{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2023,12,11]],"date-time":"2023-12-11T13:24:29Z","timestamp":1702301069032},"reference-count":0,"publisher":"Ordem dos Medicos","issue":"5","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Acta Med Port"],"abstract":"<jats:p>A calcifica\u00e7\u00e3o dos n\u00facleos da base, ou s\u00edndrome de Fahr, pode ser secund\u00e1ria a variadas doen\u00e7as, nomeadamente as que cursam\u00a0com envolvimento da paratir\u00f3ide. Dist\u00farbios do movimento s\u00e3o achados cl\u00ednicos comuns, mas a coreia \u00e9 observada em menos de\u00a020% dos casos e a distonia apenas em 8%. Apresentamos o caso de um homem de 49 anos com antecedentes de tiroidectomia,\u00a0admitido no servi\u00e7o de urg\u00eancia com coreia aguda generalizada e distonia focal dolorosa dos p\u00e9s, cujo estudo laboratorial revelava\u00a0hipocalc\u00e9mia e rabdomi\u00f3lise e a tomografia computorizada cr\u00e2nio-encef\u00e1lica mostrava calcifica\u00e7\u00f5es parenquimatosas extensas com\u00a0envolvimento dos n\u00facleos da base. A alargada investiga\u00e7\u00e3o complementar permitiu fazer o diagn\u00f3stico de s\u00edndrome de Fahr secund\u00e1ria a hipoparatiroidismo iatrog\u00e9nico. Ap\u00f3s estabiliza\u00e7\u00e3o da calc\u00e9mia, a evolu\u00e7\u00e3o cl\u00ednica foi favor\u00e1vel com resolu\u00e7\u00e3o dos sintomasneurol\u00f3gicos. A hipocalc\u00e9mia deve ser investigada e corrigida depois de tiroidectomias, dada a irreversibilidade das calcifica\u00e7\u00f5es\u00a0intracerebrais e as potenciais consequ\u00eancias neurol\u00f3gicas e sist\u00e9micas.<\/jats:p>","DOI":"10.20344\/amp.11026","type":"journal-article","created":{"date-parts":[[2019,7,9]],"date-time":"2019-07-09T11:38:37Z","timestamp":1562672317000},"page":"402-406","source":"Crossref","is-referenced-by-count":2,"title":["Coreia Aguda Generalizada, Distonia e Calcifica\u00e7\u00f5es Cerebrais: A Prop\u00f3sito de um Caso Cl\u00ednico"],"prefix":"10.20344","volume":"32","author":[{"given":"Joana","family":"Ramos-Lopes","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ana","family":"Br\u00e1s","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ana","family":"Morgadinho","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Fradique","family":"Moreira","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"8464","published-online":{"date-parts":[[2019,5,31]]},"container-title":["Acta M\u00e9dica Portuguesa"],"original-title":[],"link":[{"URL":"https:\/\/www.actamedicaportuguesa.com\/revista\/index.php\/amp\/article\/download\/11026\/5704","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/www.actamedicaportuguesa.com\/revista\/index.php\/amp\/article\/download\/11026\/5704","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,10,24]],"date-time":"2022-10-24T22:35:23Z","timestamp":1666650923000},"score":1,"resource":{"primary":{"URL":"https:\/\/www.actamedicaportuguesa.com\/revista\/index.php\/amp\/article\/view\/11026"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2019,5,31]]},"references-count":0,"journal-issue":{"issue":"5","published-online":{"date-parts":[[2019,5,31]]}},"URL":"https:\/\/doi.org\/10.20344\/amp.11026","relation":{},"ISSN":["1646-0758","0870-399X"],"issn-type":[{"value":"1646-0758","type":"electronic"},{"value":"0870-399X","type":"print"}],"subject":[],"published":{"date-parts":[[2019,5,31]]}}}