{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T14:36:14Z","timestamp":1787754974417,"version":"build-2784847793"},"reference-count":17,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"3","content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"abstract":"<jats:sec>\n                    <jats:title>Case:<\/jats:title>\n                    <jats:p>A 40-year-old Colombian woman presented with a 7-year history of progressive lower-limb pain. Sclerosis of the diaphyseal tibia and femur was observed in her latest x-ray images. A narrowing of the medullary canal is observed in Camurati-Engelmann disease (CED), a rare and progressive diaphyseal dysplasia that was confirmed in this patient by genetic testing. Medical treatment was unsuccessful; thus, surgical treatment consisted of decompression by drilling of the medullary canal was performed, achieving successful pain release.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Conclusion:<\/jats:title>\n                    <jats:p>Surgical treatment should be considered for patients with CED when the medical treatment is unsuccessful because doing so reduces bone overgrowth, leading to pain relief.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.2106\/jbjs.cc.20.01042","type":"journal-article","created":{"date-parts":[[2021,8,5]],"date-time":"2021-08-05T15:00:08Z","timestamp":1628175608000},"update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":1,"title":["Surgery Treatment of an Adult Patient with Camurati-Engelmann Disease"],"prefix":"10.2106","volume":"11","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-5680-6781","authenticated-orcid":false,"given":"Fernando","family":"Saboya","sequence":"first","affiliation":[{"name":"Department of Orthopedics Oncology, Hospital de San Jose, Bogota, Colombia"},{"name":"Fundacion Universitaria de Ciencias de la Salud, Bogota, Colombia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-6190-6805","authenticated-orcid":false,"given":"Adriana","family":"Medina","sequence":"additional","affiliation":[{"name":"Fundacion Universitaria de Ciencias de la Salud, Bogota, Colombia"},{"name":"Department of endocrinology, Hospital de San Jose, Bogota, Colombia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-9594-7947","authenticated-orcid":false,"given":"Sergio","family":"Cadavid","sequence":"additional","affiliation":[{"name":"Department of Orthopedics Oncology, Hospital de San Jose, Bogota, Colombia"},{"name":"Fundacion Universitaria de Ciencias de la Salud, Bogota, Colombia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-4880-5791","authenticated-orcid":false,"given":"Ruben","family":"Fuentes","sequence":"additional","affiliation":[{"name":"Fundacion Universitaria de Ciencias de la Salud, Bogota, Colombia"},{"name":"Department of endocrinology, Hospital de San Jose, Bogota, Colombia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7728-1523","authenticated-orcid":false,"given":"Carlos Eduardo","family":"Jim\u00e9nez-Canizales","sequence":"additional","affiliation":[{"name":"Fundacion Universitaria de Ciencias de la Salud, Bogota, Colombia"},{"name":"Department of endocrinology, Hospital de San Jose, Bogota, Colombia"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"276","published-online":{"date-parts":[[2021,7]]},"reference":[{"issue":"Sect Study Dis Child","key":"bib1-20240805","first-page":"17","article-title":"Case for diagnosis","volume":"14","author":"Cockayne","year":"1921","journal-title":"Proc R Soc Med."},{"key":"bib2-20240805","doi-asserted-by":"crossref","first-page":"143","DOI":"10.1086\/302728","article-title":"Genetic mapping of the Camurati-Engelmann disease locus to chromosome 19q13.1-13.3","volume":"66","author":"Ghadami","year":"2000","journal-title":"Am J Hum Genet."},{"key":"bib3-20240805","doi-asserted-by":"crossref","first-page":"461","DOI":"10.2106\/00004623-197355030-00002","article-title":"Progressive diaphyseal dysplasia. 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