{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,5,12]],"date-time":"2025-05-12T06:40:07Z","timestamp":1747032007474,"version":"3.40.5"},"reference-count":30,"publisher":"Media Sphere Publishing House","issue":"4","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["S.S. Korsakov J. Neuro. Psych."],"published-print":{"date-parts":[[2025,5,12]]},"abstract":"<jats:p>Beh\u00e7et\u2019s disease (BD) is an autoimmune vasculitis of unclear etiology characterized by a wide range of systemic manifestations. The nervous system is involved in approximately 10% of patients with BD (neuro-Beh\u00e7et). Diagnosis of neuro-Beh\u00e7et is challenging, especially in the case of BD onset with neurological manifestations, and is based on a combination of clinical, laboratory, and neuroimaging data. To verify the diagnosis of neuro-Beh\u00e7et, a wide range of conditions with similar manifestations must be ruled out: multiple sclerosis, neuromyelitis optica spectrum disorder, neurosarcoidosis, and many rare autoimmune diseases (e.g., Cogan syndrome, Susac syndrome, Vogt-Koyanagi-Harada syndrome). This article presents a brief literature review highlighting the challenges of neuro-Beh\u00e7et differential diagnosis and a clinical case of a 34-year-old male patient with a criteria-based diagnosis of BD with neurological manifestations.<\/jats:p>","DOI":"10.17116\/jnevro2025125041108","type":"journal-article","created":{"date-parts":[[2025,5,12]],"date-time":"2025-05-12T05:58:15Z","timestamp":1747029495000},"page":"108","source":"Crossref","is-referenced-by-count":0,"title":["Challenges of differential diagnosis in the verification of Beh\u00e7et\u2019s disease with neurological manifestations"],"prefix":"10.17116","volume":"125","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-3727-8017","authenticated-orcid":false,"given":"A.I.","family":"Vlasenko","sequence":"first","affiliation":[{"name":"Almazov National Medical Research Center","place":["St. Petersburg, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-0175-3085","authenticated-orcid":false,"given":"M.P.","family":"Topuzova","sequence":"additional","affiliation":[{"name":"Almazov National Medical Research Center","place":["St. Petersburg, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-2230-3750","authenticated-orcid":false,"given":"V.A.","family":"Malko","sequence":"additional","affiliation":[{"name":"Almazov National Medical Research Center","place":["St. Petersburg, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-1848-8775","authenticated-orcid":false,"given":"G.N.","family":"Bisaga","sequence":"additional","affiliation":[{"name":"Almazov National Medical Research Center","place":["St. Petersburg, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-7180-1898","authenticated-orcid":false,"given":"T.A.","family":"Pavlova","sequence":"additional","affiliation":[{"name":"Almazov National Medical Research Center","place":["St. Petersburg, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0009-0009-1260-4171","authenticated-orcid":false,"given":"A.P.","family":"Abramova","sequence":"additional","affiliation":[{"name":"Almazov National Medical Research Center","place":["St. Petersburg, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-6258-1793","authenticated-orcid":false,"given":"A.O.","family":"Chistyakova","sequence":"additional","affiliation":[{"name":"Almazov National Medical Research Center","place":["St. Petersburg, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4441-1165","authenticated-orcid":false,"given":"T.M.","family":"Alekseeva","sequence":"additional","affiliation":[{"name":"Almazov National Medical Research Center","place":["St. Petersburg, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"6743","reference":[{"key":"key-10.17116\/jnevro2025125041108-1","doi-asserted-by":"publisher","DOI":"10.1016\/j.radcr.2022.05.070"},{"key":"key-10.17116\/jnevro2025125041108-2","doi-asserted-by":"publisher","DOI":"10.1016\/S1474-4422(09)70015-8"},{"key":"key-10.17116\/jnevro2025125041108-3","doi-asserted-by":"publisher","DOI":"10.1016\/j.msard.2019.101906"},{"key":"key-10.17116\/jnevro2025125041108-4","doi-asserted-by":"publisher","DOI":"10.4103\/0028-3886.246252"},{"key":"key-10.17116\/jnevro2025125041108-5","unstructured":"Akman-Demir G, Mutlu M, Kiyat-Atamer A, et al. 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