{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,14]],"date-time":"2026-05-14T02:12:03Z","timestamp":1778724723667,"version":"3.51.4"},"reference-count":20,"publisher":"Media Sphere Publishing House","issue":"4","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Burdenko's Journal of Neurosurgery"],"published-print":{"date-parts":[[2024,4,23]]},"abstract":"<jats:p>Dysembryoplastic neuroepithelial tumor (DNET) is a benign mixed neuronal-glial neoplasm (WHO grade 1). DNET is most often localized in temporal lobes and found in children and young people with epilepsy. There a few cases of DNET in ventricular system with dissemination along the ependyma in the world literature. Material and methods. We present a rare case of T1- and T2-negative ventricular system tumor. Only FIESTA imaging revealed dissemination with multiple focal lesions of the third ventricle, its bottom and lateral walls, anterior horns of lateral ventricles, cerebellar vermis, cervical and lumbar spinal cord. Results. The patient underwent transcortical endoscopic biopsy of the third ventricle tumor with simultaneous ventriculoperitoneal shunting. DNET was diagnosed, and radiotherapy was subsequently performed. Literature data on this issue were analyzed. Conclusion. To date, disseminated forms of DNET are extremely rare. X-ray features and morphological results allow us to establish the correct diagnosis and determine further treatment strategy.<\/jats:p>","DOI":"10.17116\/neiro20248804192","type":"journal-article","created":{"date-parts":[[2024,8,22]],"date-time":"2024-08-22T05:10:01Z","timestamp":1724303401000},"page":"92","source":"Crossref","is-referenced-by-count":1,"title":["Disseminated ependymal dysembryoplastic neuroepithelial tumor: a case report and literature review"],"prefix":"10.17116","volume":"88","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-7136-0693","authenticated-orcid":false,"given":"Yu.V.","family":"Kushel","sequence":"first","affiliation":[{"name":"Burdenko Neurosurgical Center","place":["Moscow, Russia"]},{"name":"Central Clinical Hospital with Polyclinic of the Presidential Administration","place":["Moscow, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-6520-4296","authenticated-orcid":false,"given":"M.A.","family":"Kutin","sequence":"additional","affiliation":[{"name":"Burdenko Neurosurgical Center","place":["Moscow, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3827-8676","authenticated-orcid":false,"given":"V.V.","family":"Ivanov","sequence":"additional","affiliation":[{"name":"Burdenko Neurosurgical Center","place":["Moscow, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-9789-3452","authenticated-orcid":false,"given":"I.V.","family":"Chernov","sequence":"additional","affiliation":[{"name":"Burdenko Neurosurgical Center","place":["Moscow, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0009-0003-1915-8107","authenticated-orcid":false,"given":"D.Sh.","family":"Adueva","sequence":"additional","affiliation":[{"name":"Burdenko Neurosurgical Center","place":["Moscow, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4480-0275","authenticated-orcid":false,"given":"I.N.","family":"Pronin","sequence":"additional","affiliation":[{"name":"Burdenko Neurosurgical Center","place":["Moscow, Russia"]},{"name":"Russian Medical Academy of Continuing Professional Education","place":["Moscow, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"L.V.","family":"Shishkina","sequence":"additional","affiliation":[{"name":"Burdenko Neurosurgical Center","place":["Moscow, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-3523-9885","authenticated-orcid":false,"given":"E.S.","family":"Konovalova","sequence":"additional","affiliation":[{"name":"Burdenko Neurosurgical Center","place":["Moscow, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-9333-9473","authenticated-orcid":false,"given":"P.L.","family":"Kalinin","sequence":"additional","affiliation":[{"name":"Burdenko Neurosurgical Center","place":["Moscow, Russia"]}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"6743","reference":[{"key":"key-10.17116\/neiro20248804192-1","doi-asserted-by":"publisher","DOI":"10.1093\/neuonc\/noab106"},{"key":"key-10.17116\/neiro20248804192-2","doi-asserted-by":"publisher","DOI":"10.1007\/s00401-007-0243-4"},{"key":"key-10.17116\/neiro20248804192-3","doi-asserted-by":"publisher","DOI":"10.1227\/00006123-198811000-00002"},{"key":"key-10.17116\/neiro20248804192-4","doi-asserted-by":"publisher","DOI":"10.1016\/j.wneu.2017.04.093"},{"key":"key-10.17116\/neiro20248804192-5","doi-asserted-by":"publisher","DOI":"10.1093\/ajcp\/97.3.398"},{"key":"key-10.17116\/neiro20248804192-6","doi-asserted-by":"publisher","DOI":"10.3348\/kjr.2012.13.4.492"},{"key":"key-10.17116\/neiro20248804192-7","doi-asserted-by":"publisher","DOI":"10.1111\/j.1750-3639.2010.00386.x"},{"key":"key-10.17116\/neiro20248804192-8","doi-asserted-by":"publisher","DOI":"10.1007\/s00234-013-1135-z"},{"key":"key-10.17116\/neiro20248804192-9","doi-asserted-by":"publisher","DOI":"10.1007\/s00234-009-0511-1"},{"key":"key-10.17116\/neiro20248804192-10","doi-asserted-by":"publisher","DOI":"10.1097\/01.rct.0000243453.33610.9d"},{"key":"key-10.17116\/neiro20248804192-11","doi-asserted-by":"publisher","DOI":"10.1227\/01.NEU.0000255530.46092.AA"},{"key":"key-10.17116\/neiro20248804192-12","unstructured":"Bilginer B, S\u00f6ylemezo\u011flu F, Cila A, Akalan N. 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