010parietal lobe. Focal inhibitory motor seizures can be difficult to differentiate from other clinical entities such as stroke, migraine or postictal paresis. We describe the case of a 40\u2010year\u2010old patient suffering from Sturge\u2010Weber syndrome, admitted due to prolonged right\u2010sided hemiparesis following a usual seizure. Repeated EEGs during the prolonged deficit showed only intermittent left fronto\u2010parietal sharp waves. <jats:sup>99m<\/jats:sup>Tc HMPAO\u2010brain SPECT performed seven days after the last seizure showed a vast area of parieto\u2010occipital hyperperfusion in the left hemisphere. Aggressive antiepileptic therapy dramatically improved the clinical symptoms and scintigraphic images, which corroborated the diagnosis of ictal paresis. This case highlights the role of SPECT in the evaluation of Sturge\u2010Weber syndrome, not only to investigate progressive neurological deterioration, but also exacerbation of seizures or prolonged neurological deficits. In fact, it may be possible to document ongoing epileptic activity using SPECT, despite a non\u2010contributory EEG, which may be of help in adapting a therapeutic strategy.<\/jats:p>","DOI":"10.1684\/epd.2015.0755","type":"journal-article","created":{"date-parts":[[2019,8,2]],"date-time":"2019-08-02T13:24:19Z","timestamp":1564752259000},"page":"328-331","source":"Crossref","is-referenced-by-count":6,"title":["Focal inhibitory seizure with prolonged deficit in adult Sturge\u2010Weber syndrome"],"prefix":"10.1002","volume":"17","author":[{"given":"Jerome","family":"Aupy","sequence":"first","affiliation":[{"name":"Centre Hospitalier Universitaire de Bordeaux, P\u00f4le de Neurosciences Cliniques"},{"name":"Institut des Maladies Neurod\u00e9g\u00e9n\u00e9ratives, CNRS UMR 5293"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Charlotte","family":"Bonnet","sequence":"additional","affiliation":[{"name":"Centre Hospitalier Universitaire de Bordeaux, P\u00f4le de Neurosciences Cliniques"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jean\u2010Simon","family":"Arnould","sequence":"additional","affiliation":[{"name":"Centre Hospitalier Universitaire de Bordeaux, Service de M\u00e9decine Nucl\u00e9aire"},{"name":"Universit\u00e9 de Bordeaux, INCIA, CNRS UMR 5287 Bordeaux France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Philippe","family":"Fernandez","sequence":"additional","affiliation":[{"name":"Centre Hospitalier Universitaire de Bordeaux, Service de M\u00e9decine Nucl\u00e9aire"},{"name":"Universit\u00e9 de Bordeaux, INCIA, CNRS UMR 5287 Bordeaux France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Cecile","family":"Marchal","sequence":"additional","affiliation":[{"name":"Centre Hospitalier Universitaire de Bordeaux, P\u00f4le de Neurosciences Cliniques"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Paolo","family":"Zanotti\u2010Fregonara","sequence":"additional","affiliation":[{"name":"Centre Hospitalier Universitaire de Bordeaux, Service de M\u00e9decine Nucl\u00e9aire"},{"name":"Universit\u00e9 de Bordeaux, INCIA, CNRS UMR 5287 Bordeaux France"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2015,10]]},"reference":[{"key":"e_1_2_5_2_1","doi-asserted-by":"publisher","DOI":"10.1385\/NCC:2:1:029"},{"key":"e_1_2_5_3_1","first-page":"185","article-title":"Somatomotor seizures of frontal lobe origin","volume":"57","author":"Chauvel P.","year":"1992","journal-title":"Adv Neurol"},{"key":"e_1_2_5_4_1","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.52.12.1402"},{"key":"e_1_2_5_5_1","doi-asserted-by":"publisher","DOI":"10.1017\/S0317167100024331"},{"key":"e_1_2_5_6_1","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/123.8.1710"},{"key":"e_1_2_5_7_1","doi-asserted-by":"publisher","DOI":"10.1097\/RLU.0b013e31826c0cf1"},{"key":"e_1_2_5_8_1","first-page":"115","article-title":"Cortical electrical stimulation in humans. 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