{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,20]],"date-time":"2025-10-20T00:20:55Z","timestamp":1760919655260,"version":"build-2065373602"},"reference-count":28,"publisher":"Wiley","issue":"3","license":[{"start":{"date-parts":[[2008,3,1]],"date-time":"2008-03-01T00:00:00Z","timestamp":1204329600000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Journal of Periodontology"],"published-print":{"date-parts":[[2008,3]]},"abstract":"<jats:p><jats:bold>Background:<\/jats:bold> Sturge\u2010Weber syndrome (encephalotrigeminal angiomatosis) is a rather uncommon congenital condition that is characterized by a combination of venous angioma of leptomeninges over the cerebral cortex and ipsilateral angiomatous lesions of the face and sometimes of the skull, jaws, and oral soft tissues. It is commonly referred to as Sturge\u2010Weber syndrome after Sturge and Weber who first described this affliction in 1879. This article presents a case of Sturge\u2010Weber syndrome associated with severe gingival enlargement, its management, and follow\u2010up results.<\/jats:p><jats:p><jats:bold>Methods:<\/jats:bold> A 15\u2010year\u2010old male patient was referred to the Department of Periodontics, Government Dental College and Hospital, for severe gingival enlargement. A detailed dental and medical history, clinical examination, and investigations confirmed the diagnosis of Sturge\u2010Weber syndrome. This report reveals a classic presentation of the syndrome with emphasis on its oral manifestations. Periodontal management included thorough scaling and root planing followed by periodontal flap surgery to treat the gingival enlargement. Histopathologic examination of the excisional biopsy specimen revealed features suggestive of fibrous gingival enlargement.<\/jats:p><jats:p><jats:bold>Results:<\/jats:bold> Reevaluation of the patient after 2 years showed remarkable (90%) reduction of the gingival enlargement in the maxillary arch and complete diminution (100%) in the mandibular arch. However, a slight recurrence was noted in the maxillary right quadrant.<\/jats:p><jats:p><jats:bold>Conclusions:<\/jats:bold> Sturge\u2010Weber syndrome is clinically important to the periodontist because of its associated gingival vascular features and their complicating manifestations. Periodic systemic and oral examinations are recommended to identify and prevent any complications from the cranial and oral lesions.<\/jats:p>","DOI":"10.1902\/jop.2008.060478","type":"journal-article","created":{"date-parts":[[2008,3,3]],"date-time":"2008-03-03T09:21:35Z","timestamp":1204536095000},"page":"549-555","source":"Crossref","is-referenced-by-count":21,"title":["Periodontal Management of Gingival Enlargement Associated With Sturge\u2010Weber Syndrome"],"prefix":"10.1002","volume":"79","author":[{"given":"Rahul S.","family":"Bhansali","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ramreddy K.","family":"Yeltiwar","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Amit A.","family":"Agrawal","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2008,3]]},"reference":[{"key":"e_1_2_6_2_1","first-page":"157","volume-title":"Textbook of Oral Pathology","author":"Shafer WG","year":"1983"},{"key":"e_1_2_6_3_1","doi-asserted-by":"publisher","DOI":"10.1902\/jop.1969.40.4.243"},{"key":"e_1_2_6_4_1","first-page":"223","volume-title":"Handbook of Clinical Neurology, Vol. 14.","author":"Alexander GL","year":"1972"},{"key":"e_1_2_6_5_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0031-3955(16)38367-5"},{"key":"e_1_2_6_6_1","doi-asserted-by":"publisher","DOI":"10.1001\/jama.1958.02990350007002"},{"key":"e_1_2_6_7_1","doi-asserted-by":"publisher","DOI":"10.1001\/jama.1906.25210030020002e"},{"key":"e_1_2_6_8_1","first-page":"419","article-title":"Ophthalmic aspects of Sturge Weber syndrome","volume":"56","author":"Millar SJN","year":"1965","journal-title":"Proc R Soc Med"},{"key":"e_1_2_6_9_1","doi-asserted-by":"publisher","DOI":"10.1016\/0030-4220(61)90272-9"},{"key":"e_1_2_6_10_1","doi-asserted-by":"publisher","DOI":"10.1016\/0030-4220(60)90006-2"},{"key":"e_1_2_6_11_1","doi-asserted-by":"publisher","DOI":"10.1016\/0030-4220(57)90165-2"},{"key":"e_1_2_6_12_1","doi-asserted-by":"publisher","DOI":"10.1016\/0030-4220(52)90216-8"},{"key":"e_1_2_6_13_1","first-page":"96","article-title":"Sturge\u2010Weber disease","volume":"25","author":"Brushfield T","year":"1928","journal-title":"Br J Child Dis"},{"key":"e_1_2_6_14_1","first-page":"406","volume-title":"Syndromes of Head and Neck","author":"Gorlin RJ","year":"1990"},{"key":"e_1_2_6_15_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.1320190204"},{"key":"e_1_2_6_16_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-3476(76)80397-6"},{"key":"e_1_2_6_17_1","doi-asserted-by":"publisher","DOI":"10.1001\/archderm.1973.01620240063019"},{"key":"e_1_2_6_18_1","doi-asserted-by":"publisher","DOI":"10.1097\/00005072-195707000-00006"},{"key":"e_1_2_6_19_1","first-page":"355","article-title":"Review and hypotheses: Somatic mosaicism: Observations related to clinical genetics","volume":"43","author":"Hall JG","year":"1988","journal-title":"Am J Hum Genet"},{"key":"e_1_2_6_20_1","doi-asserted-by":"publisher","DOI":"10.1001\/archpedi.1972.02110110135019"},{"key":"e_1_2_6_21_1","doi-asserted-by":"publisher","DOI":"10.3109\/00016925109136671"},{"key":"e_1_2_6_22_1","doi-asserted-by":"publisher","DOI":"10.2176\/nmc.29.60"},{"key":"e_1_2_6_23_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-051X.1996.tb02072.x"},{"key":"e_1_2_6_24_1","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.73.8.2909"},{"key":"e_1_2_6_25_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-0714.1982.tb00171.x"},{"key":"e_1_2_6_26_1","doi-asserted-by":"publisher","DOI":"10.1902\/jop.1999.70.12.1464"},{"key":"e_1_2_6_27_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0278-2391(86)80077-5"},{"key":"e_1_2_6_28_1","first-page":"140","article-title":"Sturge\u2010Weber syndrome with intraoral manifestations. 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