{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T14:46:13Z","timestamp":1787755573739,"version":"build-2784847793"},"reference-count":18,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"2","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"abstract":"\n Case:<\/jats:title>\n An 18-year-old man with Ullrich congenital muscular dystrophy (UCMD) noted difficulty of looking forward and discomfort swallowing and breathing because of his hyperextended neck. We treated his cervical deformity with posterior spinal correction and fusion alone. He underwent a tracheotomy because of lung function deterioration 2 years after cervical surgery. The tracheotomy was performed safely because the anterior cervical spine anatomy was normalized and soft tissues around trachea were preserved by the posterior cervical correction.<\/jats:p>\n <\/jats:sec>\n \n Conclusion:<\/jats:title>\n Cervical hyperextension can be a problem in patients with UCMD. Posterior spinal correction and fusion may be a preferable solution.<\/jats:p>\n <\/jats:sec>","DOI":"10.2106\/jbjs.cc.19.00392","type":"journal-article","created":{"date-parts":[[2020,6,8]],"date-time":"2020-06-08T10:01:23Z","timestamp":1591610483000},"page":"e0392-e0392","source":"Crossref","is-referenced-by-count":2,"title":["Cervical Hyperextension Treated by Posterior Spinal Correction and Fusion in A Patient with Ullrich Congenital Muscular Dystrophy"],"prefix":"10.2106","volume":"10","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-9460-3408","authenticated-orcid":false,"given":"Wataru","family":"Saito","sequence":"first","affiliation":[{"name":"Department of Orthopedic Surgery, Kitasato University School of Medicine, Sagamihara, Kanagawa, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4853-8040","authenticated-orcid":false,"given":"Takayuki","family":"Imura","sequence":"additional","affiliation":[{"name":"Department of Orthopedic Surgery, Kitasato University School of Medicine, Sagamihara, Kanagawa, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-3082-9739","authenticated-orcid":false,"given":"Masayuki","family":"Miyagi","sequence":"additional","affiliation":[{"name":"Department of Orthopedic Surgery, Kitasato University School of Medicine, Sagamihara, Kanagawa, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7499-7008","authenticated-orcid":false,"given":"Toshiyuki","family":"Nakazawa","sequence":"additional","affiliation":[{"name":"Department of Orthopedic Surgery, Kitasato University School of Medicine, Sagamihara, Kanagawa, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-2407-9123","authenticated-orcid":false,"given":"Masashi","family":"Takaso","sequence":"additional","affiliation":[{"name":"Department of Orthopedic Surgery, Kitasato University School of Medicine, Sagamihara, Kanagawa, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-6500-9004","authenticated-orcid":false,"given":"Gen","family":"Inoue","sequence":"additional","affiliation":[{"name":"Department of Orthopedic Surgery, Kitasato University School of Medicine, Sagamihara, Kanagawa, Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","published-online":{"date-parts":[[2020]]},"reference":[{"key":"bib1-20230720","doi-asserted-by":"crossref","first-page":"171","DOI":"10.1007\/BF02864097","article-title":"Kongenitale, atonisch-skelerotische Muskeldystrophie, ein weiterer Typus der heredodegenerativen Erkrankungen des neuromuskul\u00e4ren Systems [in German]","volume":"126","author":"Ullrich","year":"1930","journal-title":"Z Ges Neurol Psychiat."},{"key":"bib2-20230720","doi-asserted-by":"crossref","first-page":"81","DOI":"10.1016\/B978-0-08-045031-5.00005-0","article-title":"The 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