{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T14:38:39Z","timestamp":1787755119770,"version":"build-2784847793"},"reference-count":15,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"1","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"abstract":"<jats:sec>\n                    <jats:title>Case:<\/jats:title>\n                    <jats:p>\n                      An eight-year-old boy presented with acute encephalopathy due to posterior circulation ischemic stroke. He was found to have vertebral artery stenosis secondary to atlantoaxial instability (AAI) due to an os odontoideum. Occipitocervical fusion was performed 4 weeks after stroke. The child improved neurologically and regained independent ambulation. He had indications of an underlying spondyloepiphyseal dysplasia with joint luxation and whole-exome sequencing diagnosed\n                      <jats:italic toggle=\"yes\">CHST3<\/jats:italic>\n                      -related skeletal dysplasia.\n                    <\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Conclusion:<\/jats:title>\n                    <jats:p>\n                      As far as we know, this AAI due to an os odontoideum is a previously unreported complication of\n                      <jats:italic toggle=\"yes\">CHST3<\/jats:italic>\n                      -related skeletal dysplasia. Occipitocervical fusion yielded good clinical results with the 1-year follow-up.\n                    <\/jats:p>\n                  <\/jats:sec>","DOI":"10.2106\/jbjs.cc.20.00393","type":"journal-article","created":{"date-parts":[[2021,2,27]],"date-time":"2021-02-27T00:18:16Z","timestamp":1614385096000},"update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":2,"title":["Posterior Circulation Stroke due to Atlantoaxial Instability in CHST3-Related Skeletal Dysplasia"],"prefix":"10.2106","volume":"11","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-8561-9157","authenticated-orcid":false,"given":"Arjun","family":"Dhawale","sequence":"first","affiliation":[{"name":"Department of Orthopaedics, Sir H.N. Reliance Foundation Hospital, Mumbai, Maharashtra, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-8754-2229","authenticated-orcid":false,"given":"Shruti","family":"Bajaj","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Sir H.N. Reliance Foundation Hospital, Mumbai, Maharashtra, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4879-1636","authenticated-orcid":false,"given":"Kshitij","family":"Chaudhary","sequence":"additional","affiliation":[{"name":"Department of Orthopaedics, Sir H.N. Reliance Foundation Hospital, Mumbai, Maharashtra, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-1636-0815","authenticated-orcid":false,"given":"Tushar","family":"Agarwal","sequence":"additional","affiliation":[{"name":"Department of Orthopaedics, Bhaktivedanta Hospital and Research Institute, Thane, Maharashtra, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-2284-8785","authenticated-orcid":false,"given":"Sandeep","family":"Garg","sequence":"additional","affiliation":[{"name":"Department of Pediatrics, Bhaktivedanta Hospital and Research Institute, Thane, Maharashtra, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-2620-264X","authenticated-orcid":false,"given":"Himanshu","family":"Choudhury","sequence":"additional","affiliation":[{"name":"Department of Radiology, Sir H.N. 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